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2. A new myasthenic syndrome with end-plate acetylcholinesterase deficiency, small nerve terminals, and reduced acetylcholine release. Engel AG; Lambert EH; Gomez MR Ann Neurol; 1977 Apr; 1(4):315-30. PubMed ID: 214017 [TBL] [Abstract][Full Text] [Related]
3. Patients with congenital myasthenia associated with end-plate acetylcholinesterase deficiency show normal sequence, mRNA splicing, and assembly of catalytic subunits. Camp S; Bon S; Li Y; Getman DK; Engel AG; Massoulié J; Taylor P J Clin Invest; 1995 Jan; 95(1):333-40. PubMed ID: 7814634 [TBL] [Abstract][Full Text] [Related]
4. Three novel COLQ mutations and variation of phenotypic expressivity due to G240X. Shapira YA; Sadeh ME; Bergtraum MP; Tsujino A; Ohno K; Shen XM; Brengman J; Edwardson S; Matoth I; Engel AG Neurology; 2002 Feb; 58(4):603-9. PubMed ID: 11865139 [TBL] [Abstract][Full Text] [Related]
5. Human endplate acetylcholinesterase deficiency caused by mutations in the collagen-like tail subunit (ColQ) of the asymmetric enzyme. Ohno K; Brengman J; Tsujino A; Engel AG Proc Natl Acad Sci U S A; 1998 Aug; 95(16):9654-9. PubMed ID: 9689136 [TBL] [Abstract][Full Text] [Related]
7. The spectrum of mutations causing end-plate acetylcholinesterase deficiency. Ohno K; Engel AG; Brengman JM; Shen XM; Heidenreich F; Vincent A; Milone M; Tan E; Demirci M; Walsh P; Nakano S; Akiguchi I Ann Neurol; 2000 Feb; 47(2):162-70. PubMed ID: 10665486 [TBL] [Abstract][Full Text] [Related]
9. End-plate acetylcholinesterase deficiency associated with small nerve terminals and reduced acetylcholine release. A new syndrome. Engel AG; Lambert EH; Gomez MR Int J Neurol; 1980; 14(1):73-86. PubMed ID: 6293992 [No Abstract] [Full Text] [Related]
10. Congenital end-plate acetylcholinesterase deficiency caused by a nonsense mutation and an A-->G splice-donor-site mutation at position +3 of the collagenlike-tail-subunit gene (COLQ): how does G at position +3 result in aberrant splicing? Ohno K; Brengman JM; Felice KJ; Cornblath DR; Engel AG Am J Hum Genet; 1999 Sep; 65(3):635-44. PubMed ID: 10441569 [TBL] [Abstract][Full Text] [Related]
11. Two novel mutations in the COLQ gene cause endplate acetylcholinesterase deficiency. Ishigaki K; Nicolle D; Krejci E; Leroy JP; Koenig J; Fardeau M; Eymard B; Hantaï D Neuromuscul Disord; 2003 Mar; 13(3):236-44. PubMed ID: 12609505 [TBL] [Abstract][Full Text] [Related]
12. Butyrylcholinesterase and acetylcholinesterase activity and quantal transmitter release at normal and acetylcholinesterase knockout mouse neuromuscular junctions. Minic J; Chatonnet A; Krejci E; Molgó J Br J Pharmacol; 2003 Jan; 138(1):177-87. PubMed ID: 12522088 [TBL] [Abstract][Full Text] [Related]
13. Targeting acetylcholinesterase to the neuromuscular synapse. Rotundo RL; Rossi SG; Kimbell LM; Ruiz C; Marrero E Chem Biol Interact; 2005 Dec; 157-158():15-21. PubMed ID: 16289417 [TBL] [Abstract][Full Text] [Related]
14. Butyrylcholinesterase and the control of synaptic responses in acetylcholinesterase knockout mice. Girard E; Bernard V; Minic J; Chatonnet A; Krejci E; Molgó J Life Sci; 2007 May; 80(24-25):2380-5. PubMed ID: 17467011 [TBL] [Abstract][Full Text] [Related]
15. A newly recognized congenital myasthenic syndrome attributed to a prolonged open time of the acetylcholine-induced ion channel. Engel AG; Lambert EH; Mulder DM; Torres CF; Sahashi K; Bertorini TE; Whitaker JN Ann Neurol; 1982 Jun; 11(6):553-69. PubMed ID: 6287911 [TBL] [Abstract][Full Text] [Related]
16. Congenital myasthenic syndromes: I. Deficiency and short open-time of the acetylcholine receptor. Engel AG; Nagel A; Walls TJ; Harper CM; Waisburg HA Muscle Nerve; 1993 Dec; 16(12):1284-92. PubMed ID: 8232383 [TBL] [Abstract][Full Text] [Related]
17. Dermatan sulfate and de-sulfated heparin solubilized collagen-tailed acetylcholinesterase from the rat neuromuscular junction. von Bernhardi R; Inestrosa NC Brain Res; 1990 Oct; 529(1-2):91-5. PubMed ID: 2282507 [TBL] [Abstract][Full Text] [Related]
18. A major portion of synaptic basal lamina acetylcholinesterase is detached by high salt- and heparin-containing buffers from rat diaphragm muscle and Torpedo electric organ. Casanueva OI; García-Huidobro T; Campos EO; Aldunate R; Garrido J; Inestrosa NC J Biol Chem; 1998 Feb; 273(7):4258-65. PubMed ID: 9461624 [TBL] [Abstract][Full Text] [Related]
19. Novel congenital myasthenic syndromes associated with defects in quantal release. Milone M; Fukuda T; Shen XM; Tsujino A; Brengman J; Engel AG Neurology; 2006 Apr; 66(8):1223-9. PubMed ID: 16525123 [TBL] [Abstract][Full Text] [Related]
20. Intracellular acetylcholinesterase of adult rat myofibers is more concentrated in endplate than non-endplate regions. Donoso JA; Stiles JR; Fernandez HL J Neurosci Res; 1987; 17(2):146-53. PubMed ID: 3586068 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]