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3. Molecular analysis of dihydropteridine reductase deficiency: identification of two novel mutations in Japanese patients. Ikeda H; Matsubara Y; Mikami H; Kure S; Owada M; Gough T; Smooker PM; Dobbs M; Dahl HH; Cotton RG; Narisawa K Hum Genet; 1997 Oct; 100(5-6):637-42. PubMed ID: 9341885 [TBL] [Abstract][Full Text] [Related]
4. Dihydropteridine reductase deficiency: physical structure of the QDPR gene, identification of two new mutations and genotype-phenotype correlations. Dianzani I; de Sanctis L; Smooker PM; Gough TJ; Alliaudi C; Brusco A; Spada M; Blau N; Dobos M; Zhang HP; Yang N; Ponzone A; Armarego WL; Cotton RG Hum Mutat; 1998; 12(4):267-73. PubMed ID: 9744478 [TBL] [Abstract][Full Text] [Related]
5. The spectrum of mutations in dihydropteridine reductase deficiency. Smooker PM; Howells DW; Dianzani I; Cotton RG Adv Exp Med Biol; 1993; 338():135-8. PubMed ID: 8304097 [No Abstract] [Full Text] [Related]
6. Role of aspartate-37 in determining cofactor specificity and binding in rat liver dihydropteridine reductase. Matthews DA; Varughese KI; Skinner M; Xuong NH; Hoch J; Trach K; Schneider M; Bray T; Whiteley JM Arch Biochem Biophys; 1991 Jun; 287(2):234-9. PubMed ID: 1898002 [TBL] [Abstract][Full Text] [Related]
7. Insertion of an extra codon for threonine is a cause of dihydropteridine reductase deficiency. Howells DW; Forrest SM; Dahl HH; Cotton RG Am J Hum Genet; 1990 Aug; 47(2):279-85. PubMed ID: 2116088 [TBL] [Abstract][Full Text] [Related]
8. [Diagnosis, treatment and gene mutation analysis of the first case with dihydropteridine reductase deficiency in the mainland of China]. Ye J; Qiu WJ; Han LS; Zhang HW; Zhou JD; Gao XL; Wang Y; Gu XF Zhonghua Er Ke Za Zhi; 2008 Apr; 46(4):281-5. PubMed ID: 19099731 [TBL] [Abstract][Full Text] [Related]
9. Molecular analysis of 16 Turkish families with DHPR deficiency using denaturing gradient gel electrophoresis (DGGE). Romstad A; Kalkanoğlu HS; Coşkun T; Demirkol M; Tokatli A; Dursun A; Baykal T; Ozalp I; Guldberg P; Güttler F Hum Genet; 2000 Dec; 107(6):546-53. PubMed ID: 11153907 [TBL] [Abstract][Full Text] [Related]
10. Structural and mechanistic implications of incorporating naturally occurring aberrant mutations of human dihydropteridine reductase into a rat model. Varughese KI; Xuong NH; Whiteley JM Int J Pept Protein Res; 1994 Sep; 44(3):278-87. PubMed ID: 7822105 [TBL] [Abstract][Full Text] [Related]
11. A mutation causing DHPR deficiency results in a frameshift and a secondary splicing defect. Smooker PM; Christodoulou J; McInnes RR; Cotton RG J Med Genet; 1995 Mar; 32(3):220-3. PubMed ID: 7783174 [TBL] [Abstract][Full Text] [Related]
12. Molecular characterization of Drosophila melanogaster dihydropteridine reductase. Park D; Park S; Yim J Biochim Biophys Acta; 2000 Jun; 1492(1):247-51. PubMed ID: 11004497 [TBL] [Abstract][Full Text] [Related]
13. Two new mutations in the dihydropteridine reductase gene in patients with tetrahydrobiopterin deficiency. Dianzani I; Howells DW; Ponzone A; Saleeba JA; Smooker PM; Cotton RG J Med Genet; 1993 Jun; 30(6):465-9. PubMed ID: 8326489 [TBL] [Abstract][Full Text] [Related]
14. Human dihydropteridine reductase: characterisation of a cDNA clone and its use in analysis of patients with dihydropteridine reductase deficiency. Dahl HH; Hutchison W; McAdam W; Wake S; Morgan FJ; Cotton RG Nucleic Acids Res; 1987 Mar; 15(5):1921-32. PubMed ID: 3031582 [TBL] [Abstract][Full Text] [Related]
15. A series of mutations in the dihydropteridine reductase gene resulting in either abnormal RNA splicing or DHPR protein defects. Mutations in brief no. 244. Online. Smooker PM; Gough TJ; Cotton RG; Alliaudi C; de Sanctis L; Dianzani I Hum Mutat; 1999; 13(6):503-4. PubMed ID: 10408783 [TBL] [Abstract][Full Text] [Related]
16. Heterogeneity of the molecular defect in human dihydropteridine reductase deficiency. Firgaira FA; Choo KH; Cotton RG; Danks DM Biochem J; 1981 Sep; 198(3):677-82. PubMed ID: 7326033 [TBL] [Abstract][Full Text] [Related]
17. The crystallographic structure of a human dihydropteridine reductase NADH binary complex expressed in Escherichia coli by a cDNA constructed from its rat homologue. Su Y; Varughese KI; Xuong NH; Bray TL; Roche DJ; Whiteley JM J Biol Chem; 1993 Dec; 268(36):26836-41. PubMed ID: 8262916 [TBL] [Abstract][Full Text] [Related]
18. Structure and expression of human dihydropteridine reductase. Lockyer J; Cook RG; Milstien S; Kaufman S; Woo SL; Ledley FD Proc Natl Acad Sci U S A; 1987 May; 84(10):3329-33. PubMed ID: 3033643 [TBL] [Abstract][Full Text] [Related]
20. Evaluation of a fetus at risk for dihydropteridine reductase deficiency by direct mutation analysis using denaturing gradient gel electrophoresis. Kalkanoglu HS; Romstad A; Coşkun T; Güttler F Prenat Diagn; 2001 Oct; 21(10):868-70. PubMed ID: 11746132 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]