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5. Dysautonomia in an infant with secondary hyperammonemia due to propionyl coenzyme A carboxylase deficiency. Harris DJ; Yang BI; Wolf B; Snodgrass PJ Pediatrics; 1980 Jan; 65(1):107-10. PubMed ID: 7355003 [TBL] [Abstract][Full Text] [Related]
6. [Hyperammonemias of childhood. I. Enzymopathies of the urea cycle]. Kopieczna-Grzebieniak E; Toborek M; Tarnawski R; Jakubowska D Pediatr Pol; 1987 Oct; 62(10):727-32. PubMed ID: 3328149 [No Abstract] [Full Text] [Related]
7. Detection of carbamyl phosphate synthetase 1 deficiency using duodenal biopsy samples. Hoogenraad NJ; Mitchell JD; Don NA; Sutherland TM; Mc Leay AC Arch Dis Child; 1980 Apr; 55(4):292-5. PubMed ID: 7416778 [TBL] [Abstract][Full Text] [Related]
8. Siblings with carbamyl phosphate synthetase I deficiency. Asanuma K; Takeuchi Y; Kanda M; Kikuchi Y; Yano N; Kakinuma H Acta Pathol Jpn; 1984 Jul; 34(4):901-10. PubMed ID: 6485804 [TBL] [Abstract][Full Text] [Related]
9. [Remarks on a clinical case of partial carbamyl phosphate synthetase deficiency]. Gomirato G; Giaretto G; Bonomi A; Rossi E; Rovere A; Radeschi G; Crosato M Minerva Pediatr; 1989 Feb; 41(2):105-8. PubMed ID: 2739630 [TBL] [Abstract][Full Text] [Related]
10. Periodic hyperammonemia, hyperlysinemia, and homocitrullinuria associated with decreased argininosuccinate synthetase and arginase activities. Sogawa H; Oyanagi K; Nakao T Pediatr Res; 1977 Sep; 11(9 Pt 1):949-53. PubMed ID: 904980 [No Abstract] [Full Text] [Related]
11. [Carbamyl phosphate synthetase I deficiency]. Ohtake A; Mori M Tanpakushitsu Kakusan Koso; 1988 Apr; 33(5):497-9. PubMed ID: 3270854 [No Abstract] [Full Text] [Related]
12. Successful treatment of severe carbamyl phosphate synthetase I deficiency. Van de Bor M; Mooy P; van Zoeren D; Berger R; van Gelderen HH; Teijema HL Arch Dis Child; 1984 Dec; 59(12):1183-5. PubMed ID: 6524951 [TBL] [Abstract][Full Text] [Related]
13. Kinetic abnormalities of carbamyl phosphate synthetase-I in a case of congenital hyperammonaemia. Qureshi IA; Letarte J; Ouellet R; Lemieux B; Cathelineau L J Inherit Metab Dis; 1986; 9(3):253-60. PubMed ID: 3099069 [TBL] [Abstract][Full Text] [Related]
14. Cognitive functioning in two sisters with carbamyl phosphate synthetase I deficiency. Sassaman EA; Zartler AS; Mulick JA J Pediatr Psychol; 1981 Jun; 6(2):171-5. PubMed ID: 7252721 [No Abstract] [Full Text] [Related]
15. Use of keto acids in inborn errors of urea synthesis. Brusilow S; Batshaw M; Walser M Curr Concepts Nutr; 1979; 8():65-75. PubMed ID: 527359 [TBL] [Abstract][Full Text] [Related]
18. [Comments on the contribution, Therapy of hyperammonemia in carbamylphosphate synthetase deficiency with peritoneal dialysis and venovenous hemofiltration, by B. Lettgen et al]. Brockstedt M Monatsschr Kinderheilkd; 1992 Jul; 140(7):431. PubMed ID: 1308100 [No Abstract] [Full Text] [Related]
19. Severe neonatal deficiency of carbamylphosphate synthetase. Lambotte C; Adam A; Van Der Hofstadt J; Dodinval-Versie J; Gielen J Acta Paediatr Belg; 1977; 30(3):151-5. PubMed ID: 204150 [No Abstract] [Full Text] [Related]