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5. Mutation at the phenylalanine hydroxylase gene (PAH) and its use to document population genetic variation: the Quebec experience. Carter KC; Byck S; Waters PJ; Richards B; Nowacki PM; Laframboise R; Lambert M; Treacy E; Scriver CR Eur J Hum Genet; 1998 Jan; 6(1):61-70. PubMed ID: 9781015 [TBL] [Abstract][Full Text] [Related]
6. The phenylalanine hydroxylase locus: a marker for the history of phenylketonuria and human genetic diversity. PAH Mutation Analysis Consortium. Scriver CR; Byck S; Prevost L; Hoang L Ciba Found Symp; 1996; 197():73-90; discussion 90-6. PubMed ID: 8827369 [TBL] [Abstract][Full Text] [Related]
7. PAHdb 2003: what a locus-specific knowledgebase can do. Scriver CR; Hurtubise M; Konecki D; Phommarinh M; Prevost L; Erlandsen H; Stevens R; Waters PJ; Ryan S; McDonald D; Sarkissian C Hum Mutat; 2003 Apr; 21(4):333-44. PubMed ID: 12655543 [TBL] [Abstract][Full Text] [Related]
8. A methodological strategy for PAH genotyping in populations with a marked molecular heterogeneity of hyperphenylalaninemia. Romano V; Lio D; Calì F; Scola L; Leggio L; D'Anna C; DeLeo G; Salermo A Mol Cell Probes; 2001 Feb; 15(1):13-9. PubMed ID: 11284432 [TBL] [Abstract][Full Text] [Related]
9. The PAH gene, phenylketonuria, and a paradigm shift. Scriver CR Hum Mutat; 2007 Sep; 28(9):831-45. PubMed ID: 17443661 [TBL] [Abstract][Full Text] [Related]
10. Two missense mutations causing mild hyperphenylalaninemia associated with DNA haplotype 12. Svensson E; Eisensmith RC; Dworniczak B; von Döbeln U; Hagenfeldt L; Horst J; Woo SL Hum Mutat; 1992; 1(2):129-37. PubMed ID: 1301200 [TBL] [Abstract][Full Text] [Related]
11. In vitro expression analysis of mutations in phenylalanine hydroxylase: linking genotype to phenotype and structure to function. Waters PJ; Parniak MA; Nowacki P; Scriver CR Hum Mutat; 1998; 11(1):4-17. PubMed ID: 9450897 [TBL] [Abstract][Full Text] [Related]
12. The spectrum of phenylketonuria genotypes in the Armenian population: identification of three novel mutant PAH alleles. Kostandyan N; Britschgi C; Matevosyan A; Oganezova A; Davtyan A; Blau N; Steinmann B; Thöny B Mol Genet Metab; 2011; 104 Suppl():S93-6. PubMed ID: 21890392 [TBL] [Abstract][Full Text] [Related]
13. CpG methylation accounts for a recurrent mutation (c.1222C>T) in the human PAH gene. Murphy BC; Scriver CR; Singh SM Hum Mutat; 2006 Sep; 27(9):975. PubMed ID: 16917891 [TBL] [Abstract][Full Text] [Related]
14. In vitro and in vivo correlations for I65T and M1V mutations at the phenylalanine hydroxylase locus. John SW; Scriver CR; Laframboise R; Rozen R Hum Mutat; 1992; 1(2):147-53. PubMed ID: 1301201 [TBL] [Abstract][Full Text] [Related]
15. Phenylketonuria in The Netherlands: 93% of the mutations are detected by single-strand conformation analysis. van der Sijs-Bos CJ; Diepstraten CM; Juyn JA; Plaisier M; Giltay JC; van Spronsen FJ; Smit GP; Berger R; Smeitink JA; Poll-The BT; Ploos van Amstel JK Hum Hered; 1996; 46(4):185-90. PubMed ID: 8807319 [TBL] [Abstract][Full Text] [Related]
16. Molecular basis of phenylketonuria and related hyperphenylalaninemias: mutations and polymorphisms in the human phenylalanine hydroxylase gene. Eisensmith RC; Woo SL Hum Mutat; 1992; 1(1):13-23. PubMed ID: 1301187 [TBL] [Abstract][Full Text] [Related]
17. Genetic study of the PAH locus in the Iranian population: familial gene mutations and minihaplotypes. Razipour M; Alavinejad E; Sajedi SZ; Talebi S; Entezam M; Mohajer N; Kazemi-Sefat GE; Gharesouran J; Setoodeh A; Mohaddes Ardebili SM; Keramatipour M Metab Brain Dis; 2017 Oct; 32(5):1685-1691. PubMed ID: 28676969 [TBL] [Abstract][Full Text] [Related]
18. Mutation analysis in hyperphenylalaninemia patients from South Italy. Trunzo R; Santacroce R; D'Andrea G; Longo V; De Girolamo G; Dimatteo C; Leccese A; Lillo V; Papadia F; Margaglione M Clin Biochem; 2013 Dec; 46(18):1896-8. PubMed ID: 23792259 [TBL] [Abstract][Full Text] [Related]
19. Intra-familiar discordant PKU phenotype explained by mutation analysis in three pedigrees. Trunzo R; Santacroce R; D'Andrea G; Longo V; De Girolamo G; Dimatteo C; Leccese A; Lillo V; Papadia F; Margaglione M Clin Biochem; 2014 Feb; 47(3):233-5. PubMed ID: 24296287 [TBL] [Abstract][Full Text] [Related]
20. Predicting a clinical/biochemical phenotype for PKU/MHP patients with PAH gene mutations. Kasnauskiene J; Cimbalistiene L; Kucinskas V Genetika; 2008 Oct; 44(10):1397-403. PubMed ID: 19062537 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]