152 related articles for article (PubMed ID: 7511336)
21. Cystic fibrosis transmembrane conductance regulator (CFTR) and renal function.
Stanton BA
Wien Klin Wochenschr; 1997 Jun; 109(12-13):457-64. PubMed ID: 9261986
[TBL] [Abstract][Full Text] [Related]
22. In vitro pharmacologic restoration of CFTR-mediated chloride transport with sodium 4-phenylbutyrate in cystic fibrosis epithelial cells containing delta F508-CFTR.
Rubenstein RC; Egan ME; Zeitlin PL
J Clin Invest; 1997 Nov; 100(10):2457-65. PubMed ID: 9366560
[TBL] [Abstract][Full Text] [Related]
23. Defects in processing and trafficking of cystic fibrosis transmembrane conductance regulator.
Kunzelmann K; Nitschke R
Exp Nephrol; 2000; 8(6):332-42. PubMed ID: 11014930
[TBL] [Abstract][Full Text] [Related]
24. An immortalized cystic fibrosis tracheal epithelial cell line homozygous for the delta F508 CFTR mutation.
Kunzelmann K; Schwiebert EM; Zeitlin PL; Kuo WL; Stanton BA; Gruenert DC
Am J Respir Cell Mol Biol; 1993 May; 8(5):522-9. PubMed ID: 7683197
[TBL] [Abstract][Full Text] [Related]
25. Conformational maturation of CFTR but not its mutant counterpart (delta F508) occurs in the endoplasmic reticulum and requires ATP.
Lukacs GL; Mohamed A; Kartner N; Chang XB; Riordan JR; Grinstein S
EMBO J; 1994 Dec; 13(24):6076-86. PubMed ID: 7529176
[TBL] [Abstract][Full Text] [Related]
26. Calcium-pump inhibitors induce functional surface expression of Delta F508-CFTR protein in cystic fibrosis epithelial cells.
Egan ME; Glöckner-Pagel J; Ambrose C; Cahill PA; Pappoe L; Balamuth N; Cho E; Canny S; Wagner CA; Geibel J; Caplan MJ
Nat Med; 2002 May; 8(5):485-92. PubMed ID: 11984593
[TBL] [Abstract][Full Text] [Related]
27. Abnormal subcellular localization of mutated CFTR protein in a cystic fibrosis epithelial cell line.
Demolombe S; Baró I; Laurent M; Hongre AS; Pavirani A; Escande D
Eur J Cell Biol; 1994 Oct; 65(1):214-9. PubMed ID: 7534234
[TBL] [Abstract][Full Text] [Related]
28. A change in gating mode leading to increased intrinsic Cl- channel activity compensates for defective processing in a cystic fibrosis mutant corresponding to a mild form of the disease.
Champigny G; Imler JL; Puchelle E; Dalemans W; Gribkoff V; Hinnrasky J; Dott K; Barbry P; Pavirani A; Lazdunski M
EMBO J; 1995 Jun; 14(11):2417-23. PubMed ID: 7540133
[TBL] [Abstract][Full Text] [Related]
29. Mutation of R555 in CFTR-delta F508 enhances function and partially corrects defective processing.
Teem JL; Carson MR; Welsh MJ
Recept Channels; 1996; 4(1):63-72. PubMed ID: 8723647
[TBL] [Abstract][Full Text] [Related]
30. Molecular basis of defective anion transport in L cells expressing recombinant forms of CFTR.
Yang Y; Devor DC; Engelhardt JF; Ernst SA; Strong TV; Collins FS; Cohn JA; Frizzell RA; Wilson JM
Hum Mol Genet; 1993 Aug; 2(8):1253-61. PubMed ID: 7691345
[TBL] [Abstract][Full Text] [Related]
31. Calnexin Delta 185-520 partially reverses the misprocessing of the Delta F508 cystic fibrosis transmembrane conductance regulator.
Okiyoneda T; Wada I; Jono H; Shuto T; Yoshitake K; Nakano N; Nagayama S; Harada K; Isohama Y; Miyata T; Kai H
FEBS Lett; 2002 Aug; 526(1-3):87-92. PubMed ID: 12208510
[TBL] [Abstract][Full Text] [Related]
32. Functional CFTR in endosomal compartment of CFTR-expressing fibroblasts and T84 cells.
Biwersi J; Verkman AS
Am J Physiol; 1994 Jan; 266(1 Pt 1):C149-56. PubMed ID: 7508186
[TBL] [Abstract][Full Text] [Related]
33. Pseudomonas aeruginosa-induced apoptosis is defective in respiratory epithelial cells expressing mutant cystic fibrosis transmembrane conductance regulator.
Cannon CL; Kowalski MP; Stopak KS; Pier GB
Am J Respir Cell Mol Biol; 2003 Aug; 29(2):188-97. PubMed ID: 12878584
[TBL] [Abstract][Full Text] [Related]
34. Differential localization of the cystic fibrosis transmembrane conductance regulator in normal and cystic fibrosis airway epithelium.
Puchelle E; Gaillard D; Ploton D; Hinnrasky J; Fuchey C; Boutterin MC; Jacquot J; Dreyer D; Pavirani A; Dalemans W
Am J Respir Cell Mol Biol; 1992 Nov; 7(5):485-91. PubMed ID: 1384582
[TBL] [Abstract][Full Text] [Related]
35. A mouse model for the delta F508 allele of cystic fibrosis.
Zeiher BG; Eichwald E; Zabner J; Smith JJ; Puga AP; McCray PB; Capecchi MR; Welsh MJ; Thomas KR
J Clin Invest; 1995 Oct; 96(4):2051-64. PubMed ID: 7560099
[TBL] [Abstract][Full Text] [Related]
36. Normal function of the cystic fibrosis conductance regulator protein can be associated with homozygous (Delta)F508 mutation.
Sermet-Gaudelus I; Vallée B; Urbin I; Torossi T; Marianovski R; Fajac A; Feuillet MN; Bresson JL; Lenoir G; Bernaudin JF; Edelman A
Pediatr Res; 2002 Nov; 52(5):628-35. PubMed ID: 12409506
[TBL] [Abstract][Full Text] [Related]
37. Defective acidification of the biosynthetic pathway in cystic fibrosis.
Barasch J; al-Awqati Q
J Cell Sci Suppl; 1993; 17():229-33. PubMed ID: 7511615
[TBL] [Abstract][Full Text] [Related]
38. The cystic fibrosis transmembrane conductance regulator. Overexpression, purification, and characterization of wild type and delta F508 mutant forms of the first nucleotide binding fold in fusion with the maltose-binding protein.
Ko YH; Thomas PJ; Delannoy MR; Pedersen PL
J Biol Chem; 1993 Nov; 268(32):24330-8. PubMed ID: 7693699
[TBL] [Abstract][Full Text] [Related]
39. Cystic fibrosis transmembrane conductance regulator mutations that disrupt nucleotide binding.
Logan J; Hiestand D; Daram P; Huang Z; Muccio DD; Hartman J; Haley B; Cook WJ; Sorscher EJ
J Clin Invest; 1994 Jul; 94(1):228-36. PubMed ID: 7518829
[TBL] [Abstract][Full Text] [Related]
40. Mislocalization of delta F508 CFTR in cystic fibrosis sweat gland.
Kartner N; Augustinas O; Jensen TJ; Naismith AL; Riordan JR
Nat Genet; 1992 Aug; 1(5):321-7. PubMed ID: 1284548
[TBL] [Abstract][Full Text] [Related]
[Previous] [Next] [New Search]