236 related articles for article (PubMed ID: 7946341)
1. A mutant neurofilament subunit causes massive, selective motor neuron death: implications for the pathogenesis of human motor neuron disease.
Lee MK; Marszalek JR; Cleveland DW
Neuron; 1994 Oct; 13(4):975-88. PubMed ID: 7946341
[TBL] [Abstract][Full Text] [Related]
2. Increased expression of neurofilament subunit NF-L produces morphological alterations that resemble the pathology of human motor neuron disease.
Xu Z; Cork LC; Griffin JW; Cleveland DW
Cell; 1993 Apr; 73(1):23-33. PubMed ID: 8462100
[TBL] [Abstract][Full Text] [Related]
3. Involvement of neurofilaments in motor neuron disease.
Xu Z; Cork LC; Griffin JW; Cleveland DW
J Cell Sci Suppl; 1993; 17():101-8. PubMed ID: 8144684
[TBL] [Abstract][Full Text] [Related]
4. Human midsized neurofilament subunit induces motor neuron disease in transgenic mice.
Gama Sosa MA; Friedrich VL; DeGasperi R; Kelley K; Wen PH; Senturk E; Lazzarini RA; Elder GA
Exp Neurol; 2003 Nov; 184(1):408-19. PubMed ID: 14637110
[TBL] [Abstract][Full Text] [Related]
5. Neurofilament subunit NF-H modulates axonal diameter by selectively slowing neurofilament transport.
Marszalek JR; Williamson TL; Lee MK; Xu Z; Hoffman PN; Becher MW; Crawford TO; Cleveland DW
J Cell Biol; 1996 Nov; 135(3):711-24. PubMed ID: 8909545
[TBL] [Abstract][Full Text] [Related]
6. Bcl-2 overexpression does not protect neurons from mutant neurofilament-mediated motor neuron degeneration.
Houseweart MK; Cleveland DW
J Neurosci; 1999 Aug; 19(15):6446-56. PubMed ID: 10414973
[TBL] [Abstract][Full Text] [Related]
7. Ultrastructural evidence of neurofilament involvement in immune-mediated motor neuron injury.
Liu YL; Guo YS; Xu L; Wu SY; Wu DX; Yang C; Li CY
Neurol Res; 2008 Nov; 30(9):990-4. PubMed ID: 18662498
[TBL] [Abstract][Full Text] [Related]
8. Formation of intermediate filament protein aggregates with disparate effects in two transgenic mouse models lacking the neurofilament light subunit.
Beaulieu JM; Jacomy H; Julien JP
J Neurosci; 2000 Jul; 20(14):5321-8. PubMed ID: 10884316
[TBL] [Abstract][Full Text] [Related]
9. Disruption of dynein/dynactin inhibits axonal transport in motor neurons causing late-onset progressive degeneration.
LaMonte BH; Wallace KE; Holloway BA; Shelly SS; Ascaño J; Tokito M; Van Winkle T; Howland DS; Holzbaur EL
Neuron; 2002 May; 34(5):715-27. PubMed ID: 12062019
[TBL] [Abstract][Full Text] [Related]
10. Sequence variants in human neurofilament proteins: absence of linkage to familial amyotrophic lateral sclerosis.
Vechio JD; Bruijn LI; Xu Z; Brown RH; Cleveland DW
Ann Neurol; 1996 Oct; 40(4):603-10. PubMed ID: 8871580
[TBL] [Abstract][Full Text] [Related]
11. Selective Motor Neuron Resistance and Recovery in a New Inducible Mouse Model of TDP-43 Proteinopathy.
Spiller KJ; Cheung CJ; Restrepo CR; Kwong LK; Stieber AM; Trojanowski JQ; Lee VM
J Neurosci; 2016 Jul; 36(29):7707-17. PubMed ID: 27445147
[TBL] [Abstract][Full Text] [Related]
12. Extra neurofilament NF-L subunits rescue motor neuron disease caused by overexpression of the human NF-H gene in mice.
Meier J; Couillard-Després S; Jacomy H; Gravel C; Julien JP
J Neuropathol Exp Neurol; 1999 Oct; 58(10):1099-110. PubMed ID: 10515233
[TBL] [Abstract][Full Text] [Related]
13. Mechanisms of selective motor neuron death in transgenic mouse models of motor neuron disease.
Cleveland DW; Bruijn LI; Wong PC; Marszalek JR; Vechio JD; Lee MK; Xu XS; Borchelt DR; Sisodia SS; Price DL
Neurology; 1996 Oct; 47(4 Suppl 2):S54-61; discussion S61-2. PubMed ID: 8858052
[TBL] [Abstract][Full Text] [Related]
14. Defective axonal transport in a transgenic mouse model of amyotrophic lateral sclerosis.
Collard JF; Côté F; Julien JP
Nature; 1995 May; 375(6526):61-4. PubMed ID: 7536898
[TBL] [Abstract][Full Text] [Related]
15. RNA-binding protein is involved in aggregation of light neurofilament protein and is implicated in the pathogenesis of motor neuron degeneration.
Lin H; Zhai J; Schlaepfer WW
Hum Mol Genet; 2005 Dec; 14(23):3643-59. PubMed ID: 16236762
[TBL] [Abstract][Full Text] [Related]
16. Mechanisms of selective motor neuron death in ALS: insights from transgenic mouse models of motor neuron disease.
Bruijn LI; Cleveland DW
Neuropathol Appl Neurobiol; 1996 Oct; 22(5):373-87. PubMed ID: 8930947
[TBL] [Abstract][Full Text] [Related]
17. Neurofilaments and orthograde transport are reduced in ventral root axons of transgenic mice that express human SOD1 with a G93A mutation.
Zhang B; Tu P; Abtahian F; Trojanowski JQ; Lee VM
J Cell Biol; 1997 Dec; 139(5):1307-15. PubMed ID: 9382875
[TBL] [Abstract][Full Text] [Related]
18. Mice overexpressing the human neurofilament heavy gene as a model of ALS.
Julien JP; Côté F; Collard JF
Neurobiol Aging; 1995; 16(3):487-90; discussion 490-2. PubMed ID: 7566355
[TBL] [Abstract][Full Text] [Related]
19. Disruption of neurofilament network with aggregation of light neurofilament protein: a common pathway leading to motor neuron degeneration due to Charcot-Marie-Tooth disease-linked mutations in NFL and HSPB1.
Zhai J; Lin H; Julien JP; Schlaepfer WW
Hum Mol Genet; 2007 Dec; 16(24):3103-16. PubMed ID: 17881652
[TBL] [Abstract][Full Text] [Related]
20. Mitochondrial and axonal abnormalities precede disruption of the neurofilament network in a model of charcot-marie-tooth disease type 2E and are prevented by heat shock proteins in a mutant-specific fashion.
Tradewell ML; Durham HD; Mushynski WE; Gentil BJ
J Neuropathol Exp Neurol; 2009 Jun; 68(6):642-52. PubMed ID: 19458545
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]