404 related articles for article (PubMed ID: 8650157)
1. A gain-of-function of an amyotrophic lateral sclerosis-associated Cu,Zn-superoxide dismutase mutant: An enhancement of free radical formation due to a decrease in Km for hydrogen peroxide.
Yim MB; Kang JH; Yim HS; Kwak HS; Chock PB; Stadtman ER
Proc Natl Acad Sci U S A; 1996 Jun; 93(12):5709-14. PubMed ID: 8650157
[TBL] [Abstract][Full Text] [Related]
2. A familial amyotrophic lateral sclerosis-associated A4V Cu, Zn-superoxide dismutase mutant has a lower Km for hydrogen peroxide. Correlation between clinical severity and the Km value.
Yim HS; Kang JH; Chock PB; Stadtman ER; Yim MB
J Biol Chem; 1997 Apr; 272(14):8861-3. PubMed ID: 9083002
[TBL] [Abstract][Full Text] [Related]
3. Release of copper ions from the familial amyotrophic lateral sclerosis-associated Cu,Zn-superoxide dismutase mutants.
Eum WS; Kang JH
Mol Cells; 1999 Feb; 9(1):110-4. PubMed ID: 10102580
[TBL] [Abstract][Full Text] [Related]
4. Expression, purification, and characterization of a familial amyotrophic lateral sclerosis-associated D90A Cu,Zn-superoxide dismutase mutant.
Kim SM; Eum WS; Kang JH
Mol Cells; 1998 Aug; 8(4):478-82. PubMed ID: 9749537
[TBL] [Abstract][Full Text] [Related]
5. Enhanced oxidative damage by the familial amyotrophic lateral sclerosis-associated Cu,Zn-superoxide dismutase mutants.
Kang JH; Eum WS
Biochim Biophys Acta; 2000 Dec; 1524(2-3):162-70. PubMed ID: 11113563
[TBL] [Abstract][Full Text] [Related]
6. Enhanced free radical generation of FALS-associated Cu,Zn-SOD mutants.
Yim MB; Yim HS; Chock PB; Stadtman ER
Neurotox Res; 1999 Dec; 1(2):91-7. PubMed ID: 12835105
[TBL] [Abstract][Full Text] [Related]
7. The free radical-generating function of a familial amyotrophic lateral sclerosis-associated D90A Cu,Zn-superoxide dismutase mutant.
Kim SM; Eum WS; Kwon OB; Kang JH
Biochem Mol Biol Int; 1998 Dec; 46(6):1191-200. PubMed ID: 9891852
[TBL] [Abstract][Full Text] [Related]
8. Glycation proceeds faster in mutated Cu, Zn-superoxide dismutases related to familial amyotrophic lateral sclerosis.
Takamiya R; Takahashi M; Myint T; Park YS; Miyazawa N; Endo T; Fujiwara N; Sakiyama H; Misonou Y; Miyamoto Y; Fujii J; Taniguchi N
FASEB J; 2003 May; 17(8):938-40. PubMed ID: 12626432
[TBL] [Abstract][Full Text] [Related]
9. Stabilization of mutant Cu/Zn superoxide dismutase (SOD1) protein by coexpressed wild SOD1 protein accelerates the disease progression in familial amyotrophic lateral sclerosis mice.
Fukada K; Nagano S; Satoh M; Tohyama C; Nakanishi T; Shimizu A; Yanagihara T; Sakoda S
Eur J Neurosci; 2001 Dec; 14(12):2032-6. PubMed ID: 11860498
[TBL] [Abstract][Full Text] [Related]
10. Reexamination of the mechanism of hydroxyl radical adducts formed from the reaction between familial amyotrophic lateral sclerosis-associated Cu,Zn superoxide dismutase mutants and H2O2.
Singh RJ; Karoui H; Gunther MR; Beckman JS; Mason RP; Kalyanaraman B
Proc Natl Acad Sci U S A; 1998 Jun; 95(12):6675-80. PubMed ID: 9618471
[TBL] [Abstract][Full Text] [Related]
11. Characterization of wild-type and amyotrophic lateral sclerosis-related mutant Cu,Zn-superoxide dismutases overproduced in baculovirus-infected insect cells.
Fujii J; Myint T; Seo HG; Kayanoki Y; Ikeda Y; Taniguchi N
J Neurochem; 1995 Apr; 64(4):1456-61. PubMed ID: 7891072
[TBL] [Abstract][Full Text] [Related]
12. Gain in functions of mutant Cu,Zn-superoxide dismutases as a causative factor in familial amyotrophic lateral sclerosis: less reactive oxidant formation but high spontaneous aggregation and precipitation.
Okado-Matsumoto A; Myint T; Fujii J; Taniguchi N
Free Radic Res; 2000 Jul; 33(1):65-73. PubMed ID: 10826922
[TBL] [Abstract][Full Text] [Related]
13. Progressive impairment of CaV1.1 function in the skeletal muscle of mice expressing a mutant type 1 Cu/Zn superoxide dismutase (G93A) linked to amyotrophic lateral sclerosis.
Beqollari D; Romberg CF; Dobrowolny G; Martini M; Voss AA; MusarĂ² A; Bannister RA
Skelet Muscle; 2016; 6():24. PubMed ID: 27340545
[TBL] [Abstract][Full Text] [Related]
14. Human Cu/Zn superoxide dismutase (SOD1) overexpression in mice causes mitochondrial vacuolization, axonal degeneration, and premature motoneuron death and accelerates motoneuron disease in mice expressing a familial amyotrophic lateral sclerosis mutant SOD1.
Jaarsma D; Haasdijk ED; Grashorn JA; Hawkins R; van Duijn W; Verspaget HW; London J; Holstege JC
Neurobiol Dis; 2000 Dec; 7(6 Pt B):623-43. PubMed ID: 11114261
[TBL] [Abstract][Full Text] [Related]
15. Identification of three mutations in the Cu,Zn-superoxide dismutase (Cu,Zn-SOD) gene with familial amyotrophic lateral sclerosis: transduction of human Cu,Zn-SOD into PC12 cells by HIV-1 TAT protein basic domain.
Chou CM; Huang CJ; Shih CM; Chen YP; Liu TP; Chen CT
Ann N Y Acad Sci; 2005 May; 1042():303-13. PubMed ID: 15965076
[TBL] [Abstract][Full Text] [Related]
16. The familial amyotrophic lateral sclerosis-associated amino acid substitutions E100G, G93A, and G93R do not influence the rate of inactivation of copper- and zinc-containing superoxide dismutase by H2O2.
Liochev SI; Chen LL; Hallewell RA; Fridovich I
Arch Biochem Biophys; 1998 Apr; 352(2):237-9. PubMed ID: 9587411
[TBL] [Abstract][Full Text] [Related]
17. Reactions of hydrogen peroxide with familial amyotrophic lateral sclerosis mutant human copper-zinc superoxide dismutases studied by pulse radiolysis.
Goto JJ; Gralla EB; Valentine JS; Cabelli DE
J Biol Chem; 1998 Nov; 273(46):30104-9. PubMed ID: 9804764
[TBL] [Abstract][Full Text] [Related]
18. Protein oxidative damage in a transgenic mouse model of familial amyotrophic lateral sclerosis.
Andrus PK; Fleck TJ; Gurney ME; Hall ED
J Neurochem; 1998 Nov; 71(5):2041-8. PubMed ID: 9798929
[TBL] [Abstract][Full Text] [Related]
19. Superoxide dismutase concentration and activity in familial amyotrophic lateral sclerosis.
Bowling AC; Barkowski EE; McKenna-Yasek D; Sapp P; Horvitz HR; Beal MF; Brown RH
J Neurochem; 1995 May; 64(5):2366-9. PubMed ID: 7722523
[TBL] [Abstract][Full Text] [Related]
20. Superoxide-dependent peroxidase activity of H48Q: a superoxide dismutase variant associated with familial amyotrophic lateral sclerosis.
Liochev SI; Chen LL; Hallewell RA; Fridovich I
Arch Biochem Biophys; 1997 Oct; 346(2):263-8. PubMed ID: 9343373
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]