136 related articles for article (PubMed ID: 8051938)
1. Mitochondrial creatine kinase activity in patients with disturbed energy generation in muscle mitochondria.
Smeitink J; Ruitenbeek W; Sengers R; Wevers R; van Lith T; Trijbels F
J Inherit Metab Dis; 1994; 17(1):67-73. PubMed ID: 8051938
[TBL] [Abstract][Full Text] [Related]
2. Variations of muscle mitochondrial creatine kinase activity in mitochondrial diseases.
Bouzidi MF; Enjolras N; Carrier H; Vial C; Lopez-Mediavilla C; Burt-Pichat B; Couthon F; Godinot C
Biochim Biophys Acta; 1996 Jun; 1316(2):61-70. PubMed ID: 8672552
[TBL] [Abstract][Full Text] [Related]
3. Maintained coupling of oxidative phosphorylation to creatine kinase activity in sarcomeric mitochondrial creatine kinase-deficient mice.
Boehm E; Veksler V; Mateo P; Lenoble C; Wieringa B; Ventura-Clapier R
J Mol Cell Cardiol; 1998 May; 30(5):901-12. PubMed ID: 9618231
[TBL] [Abstract][Full Text] [Related]
4. [Mitochondrial myopathies and encephalomyopathies. Neuromuscular and central nervous system diseases caused by defects in mitochondrial oxidative metabolism].
Siemes H
Monatsschr Kinderheilkd; 1985 Nov; 133(11):798-805. PubMed ID: 3935918
[TBL] [Abstract][Full Text] [Related]
5. Deficiency of the adenine nucleotide translocator in muscle of a patient with myopathy and lactic acidosis: a new mitochondrial defect.
Bakker HD; Scholte HR; Van den Bogert C; Ruitenbeek W; Jeneson JA; Wanders RJ; Abeling NG; Dorland B; Sengers RC; Van Gennip AH
Pediatr Res; 1993 Apr; 33(4 Pt 1):412-7. PubMed ID: 8479824
[TBL] [Abstract][Full Text] [Related]
6. Mitochondrial creatine kinase containing crystals, creatine content and mitochondrial creatine kinase activity in chronic progressive external ophthalmoplegia.
Smeitink J; Stadhouders A; Sengers R; Ruitenbeek W; Wevers R; ter Laak H; Trijbels F
Neuromuscul Disord; 1992; 2(1):35-40. PubMed ID: 1525556
[TBL] [Abstract][Full Text] [Related]
7. Heterogeneity of mitochondrial creatine kinase.
Kanemitsu F; Kageoka T; Kira S
J Chromatogr B Analyt Technol Biomed Life Sci; 2004 Jul; 806(2):95-100. PubMed ID: 15171917
[TBL] [Abstract][Full Text] [Related]
8. A method for quantitative measurement of mitochondrial creatine kinase in human skeletal muscle.
Smeitink J; Wevers R; Hulshof J; Ruitenbeek W; van Lith T; Sengers R; Trijbels F; Korenke C; Wallimann T
Ann Clin Biochem; 1992 Mar; 29 ( Pt 2)():196-201. PubMed ID: 1626924
[TBL] [Abstract][Full Text] [Related]
9. Mitochondrial creatine kinase: a major constituent of pathological inclusions seen in mitochondrial myopathies.
Stadhouders AM; Jap PH; Winkler HP; Eppenberger HM; Wallimann T
Proc Natl Acad Sci U S A; 1994 May; 91(11):5089-93. PubMed ID: 8197190
[TBL] [Abstract][Full Text] [Related]
10. Deficiency of the reduced nicotinamide adenine dinucleotide dehydrogenase component of complex I of mitochondrial electron transport. Fatal infantile lactic acidosis and hypermetabolism with skeletal-cardiac myopathy and encephalopathy.
Hoppel CL; Kerr DS; Dahms B; Roessmann U
J Clin Invest; 1987 Jul; 80(1):71-7. PubMed ID: 3110216
[TBL] [Abstract][Full Text] [Related]
11. Mitochondrial creatine kinase is a prime target of peroxynitrite-induced modification and inactivation.
Stachowiak O; Dolder M; Wallimann T; Richter C
J Biol Chem; 1998 Jul; 273(27):16694-9. PubMed ID: 9642223
[TBL] [Abstract][Full Text] [Related]
12. Mitochondrial creatine kinase isoform expression does not correlate with its mode of action.
Anflous K; Veksler V; Mateo P; Samson F; Saks V; Ventura-Clapier R
Biochem J; 1997 Feb; 322 ( Pt 1)(Pt 1):73-8. PubMed ID: 9078245
[TBL] [Abstract][Full Text] [Related]
13. Defects in the mitochondrial energy metabolism outside the respiratory chain and the pyruvate dehydrogenase complex.
Trijbels FJ; Ruitenbeek W; Huizing M; Wendel U; Smeitink JA; Sengers RC
Mol Cell Biochem; 1997 Sep; 174(1-2):243-7. PubMed ID: 9309695
[TBL] [Abstract][Full Text] [Related]
14. Ethylmalonic acid inhibits mitochondrial creatine kinase activity from cerebral cortex of young rats in vitro.
Leipnitz G; Schuck PF; Ribeiro CA; Dalcin KB; Assis DR; Barschak AG; Pulrolnik V; Wannmacher CM; Wyse AT; Wajner M
Neurochem Res; 2003 May; 28(5):771-7. PubMed ID: 12716029
[TBL] [Abstract][Full Text] [Related]
15. Interaction of mitochondrial creatine kinase with model membranes. A monolayer study.
Rojo M; Hovius R; Demel R; Wallimann T; Eppenberger HM; Nicolay K
FEBS Lett; 1991 Apr; 281(1-2):123-9. PubMed ID: 2015883
[TBL] [Abstract][Full Text] [Related]
16. Skeletal muscles of mice deficient in muscle creatine kinase lack burst activity.
van Deursen J; Heerschap A; Oerlemans F; Ruitenbeek W; Jap P; ter Laak H; Wieringa B
Cell; 1993 Aug; 74(4):621-31. PubMed ID: 8358791
[TBL] [Abstract][Full Text] [Related]
17. Maturation of mitochondrial and other isoenzymes of creatine kinase in skeletal muscle of preterm born infants.
Smeitink J; Ruitenbeek W; van Lith T; Sengers R; Trijbels F; Wevers R; Sperl W; de Graaf R
Ann Clin Biochem; 1992 May; 29 ( Pt 3)():302-6. PubMed ID: 1319128
[TBL] [Abstract][Full Text] [Related]
18. Mitochondrial affinity for ADP is twofold lower in creatine kinase knock-out muscles. Possible role in rescuing cellular energy homeostasis.
ter Veld F; Jeneson JA; Nicolay K
FEBS J; 2005 Feb; 272(4):956-65. PubMed ID: 15691329
[TBL] [Abstract][Full Text] [Related]
19. Variation in mitochondrial DNA levels in muscle from normal controls. Is depletion of mtDNA in patients with mitochondrial myopathy a distinct clinical syndrome.
Poulton J; Sewry C; Potter CG; Bougeron T; Chretien D; Wijburg FA; Morten KJ; Brown G
J Inherit Metab Dis; 1995; 18(1):4-20. PubMed ID: 7623440
[TBL] [Abstract][Full Text] [Related]
20. Mitochondria and diabetes. Genetic, biochemical, and clinical implications of the cellular energy circuit.
Gerbitz KD; Gempel K; Brdiczka D
Diabetes; 1996 Feb; 45(2):113-26. PubMed ID: 8549853
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
