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8. A delta F508 mutation in mouse cystic fibrosis transmembrane conductance regulator results in a temperature-sensitive processing defect in vivo. French PJ; van Doorninck JH; Peters RH; Verbeek E; Ameen NA; Marino CR; de Jonge HR; Bijman J; Scholte BJ J Clin Invest; 1996 Sep; 98(6):1304-12. PubMed ID: 8823295 [TBL] [Abstract][Full Text] [Related]
9. Abnormal subcellular localization of mutated CFTR protein in a cystic fibrosis epithelial cell line. Demolombe S; Baró I; Laurent M; Hongre AS; Pavirani A; Escande D Eur J Cell Biol; 1994 Oct; 65(1):214-9. PubMed ID: 7534234 [TBL] [Abstract][Full Text] [Related]
10. A mouse model for the delta F508 allele of cystic fibrosis. Zeiher BG; Eichwald E; Zabner J; Smith JJ; Puga AP; McCray PB; Capecchi MR; Welsh MJ; Thomas KR J Clin Invest; 1995 Oct; 96(4):2051-64. PubMed ID: 7560099 [TBL] [Abstract][Full Text] [Related]
11. Cystic fibrosis transmembrane conductance regulator (CFTR) and renal function. Stanton BA Wien Klin Wochenschr; 1997 Jun; 109(12-13):457-64. PubMed ID: 9261986 [TBL] [Abstract][Full Text] [Related]
12. Functional activation of the cystic fibrosis trafficking mutant delta F508-CFTR by overexpression. Cheng SH; Fang SL; Zabner J; Marshall J; Piraino S; Schiavi SC; Jefferson DM; Welsh MJ; Smith AE Am J Physiol; 1995 Apr; 268(4 Pt 1):L615-24. PubMed ID: 7733303 [TBL] [Abstract][Full Text] [Related]
13. Expression of delta F508 cystic fibrosis transmembrane conductance regulator protein and related chloride transport properties in the gallbladder epithelium from cystic fibrosis patients. Dray-Charier N; Paul A; Scoazec JY; Veissière D; Mergey M; Capeau J; Soubrane O; Housset C Hepatology; 1999 Jun; 29(6):1624-34. PubMed ID: 10347100 [TBL] [Abstract][Full Text] [Related]
15. Cystic fibrosis patients with mutation 1949del84 in exon 13 of the CFTR gene have a similar clinical severity as delta F508 homozygotes. Nunes V; Casals T; Gaona A; Antiñolo G; Ferrer-Calvete J; Pérez-Frias J; Tardío E; Molano J; Estivill X Hum Mutat; 1992; 1(5):375-9. PubMed ID: 1284539 [TBL] [Abstract][Full Text] [Related]
16. A frame-shift mutation in the cystic fibrosis gene. White MB; Amos J; Hsu JM; Gerrard B; Finn P; Dean M Nature; 1990 Apr; 344(6267):665-7. PubMed ID: 1691449 [TBL] [Abstract][Full Text] [Related]
17. [The cystic fibrosis gene: mutation and the function of CFTR protein]. Goossens M Ann Pediatr (Paris); 1991 Nov; 38(9):591-4. PubMed ID: 1721508 [TBL] [Abstract][Full Text] [Related]
18. Differential localization of the cystic fibrosis transmembrane conductance regulator in normal and cystic fibrosis airway epithelium. Puchelle E; Gaillard D; Ploton D; Hinnrasky J; Fuchey C; Boutterin MC; Jacquot J; Dreyer D; Pavirani A; Dalemans W Am J Respir Cell Mol Biol; 1992 Nov; 7(5):485-91. PubMed ID: 1384582 [TBL] [Abstract][Full Text] [Related]
19. Mutations in CFTR associated with mild-disease-form Cl- channels with altered pore properties. Sheppard DN; Rich DP; Ostedgaard LS; Gregory RJ; Smith AE; Welsh MJ Nature; 1993 Mar; 362(6416):160-4. PubMed ID: 7680769 [TBL] [Abstract][Full Text] [Related]
20. [The cystic fibrosis gene, its product CFTR protein and its mutations]. Goossens M; Fanen P; Costes B; Ghanem N Bull Acad Natl Med; 1993 Mar; 177(3):371-80; discussion 380-1. PubMed ID: 7689915 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]