162 related articles for article (PubMed ID: 8714525)
1. In vitro accumulation of glucocerebroside in neuroblastoma cells: a model for study of Gaucher disease pathobiology.
Prence EM; Chaturvedi P; Newburg DS
J Neurosci Res; 1996 Feb; 43(3):365-71. PubMed ID: 8714525
[TBL] [Abstract][Full Text] [Related]
2. Macrophages exposed in vitro to conduritol B epoxide resemble Gaucher cells.
Newburg DS; Shea TB; Yatziv S; Raghavan SS; McCluer RH
Exp Mol Pathol; 1988 Jun; 48(3):317-23. PubMed ID: 3371456
[TBL] [Abstract][Full Text] [Related]
3. Glucosylceramide and Glucosylsphingosine Quantitation by Liquid Chromatography-Tandem Mass Spectrometry to Enable In Vivo Preclinical Studies of Neuronopathic Gaucher Disease.
Hamler R; Brignol N; Clark SW; Morrison S; Dungan LB; Chang HH; Khanna R; Frascella M; Valenzano KJ; Benjamin ER; Boyd RE
Anal Chem; 2017 Aug; 89(16):8288-8295. PubMed ID: 28686011
[TBL] [Abstract][Full Text] [Related]
4. beta-Glucosidase inhibition in murine peritoneal macrophages by conduritol-B-epoxide: an in vitro model of the Gaucher cell.
Newburg DS; Yatziv S; McCluer RH; Raghavan S
Biochim Biophys Acta; 1986 Jun; 877(1):121-6. PubMed ID: 3087427
[TBL] [Abstract][Full Text] [Related]
5. Correlation between enzyme activity and substrate storage in a cell culture model system for Gaucher disease.
Schueler UH; Kolter T; Kaneski CR; Zirzow GC; Sandhoff K; Brady RO
J Inherit Metab Dis; 2004; 27(5):649-58. PubMed ID: 15669681
[TBL] [Abstract][Full Text] [Related]
6. Phosphatidylcholine synthesis is elevated in neuronal models of Gaucher disease due to direct activation of CTP:phosphocholine cytidylyltransferase by glucosylceramide.
Bodennec J; Pelled D; Riebeling C; Trajkovic S; Futerman AH
FASEB J; 2002 Nov; 16(13):1814-6. PubMed ID: 12223447
[TBL] [Abstract][Full Text] [Related]
7. Elevation of intracellular glucosylceramide levels results in an increase in endoplasmic reticulum density and in functional calcium stores in cultured neurons.
Korkotian E; Schwarz A; Pelled D; Schwarzmann G; Segal M; Futerman AH
J Biol Chem; 1999 Jul; 274(31):21673-8. PubMed ID: 10419477
[TBL] [Abstract][Full Text] [Related]
8. Glucosylceramide and glucosylsphingosine metabolism in cultured fibroblasts deficient in acid beta-glucosidase activity.
Sasagasako N; Kobayashi T; Yamaguchi Y; Shinnoh N; Goto I
J Biochem; 1994 Jan; 115(1):113-9. PubMed ID: 8188616
[TBL] [Abstract][Full Text] [Related]
9. Coenzyme Q
de la Mata M; Cotán D; Oropesa-Ávila M; Villanueva-Paz M; de Lavera I; Álvarez-Córdoba M; Luzón-Hidalgo R; Suárez-Rivero JM; Tiscornia G; Sánchez-Alcázar JA
Orphanet J Rare Dis; 2017 Feb; 12(1):23. PubMed ID: 28166796
[TBL] [Abstract][Full Text] [Related]
10. Klotho-Related Protein KLrP: Structure and Functions.
Hayashi Y; Ito M
Vitam Horm; 2016; 101():1-16. PubMed ID: 27125736
[TBL] [Abstract][Full Text] [Related]
11. Phosphatidylcholine metabolism is altered in a monocyte-derived macrophage model of Gaucher disease but not in lymphocytes.
Trajkovic-Bodennec S; Bodennec J; Futerman AH
Blood Cells Mol Dis; 2004; 33(1):77-82. PubMed ID: 15223015
[TBL] [Abstract][Full Text] [Related]
12. In vivo inactivation of glycosidases by conduritol B epoxide and cyclophellitol as revealed by activity-based protein profiling.
Kuo CL; Kallemeijn WW; Lelieveld LT; Mirzaian M; Zoutendijk I; Vardi A; Futerman AH; Meijer AH; Spaink HP; Overkleeft HS; Aerts JMFG; Artola M
FEBS J; 2019 Feb; 286(3):584-600. PubMed ID: 30600575
[TBL] [Abstract][Full Text] [Related]
13. Multiple pathogenic proteins implicated in neuronopathic Gaucher disease mice.
Xu YH; Xu K; Sun Y; Liou B; Quinn B; Li RH; Xue L; Zhang W; Setchell KD; Witte D; Grabowski GA
Hum Mol Genet; 2014 Aug; 23(15):3943-57. PubMed ID: 24599400
[TBL] [Abstract][Full Text] [Related]
14. Glucocerebroside storage in normal monocyte cultures.
Hardy B; Teitelman-Weissman B; Chazan S; Neri A
Biomed Pharmacother; 1987; 41(1):40-4. PubMed ID: 3607254
[TBL] [Abstract][Full Text] [Related]
15. Glucosylceramide modulates endolysosomal pH in Gaucher disease.
Sillence DJ
Mol Genet Metab; 2013 Jun; 109(2):194-200. PubMed ID: 23628459
[TBL] [Abstract][Full Text] [Related]
16. The metabolism of glucocerebrosides - From 1965 to the present.
Futerman AH; Platt FM
Mol Genet Metab; 2017; 120(1-2):22-26. PubMed ID: 27955980
[TBL] [Abstract][Full Text] [Related]
17. The fate of glucosylceramide (glucocerebroside) in genetically impaired (lysosomal beta-glucosidase deficient) Gaucher disease diploid human fibroblasts.
Saito M; Rosenberg A
J Biol Chem; 1985 Feb; 260(4):2295-300. PubMed ID: 3919000
[TBL] [Abstract][Full Text] [Related]
18. The increased sensitivity of neurons with elevated glucocerebroside to neurotoxic agents can be reversed by imiglucerase.
Pelled D; Shogomori H; Futerman AH
J Inherit Metab Dis; 2000 Mar; 23(2):175-84. PubMed ID: 10801059
[TBL] [Abstract][Full Text] [Related]
19. The synthetic pathway for glucosylsphingosine in cultured fibroblasts.
Yamaguchi Y; Sasagasako N; Goto I; Kobayashi T
J Biochem; 1994 Sep; 116(3):704-10. PubMed ID: 7852294
[TBL] [Abstract][Full Text] [Related]
20. Glucocerebrosidase deficiency and lysosomal storage of glucocerebroside induced in cultured macrophages.
Das PK; Murray GJ; Gal AE; Barranger JA
Exp Cell Res; 1987 Feb; 168(2):463-74. PubMed ID: 3803450
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]