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6. Total branched-chain amino acids requirement in patients with maple syrup urine disease by use of indicator amino acid oxidation with L-[1-13C]phenylalanine. Riazi R; Rafii M; Clarke JT; Wykes LJ; Ball RO; Pencharz PB Am J Physiol Endocrinol Metab; 2004 Jul; 287(1):E142-9. PubMed ID: 14970005 [TBL] [Abstract][Full Text] [Related]
7. Apoptotic signaling pathways induced by acute administration of branched-chain amino acids in an animal model of maple syrup urine disease. Vilela TC; Scaini G; Furlanetto CB; Pasquali MA; Santos JP; Gelain DP; Moreira JC; Schuck PF; Ferreira GC; Streck EL Metab Brain Dis; 2017 Feb; 32(1):115-122. PubMed ID: 27510712 [TBL] [Abstract][Full Text] [Related]
8. Metabolism of branched-chain amino acids in maple syrup urine disease. Schadewaldt P; Wendel U Eur J Pediatr; 1997 Aug; 156 Suppl 1():S62-6. PubMed ID: 9266218 [TBL] [Abstract][Full Text] [Related]
10. Maple syrup urine disease: interrelations between branched-chain amino-, oxo- and hydroxyacids; implications for treatment; associations with CNS dysmyelination. Treacy E; Clow CL; Reade TR; Chitayat D; Mamer OA; Scriver CR J Inherit Metab Dis; 1992; 15(1):121-35. PubMed ID: 1583867 [TBL] [Abstract][Full Text] [Related]
11. Changes in branched-chain amino acids in an infant with maple syrup urine disease during perioperative pediatric liver transplant: A case report. Saeyup P; Tubjaroen C; Kamolvisit W; Chongsrisawat V; Thaveepunsan W Paediatr Anaesth; 2024 Apr; 34(4):366-370. PubMed ID: 38314877 [TBL] [Abstract][Full Text] [Related]
12. Treatment of the acute crisis in maple syrup urine disease. Nyhan WL; Rice-Kelts M; Klein J; Barshop BA Arch Pediatr Adolesc Med; 1998 Jun; 152(6):593-8. PubMed ID: 9641714 [TBL] [Abstract][Full Text] [Related]
13. Effects of abnormal metabolites of maple syrup urine disease on neurotransmitter receptor binding. Dwivedi C; James EC; Parmar SS Biochem Med Metab Biol; 1986 Jun; 35(3):275-8. PubMed ID: 3013257 [TBL] [Abstract][Full Text] [Related]
14. Imaging findings of anaplastic astrocytoma in a child with maple syrup urine disease: a case report. Aw-Zoretic J; Wadhwani NR; Lulla RR; Ryan ME Childs Nerv Syst; 2015 Sep; 31(9):1625-9. PubMed ID: 26084772 [TBL] [Abstract][Full Text] [Related]