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4. Molecular analysis of peroxisomal beta-oxidation enzymes in infants with peroxisomal disorders indicates heterogeneity of the primary defect. Guerroui S; Aubourg P; Chen WW; Hashimoto T; Scotto J Biochem Biophys Res Commun; 1989 May; 161(1):242-51. PubMed ID: 2471528 [TBL] [Abstract][Full Text] [Related]
5. Aberrant subcellular localization of peroxisomal 3-ketoacyl-CoA thiolase in the Zellweger syndrome and rhizomelic chondrodysplasia punctata. Balfe A; Hoefler G; Chen WW; Watkins PA Pediatr Res; 1990 Mar; 27(3):304-10. PubMed ID: 2181395 [TBL] [Abstract][Full Text] [Related]
6. [Zellweger syndrome, neonatal adrenoleukodystrophy or infantile Refsum's disease in a case with generalized peroxisome defect?]. Schmitt K; Molzer B; Stöckler S; Tulzer G; Tulzer W Wien Klin Wochenschr; 1993; 105(11):320-2. PubMed ID: 7687405 [TBL] [Abstract][Full Text] [Related]
7. Peroxisomal fatty acid beta-oxidation in relation to the accumulation of very long chain fatty acids in cultured skin fibroblasts from patients with Zellweger syndrome and other peroxisomal disorders. Wanders RJ; van Roermund CW; van Wijland MJ; Schutgens RB; Heikoop J; van den Bosch H; Schram AW; Tager JM J Clin Invest; 1987 Dec; 80(6):1778-83. PubMed ID: 3680527 [TBL] [Abstract][Full Text] [Related]
8. Phytanic acid alpha-oxidation and complementation analysis of classical Refsum and peroxisomal disorders. Poll-The BT; Skjeldal OH; Stokke O; Poulos A; Demaugre F; Saudubray JM Hum Genet; 1989 Jan; 81(2):175-81. PubMed ID: 2463966 [TBL] [Abstract][Full Text] [Related]
9. Genetic diseases caused by peroxisomal dysfunction. New findings in clinical and biochemical studies. Schutgens RB; Wanders RJ; Nijenhuis A; van den Hoek CM; Heymans HS; Schrakamp G; Bleeker-Wagemakers EM; Delleman JW; Schram AW; Tager JM Enzyme; 1987; 38(1-4):161-76. PubMed ID: 3440444 [TBL] [Abstract][Full Text] [Related]
10. Phytanic acid and very long chain fatty acids in genetic peroxisomal disorders. Molzer B; Kainz-Korschinsky M; Sundt-Heller R; Bernheimer H J Clin Chem Clin Biochem; 1989 May; 27(5):309-14. PubMed ID: 2474624 [TBL] [Abstract][Full Text] [Related]
11. [Peroxisomal neurologic diseases and Refsum disease: very long chain fatty acids and phytanic acid as diagnostic markers]. Molzer B; Stöckler S; Bernheimer H Wien Klin Wochenschr; 1992; 104(21):665-70. PubMed ID: 1282286 [TBL] [Abstract][Full Text] [Related]
12. New insights in peroxisomal beta-oxidation. Implications for human peroxisomal disorders. Van Veldhoven PP Verh K Acad Geneeskd Belg; 1998; 60(3):195-214. PubMed ID: 9803880 [TBL] [Abstract][Full Text] [Related]
13. [The contribution of peroxisomes to lipid metabolism]. Kramar R J Clin Chem Clin Biochem; 1986 Feb; 24(2):109-18. PubMed ID: 3711795 [TBL] [Abstract][Full Text] [Related]
14. Rhizomelic chondrodysplasia punctata. Deficiency of 3-oxoacyl-coenzyme A thiolase in peroxisomes and impaired processing of the enzyme. Heikoop JC; van Roermund CW; Just WW; Ofman R; Schutgens RB; Heymans HS; Wanders RJ; Tager JM J Clin Invest; 1990 Jul; 86(1):126-30. PubMed ID: 2365812 [TBL] [Abstract][Full Text] [Related]
15. Peroxisomal integral membrane proteins in livers of patients with Zellweger syndrome, infantile Refsum's disease and X-linked adrenoleukodystrophy. Small GM; Santos MJ; Imanaka T; Poulos A; Danks DM; Moser HW; Lazarow PB J Inherit Metab Dis; 1988; 11(4):358-71. PubMed ID: 2468817 [TBL] [Abstract][Full Text] [Related]
16. Infantile Refsum disease: deficiency of catalase-containing particles (peroxisomes), alkyldihydroxyacetone phosphate synthase and peroxisomal beta-oxidation enzyme proteins. Wanders RJ; Schutgens RB; Schrakamp G; van den Bosch H; Tager JM; Schram AW; Hashimoto T; Poll-Thé BT; Saudubrau JM Eur J Pediatr; 1986 Aug; 145(3):172-5. PubMed ID: 2429839 [TBL] [Abstract][Full Text] [Related]
17. [Clinical biochemical and genetic aspects of peroxisome-deficient disorders]. Suzuki Y No To Hattatsu; 1992 Mar; 24(2):194-7. PubMed ID: 1373633 [TBL] [Abstract][Full Text] [Related]
18. Biochemical features of a patient with Zellweger-like syndrome with normal PTS-1 and PTS-2 peroxisomal protein import systems: a new peroxisomal disease. Singh I; Voigt RG; Sheikh FG; Kremser K; Brown FR Biochem Mol Med; 1997 Aug; 61(2):198-207. PubMed ID: 9259985 [TBL] [Abstract][Full Text] [Related]
19. Peroxisomal beta-oxidation enzyme proteins in adrenoleukodystrophy: distinction between X-linked adrenoleukodystrophy and neonatal adrenoleukodystrophy. Chen WW; Watkins PA; Osumi T; Hashimoto T; Moser HW Proc Natl Acad Sci U S A; 1987 Mar; 84(5):1425-8. PubMed ID: 3469675 [TBL] [Abstract][Full Text] [Related]