299 related articles for article (PubMed ID: 7523390)
1. Intracellular turnover of cystic fibrosis transmembrane conductance regulator. Inefficient processing and rapid degradation of wild-type and mutant proteins.
Ward CL; Kopito RR
J Biol Chem; 1994 Oct; 269(41):25710-8. PubMed ID: 7523390
[TBL] [Abstract][Full Text] [Related]
2. Conformational maturation of CFTR but not its mutant counterpart (delta F508) occurs in the endoplasmic reticulum and requires ATP.
Lukacs GL; Mohamed A; Kartner N; Chang XB; Riordan JR; Grinstein S
EMBO J; 1994 Dec; 13(24):6076-86. PubMed ID: 7529176
[TBL] [Abstract][Full Text] [Related]
3. Turnover of the cystic fibrosis transmembrane conductance regulator (CFTR): slow degradation of wild-type and delta F508 CFTR in surface membrane preparations of immortalized airway epithelial cells.
Wei X; Eisman R; Xu J; Harsch AD; Mulberg AE; Bevins CL; Glick MC; Scanlin TF
J Cell Physiol; 1996 Aug; 168(2):373-84. PubMed ID: 8707873
[TBL] [Abstract][Full Text] [Related]
4. The common variant of cystic fibrosis transmembrane conductance regulator is recognized by hsp70 and degraded in a pre-Golgi nonlysosomal compartment.
Yang Y; Janich S; Cohn JA; Wilson JM
Proc Natl Acad Sci U S A; 1993 Oct; 90(20):9480-4. PubMed ID: 7692448
[TBL] [Abstract][Full Text] [Related]
5. Processing of mutant cystic fibrosis transmembrane conductance regulator is temperature-sensitive.
Denning GM; Anderson MP; Amara JF; Marshall J; Smith AE; Welsh MJ
Nature; 1992 Aug; 358(6389):761-4. PubMed ID: 1380673
[TBL] [Abstract][Full Text] [Related]
6. The delta F508 mutation decreases the stability of cystic fibrosis transmembrane conductance regulator in the plasma membrane. Determination of functional half-lives on transfected cells.
Lukacs GL; Chang XB; Bear C; Kartner N; Mohamed A; Riordan JR; Grinstein S
J Biol Chem; 1993 Oct; 268(29):21592-8. PubMed ID: 7691813
[TBL] [Abstract][Full Text] [Related]
7. Control of cystic fibrosis transmembrane conductance regulator membrane trafficking: not just from the endoplasmic reticulum to the Golgi.
Farinha CM; Matos P; Amaral MD
FEBS J; 2013 Sep; 280(18):4396-406. PubMed ID: 23773658
[TBL] [Abstract][Full Text] [Related]
8. Intracellular loop between transmembrane segments IV and V of cystic fibrosis transmembrane conductance regulator is involved in regulation of chloride channel conductance state.
Xie J; Drumm ML; Ma J; Davis PB
J Biol Chem; 1995 Nov; 270(47):28084-91. PubMed ID: 7499295
[TBL] [Abstract][Full Text] [Related]
9. Stoichiometry of recombinant cystic fibrosis transmembrane conductance regulator in epithelial cells and its functional reconstitution into cells in vitro.
Marshall J; Fang S; Ostedgaard LS; O'Riordan CR; Ferrara D; Amara JF; Hoppe H; Scheule RK; Welsh MJ; Smith AE
J Biol Chem; 1994 Jan; 269(4):2987-95. PubMed ID: 7507932
[TBL] [Abstract][Full Text] [Related]
10. Diffusional mobility of the cystic fibrosis transmembrane conductance regulator mutant, delta F508-CFTR, in the endoplasmic reticulum measured by photobleaching of GFP-CFTR chimeras.
Haggie PM; Stanton BA; Verkman AS
J Biol Chem; 2002 May; 277(19):16419-25. PubMed ID: 11877404
[TBL] [Abstract][Full Text] [Related]
11. Sequential quality-control checkpoints triage misfolded cystic fibrosis transmembrane conductance regulator.
Younger JM; Chen L; Ren HY; Rosser MF; Turnbull EL; Fan CY; Patterson C; Cyr DM
Cell; 2006 Aug; 126(3):571-82. PubMed ID: 16901789
[TBL] [Abstract][Full Text] [Related]
12. Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis.
Cheng SH; Gregory RJ; Marshall J; Paul S; Souza DW; White GA; O'Riordan CR; Smith AE
Cell; 1990 Nov; 63(4):827-34. PubMed ID: 1699669
[TBL] [Abstract][Full Text] [Related]
13. Chemical chaperones correct the mutant phenotype of the delta F508 cystic fibrosis transmembrane conductance regulator protein.
Brown CR; Hong-Brown LQ; Biwersi J; Verkman AS; Welch WJ
Cell Stress Chaperones; 1996 Jun; 1(2):117-25. PubMed ID: 9222597
[TBL] [Abstract][Full Text] [Related]
14. Mutant (delta F508) cystic fibrosis transmembrane conductance regulator Cl- channel is functional when retained in endoplasmic reticulum of mammalian cells.
Pasyk EA; Foskett JK
J Biol Chem; 1995 May; 270(21):12347-50. PubMed ID: 7539001
[TBL] [Abstract][Full Text] [Related]
15. Organic solutes rescue the functional defect in delta F508 cystic fibrosis transmembrane conductance regulator.
Zhang XM; Wang XT; Yue H; Leung SW; Thibodeau PH; Thomas PJ; Guggino SE
J Biol Chem; 2003 Dec; 278(51):51232-42. PubMed ID: 14532265
[TBL] [Abstract][Full Text] [Related]
16. The cystic fibrosis mutation (delta F508) does not influence the chloride channel activity of CFTR.
Li C; Ramjeesingh M; Reyes E; Jensen T; Chang X; Rommens JM; Bear CE
Nat Genet; 1993 Apr; 3(4):311-6. PubMed ID: 7526932
[TBL] [Abstract][Full Text] [Related]
17. Biochemical characterization of the cystic fibrosis transmembrane conductance regulator in normal and cystic fibrosis epithelial cells.
Sarkadi B; Bauzon D; Huckle WR; Earp HS; Berry A; Suchindran H; Price EM; Olson JC; Boucher RC; Scarborough GA
J Biol Chem; 1992 Jan; 267(3):2087-95. PubMed ID: 1370488
[TBL] [Abstract][Full Text] [Related]
18. Dysfunction of CFTR bearing the delta F508 mutation.
Welsh MJ; Denning GM; Ostedgaard LS; Anderson MP
J Cell Sci Suppl; 1993; 17():235-9. PubMed ID: 7511616
[TBL] [Abstract][Full Text] [Related]
19. Limited proteolysis as a probe for arrested conformational maturation of delta F508 CFTR.
Zhang F; Kartner N; Lukacs GL
Nat Struct Biol; 1998 Mar; 5(3):180-3. PubMed ID: 9501909
[TBL] [Abstract][Full Text] [Related]
20. Participation of the endoplasmic reticulum chaperone calnexin (p88, IP90) in the biogenesis of the cystic fibrosis transmembrane conductance regulator.
Pind S; Riordan JR; Williams DB
J Biol Chem; 1994 Apr; 269(17):12784-8. PubMed ID: 7513695
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
