These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
6. Neuropathology of Gerstmann-Sträussler-Scheinker disease. Bugiani O; Giaccone G; Piccardo P; Morbin M; Tagliavini F; Ghetti B Microsc Res Tech; 2000 Jul; 50(1):10-5. PubMed ID: 10871543 [TBL] [Abstract][Full Text] [Related]
7. Unusual clinical and molecular-pathological profile of gerstmann-Sträussler-Scheinker disease associated with a novel PRNP mutation (V176G). Simpson M; Johanssen V; Boyd A; Klug G; Masters CL; Li QX; Pamphlett R; McLean C; Lewis V; Collins SJ JAMA Neurol; 2013 Sep; 70(9):1180-5. PubMed ID: 23857164 [TBL] [Abstract][Full Text] [Related]
8. Linkage of the Indiana kindred of Gerstmann-Sträussler-Scheinker disease to the prion protein gene. Dlouhy SR; Hsiao K; Farlow MR; Foroud T; Conneally PM; Johnson P; Prusiner SB; Hodes ME; Ghetti B Nat Genet; 1992 Apr; 1(1):64-7. PubMed ID: 1363809 [TBL] [Abstract][Full Text] [Related]
9. Amyloid fibrils in Gerstmann-Sträussler-Scheinker disease (Indiana and Swedish kindreds) express only PrP peptides encoded by the mutant allele. Tagliavini F; Prelli F; Porro M; Rossi G; Giaccone G; Farlow MR; Dlouhy SR; Ghetti B; Bugiani O; Frangione B Cell; 1994 Nov; 79(4):695-703. PubMed ID: 7954833 [TBL] [Abstract][Full Text] [Related]
10. A novel PRNP Y218N mutation in Gerstmann-Sträussler-Scheinker disease with neurofibrillary degeneration. Alzualde A; Indakoetxea B; Ferrer I; Moreno F; Barandiaran M; Gorostidi A; Estanga A; Ruiz I; Calero M; van Leeuwen FW; Atares B; Juste R; Rodriguez-Martínez AB; López de Munain A J Neuropathol Exp Neurol; 2010 Aug; 69(8):789-800. PubMed ID: 20613639 [TBL] [Abstract][Full Text] [Related]
11. Prion protein preamyloid and amyloid deposits in Gerstmann-Sträussler-Scheinker disease, Indiana kindred. Giaccone G; Verga L; Bugiani O; Frangione B; Serban D; Prusiner SB; Farlow MR; Ghetti B; Tagliavini F Proc Natl Acad Sci U S A; 1992 Oct; 89(19):9349-53. PubMed ID: 1357663 [TBL] [Abstract][Full Text] [Related]
12. Dominantly inherited prion protein cerebral amyloidoses - a modern view of Gerstmann-Sträussler-Scheinker. Ghetti B; Piccardo P; Zanusso G Handb Clin Neurol; 2018; 153():243-269. PubMed ID: 29887140 [TBL] [Abstract][Full Text] [Related]
13. Variable phenotype in a P102L Gerstmann-Sträussler-Scheinker Italian family. De Michele G; Pocchiari M; Petraroli R; Manfredi M; Caneve G; Coppola G; Casali C; Saccà F; Piccardo P; Salvatore E; Berardelli A; Orio M; Barbieri F; Ghetti B; Filla A Can J Neurol Sci; 2003 Aug; 30(3):233-6. PubMed ID: 12945948 [TBL] [Abstract][Full Text] [Related]
14. Gerstmann-Sträussler-Scheinker Disease with F198S Mutation Induces Independent Tau and Prion Protein Pathologies in Bank Voles. Bruno R; Pirisinu L; Riccardi G; D'Agostino C; De Cecco E; Legname G; Cardone F; Gambetti P; Nonno R; Agrimi U; Di Bari MA Biomolecules; 2022 Oct; 12(10):. PubMed ID: 36291746 [TBL] [Abstract][Full Text] [Related]
15. Hereditary prion protein amyloidoses. Ghetti B; Tagliavini F; Takao M; Bugiani O; Piccardo P Clin Lab Med; 2003 Mar; 23(1):65-85, viii. PubMed ID: 12733425 [TBL] [Abstract][Full Text] [Related]
16. A new PRNP mutation (G131V) associated with Gerstmann-Sträussler-Scheinker disease. Panegyres PK; Toufexis K; Kakulas BA; Cernevakova L; Brown P; Ghetti B; Piccardo P; Dlouhy SR Arch Neurol; 2001 Nov; 58(11):1899-902. PubMed ID: 11709001 [TBL] [Abstract][Full Text] [Related]
17. A second case of Gerstmann-Sträussler-Scheinker disease linked to the G131V mutation in the prion protein gene in a Dutch patient. Jansen C; Parchi P; Capellari S; Strammiello R; Dopper EG; van Swieten JC; Kamphorst W; Rozemuller AJ J Neuropathol Exp Neurol; 2011 Aug; 70(8):698-702. PubMed ID: 21760536 [TBL] [Abstract][Full Text] [Related]
18. Hyperphosphorylated tau deposition parallels prion protein burden in a case of Gerstmann-Sträussler-Scheinker syndrome P102L mutation complicated with dementia. Ishizawa K; Komori T; Shimazu T; Yamamoto T; Kitamoto T; Shimazu K; Hirose T Acta Neuropathol; 2002 Oct; 104(4):342-50. PubMed ID: 12200619 [TBL] [Abstract][Full Text] [Related]
19. A new point mutation of the PRNP gene in Gerstmann-Sträussler-Scheinker case in Poland. Bratosiewicz J; Barcikowska M; Cervenakowa L; Brown P; Gajdusek DC; Liberski PP Folia Neuropathol; 2000; 38(4):164-6. PubMed ID: 11693719 [TBL] [Abstract][Full Text] [Related]
20. Gerstmann-Sträussler-Scheinker disease. II. Neurofibrillary tangles and plaques with PrP-amyloid coexist in an affected family. Ghetti B; Tagliavini F; Masters CL; Beyreuther K; Giaccone G; Verga L; Farlow MR; Conneally PM; Dlouhy SR; Azzarelli B Neurology; 1989 Nov; 39(11):1453-61. PubMed ID: 2573006 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]