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6. A new PRNP mutation (G131V) associated with Gerstmann-Sträussler-Scheinker disease. Panegyres PK; Toufexis K; Kakulas BA; Cernevakova L; Brown P; Ghetti B; Piccardo P; Dlouhy SR Arch Neurol; 2001 Nov; 58(11):1899-902. PubMed ID: 11709001 [TBL] [Abstract][Full Text] [Related]
7. Neuropathology of Gerstmann-Sträussler-Scheinker disease. Bugiani O; Giaccone G; Piccardo P; Morbin M; Tagliavini F; Ghetti B Microsc Res Tech; 2000 Jul; 50(1):10-5. PubMed ID: 10871543 [TBL] [Abstract][Full Text] [Related]
8. Gerstmann-Sträussler-Scheinker Disease with F198S Mutation Induces Independent Tau and Prion Protein Pathologies in Bank Voles. Bruno R; Pirisinu L; Riccardi G; D'Agostino C; De Cecco E; Legname G; Cardone F; Gambetti P; Nonno R; Agrimi U; Di Bari MA Biomolecules; 2022 Oct; 12(10):. PubMed ID: 36291746 [TBL] [Abstract][Full Text] [Related]
9. Gerstmann-Sträussler-Scheinker disease and the French-Alsatian A117V variant. Mohr M; Tranchant C; Steinmetz G; Floquet J; Grignon Y; Warter JM Clin Exp Pathol; 1999; 47(3-4):161-75. PubMed ID: 10472736 [TBL] [Abstract][Full Text] [Related]
10. Amyloid fibrils in Gerstmann-Sträussler-Scheinker disease (Indiana and Swedish kindreds) express only PrP peptides encoded by the mutant allele. Tagliavini F; Prelli F; Porro M; Rossi G; Giaccone G; Farlow MR; Dlouhy SR; Ghetti B; Bugiani O; Frangione B Cell; 1994 Nov; 79(4):695-703. PubMed ID: 7954833 [TBL] [Abstract][Full Text] [Related]
11. Hereditary prion protein amyloidoses. Ghetti B; Tagliavini F; Takao M; Bugiani O; Piccardo P Clin Lab Med; 2003 Mar; 23(1):65-85, viii. PubMed ID: 12733425 [TBL] [Abstract][Full Text] [Related]
12. Dominantly inherited prion protein cerebral amyloidoses - a modern view of Gerstmann-Sträussler-Scheinker. Ghetti B; Piccardo P; Zanusso G Handb Clin Neurol; 2018; 153():243-269. PubMed ID: 29887140 [TBL] [Abstract][Full Text] [Related]
13. Neurofibrillary tangles in Gerstmann-Sträussler-Scheinker syndrome with the A117V prion gene mutation. Tranchant C; Sergeant N; Wattez A; Mohr M; Warter JM; Delacourte A J Neurol Neurosurg Psychiatry; 1997 Aug; 63(2):240-6. PubMed ID: 9285466 [TBL] [Abstract][Full Text] [Related]
14. Gerstmann-Sträussler-Scheinker disease. I. Human diseases. Liberski PP; Budka H Folia Neuropathol; 2004; 42 Suppl B():120-40. PubMed ID: 16903147 [TBL] [Abstract][Full Text] [Related]
15. An autopsy report of three kindred in a Gerstmann-Sträussler-Scheinker disease P105L family with a special reference to prion protein, tau, and beta-amyloid. Ishizawa K; Mitsufuji T; Shioda K; Kobayashi A; Komori T; Nakazato Y; Kitamoto T; Araki N; Yamamoto T; Sasaki A Brain Behav; 2018 Oct; 8(10):e01117. PubMed ID: 30240140 [TBL] [Abstract][Full Text] [Related]
16. Variant Gerstmann-Sträussler syndrome with the P105L prion gene mutation: an unusual case with nigral degeneration and widespread neurofibrillary tangles. Yamazaki M; Oyanagi K; Mori O; Kitamura S; Ohyama M; Terashi A; Kitamoto T; Katayama Y Acta Neuropathol; 1999 Nov; 98(5):506-11. PubMed ID: 10541874 [TBL] [Abstract][Full Text] [Related]
17. Gerstmann-Sträussler-Scheinker syndrome with variable phenotype in a new kindred with PRNP-P102L mutation. Riudavets MA; Sraka MA; Schultz M; Rojas E; Martinetto H; Begué C; Noher de Halac I; Poleggi A; Equestre M; Pocchiari M; Sevlever G; Taratuto AL Brain Pathol; 2014 Mar; 24(2):142-7. PubMed ID: 23944754 [TBL] [Abstract][Full Text] [Related]
18. Unusual clinical and molecular-pathological profile of gerstmann-Sträussler-Scheinker disease associated with a novel PRNP mutation (V176G). Simpson M; Johanssen V; Boyd A; Klug G; Masters CL; Li QX; Pamphlett R; McLean C; Lewis V; Collins SJ JAMA Neurol; 2013 Sep; 70(9):1180-5. PubMed ID: 23857164 [TBL] [Abstract][Full Text] [Related]
19. Prion protein preamyloid and amyloid deposits in Gerstmann-Sträussler-Scheinker disease, Indiana kindred. Giaccone G; Verga L; Bugiani O; Frangione B; Serban D; Prusiner SB; Farlow MR; Ghetti B; Tagliavini F Proc Natl Acad Sci U S A; 1992 Oct; 89(19):9349-53. PubMed ID: 1357663 [TBL] [Abstract][Full Text] [Related]
20. Hyperphosphorylated tau deposition parallels prion protein burden in a case of Gerstmann-Sträussler-Scheinker syndrome P102L mutation complicated with dementia. Ishizawa K; Komori T; Shimazu T; Yamamoto T; Kitamoto T; Shimazu K; Hirose T Acta Neuropathol; 2002 Oct; 104(4):342-50. PubMed ID: 12200619 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]