169 related articles for article (PubMed ID: 8105143)
21. Adrenoleukodystrophy. The chain shortening of erucic acid (22:1(n-9)) and adrenic acid (22:4(n-6)) is deficient in neonatal adrenoleukodystrophy and normal in X-linked adrenoleukodistrophy skin fibroblasts.
Christensen E; Grønn M; Hagve TA; Kase BF; Christophersen BO
Biochim Biophys Acta; 1989 Mar; 1002(1):79-83. PubMed ID: 2538146
[TBL] [Abstract][Full Text] [Related]
22. Adrenoleukodystrophy: impaired oxidation of fatty acids due to peroxisomal lignoceroyl-CoA ligase deficiency.
Lazo O; Contreras M; Bhushan A; Stanley W; Singh I
Arch Biochem Biophys; 1989 May; 270(2):722-8. PubMed ID: 2705786
[TBL] [Abstract][Full Text] [Related]
23. Peroxisomal abnormality in fibroblasts from involved skin of CHILD syndrome. Case study and review of peroxisomal disorders in relation to skin disease.
Emami S; Rizzo WB; Hanley KP; Taylor JM; Goldyne ME; Williams ML
Arch Dermatol; 1992 Sep; 128(9):1213-22. PubMed ID: 1519936
[TBL] [Abstract][Full Text] [Related]
24. Fatty acid metabolism in liver of rats treated with hypolipidemic sulphur-substituted fatty acid analogues.
Asiedu D; Aarsland A; Skorve J; Svardal AM; Berge RK
Biochim Biophys Acta; 1990 May; 1044(2):211-21. PubMed ID: 1971517
[TBL] [Abstract][Full Text] [Related]
25. Peroxisome proliferating sulphur- and oxy-substituted fatty acid analogues are activated to acyl coenzyme A thioesters.
Aarsland A; Berge RK
Biochem Pharmacol; 1991 Jan; 41(1):53-61. PubMed ID: 1670918
[TBL] [Abstract][Full Text] [Related]
26. Characterization of acyl-CoA thioesterase activity in isolated rat liver peroxisomes. Partial purification and characterization of a long-chain acyl-CoA thioesterase.
Wilcke M; Alexson SE
Eur J Biochem; 1994 Jun; 222(3):803-11. PubMed ID: 7913034
[TBL] [Abstract][Full Text] [Related]
27. The presence of acyl-CoA hydrolase in rat brown-adipose-tissue peroxisomes.
Alexson SE; Osmundsen H; Berge RK
Biochem J; 1989 Aug; 262(1):41-6. PubMed ID: 2573347
[TBL] [Abstract][Full Text] [Related]
28. Effects of clofibric acid and tiadenol on cytosolic long-chain acyl-CoA hydrolase and peroxisomal beta-oxidation in liver and extrahepatic tissues of rats.
Katoh H; Kawashima Y; Watanuki H; Kozuka H; Isono H
Biochim Biophys Acta; 1987 Jul; 920(2):171-9. PubMed ID: 2886154
[TBL] [Abstract][Full Text] [Related]
29. Abnormal profiles of polyunsaturated fatty acids in the brain, liver, kidney and retina of patients with peroxisomal disorders.
Martinez M
Brain Res; 1992 Jun; 583(1-2):171-82. PubMed ID: 1504825
[TBL] [Abstract][Full Text] [Related]
30. Effects of sodium 2-[5-(4-chlorophenyl)pentyl]-oxirane-2-carboxylate (POCA) on fatty acid oxidation in fibroblasts from patients with peroxisomal diseases.
Suzuki Y; Shimozawa N; Yajima S; Yamaguchi S; Orii T; Hashimoto T
Biochem Pharmacol; 1991 Feb; 41(3):453-6. PubMed ID: 1994902
[TBL] [Abstract][Full Text] [Related]
31. Peroxisomal very long-chain fatty acid beta-oxidation in human skin fibroblasts: activity in Zellweger syndrome and other peroxisomal disorders.
Wanders RJ; van Roermund CW; van Wijland MJ; Heikoop J; Schutgens RB; Schram AW; Tager JM; van den Bosch H; Poll-Thé BT; Saudubray JM
Clin Chim Acta; 1987 Jul; 166(2-3):255-63. PubMed ID: 2441904
[TBL] [Abstract][Full Text] [Related]
32. Peroxisomal beta-oxidation is a significant pathway for catabolism of fatty acids in a marine teleost.
Crockett EL; Sidell BD
Am J Physiol; 1993 May; 264(5 Pt 2):R1004-9. PubMed ID: 8098915
[TBL] [Abstract][Full Text] [Related]
33. Fatty alcohol accumulation in the autosomal recessive form of rhizomelic chondrodysplasia punctata.
Rizzo WB; Craft DA; Judd LL; Moser HW; Moser AB
Biochem Med Metab Biol; 1993 Aug; 50(1):93-102. PubMed ID: 8373640
[TBL] [Abstract][Full Text] [Related]
34. Hyperpipecolic acidaemia: a diagnostic tool for peroxisomal disorders.
Peduto A; Baumgartner MR; Verhoeven NM; Rabier D; Spada M; Nassogne MC; Poll-The BT; Bonetti G; Jakobs C; Saudubray JM
Mol Genet Metab; 2004 Jul; 82(3):224-30. PubMed ID: 15234336
[TBL] [Abstract][Full Text] [Related]
35. Alkylthio acetic acids (3-thia fatty acids)--a new group of non-beta-oxidizable peroxisome-inducing fatty acid analogues--II. Dose-response studies on hepatic peroxisomal- and mitochondrial changes and long-chain fatty acid metabolizing enzymes in rats.
Berge RK; Aarsland A; Kryvi H; Bremer J; Aarsaether N
Biochem Pharmacol; 1989 Nov; 38(22):3969-79. PubMed ID: 2574577
[TBL] [Abstract][Full Text] [Related]
36. Rapid stimulation of liver palmitoyl-CoA synthetase, carnitine palmitoyltransferase and glycerophosphate acyltransferase compared to peroxisomal beta-oxidation and palmitoyl-CoA hydrolase in rats fed high-fat diets.
Berge RK; Nilsson A; Husøy AM
Biochim Biophys Acta; 1988 Jun; 960(3):417-26. PubMed ID: 2898261
[TBL] [Abstract][Full Text] [Related]
37. Phytanic acid alpha-oxidation and complementation analysis of classical Refsum and peroxisomal disorders.
Poll-The BT; Skjeldal OH; Stokke O; Poulos A; Demaugre F; Saudubray JM
Hum Genet; 1989 Jan; 81(2):175-81. PubMed ID: 2463966
[TBL] [Abstract][Full Text] [Related]
38. Metabolism of saturated and polyunsaturated very-long-chain fatty acids in fibroblasts from patients with defects in peroxisomal beta-oxidation.
Street JM; Singh H; Poulos A
Biochem J; 1990 Aug; 269(3):671-7. PubMed ID: 2117919
[TBL] [Abstract][Full Text] [Related]
39. Peroxisomal very long chain fatty acid beta-oxidation activity is determined by the level of adrenodeukodystrophy protein (ALDP) expression.
Braiterman LT; Watkins PA; Moser AB; Smith KD
Mol Genet Metab; 1999 Feb; 66(2):91-9. PubMed ID: 10068511
[TBL] [Abstract][Full Text] [Related]
40. Cytoplasmic catalase and ghostlike peroxisomes in the liver from a child with atypical chondrodysplasia punctata.
Espeel M; Heikoop JC; Smeitink JA; Beemer FA; De Craemer D; Van den Berg M; Hashimoto T; Wanders RJ; Schutgens RB; Poll-The BT
Ultrastruct Pathol; 1993; 17(6):623-36. PubMed ID: 8122328
[TBL] [Abstract][Full Text] [Related]
[Previous] [Next] [New Search]
