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3. Liver disease in the Ashkenazi-Jewish lipoamide dehydrogenase deficiency. Aptowitzer I; Saada A; Faber J; Kleid D; Elpeleg ON J Pediatr Gastroenterol Nutr; 1997 May; 24(5):599-601. PubMed ID: 9161958 [No Abstract] [Full Text] [Related]
4. Biochemical and molecular diagnosis of lipoamide dehydrogenase deficiency in a North American Ashkenazi Jewish family. Sansaricq C; Pardo S; Balwani M; Grace M; Raymond K J Inherit Metab Dis; 2006 Feb; 29(1):203-4. PubMed ID: 16601893 [TBL] [Abstract][Full Text] [Related]
5. Recurrent myoglobinuria as a presenting manifestation of very long chain acyl coenzyme A dehydrogenase deficiency. Straussberg R; Harel L; Varsano I; Elpeleg ON; Shamir R; Amir J Pediatrics; 1997 Jun; 99(6):894-6. PubMed ID: 9164788 [No Abstract] [Full Text] [Related]
6. Lipoamide dehydrogenase deficiency in Ashkenazi Jews: an insertion mutation in the mitochondrial leader sequence. Elpeleg ON; Shaag A; Glustein JZ; Anikster Y; Joseph A; Saada A Hum Mutat; 1997; 10(3):256-7. PubMed ID: 9298831 [No Abstract] [Full Text] [Related]
7. ATP synthesis in lipoamide dehydrogenase deficiency. Saada A; Aptowitzer I; Link G; Elpeleg ON Biochem Biophys Res Commun; 2000 Mar; 269(2):382-6. PubMed ID: 10708561 [TBL] [Abstract][Full Text] [Related]
8. Lipoamide dehydrogenase deficiency: a newly discovered cause of acute hepatitis in adults. Barak N; Huminer D; Segal T; Ben Ari Z; Halevy J; Tur-Kaspa R J Hepatol; 1998 Sep; 29(3):482-4. PubMed ID: 9764998 [TBL] [Abstract][Full Text] [Related]
9. Molecular basis of lipoamide dehydrogenase deficiency in Ashkenazi Jews. Shaag A; Saada A; Berger I; Mandel H; Joseph A; Feigenbaum A; Elpeleg ON Am J Med Genet; 1999 Jan; 82(2):177-82. PubMed ID: 9934985 [TBL] [Abstract][Full Text] [Related]
10. Novel mutations in a boy with dihydrolipoamide dehydrogenase deficiency. Cerna L; Wenchich L; Hansiková H; Kmoch S; Peskova K; Chrastina P; Brynda J; Zeman J Med Sci Monit; 2001; 7(6):1319-25. PubMed ID: 11687750 [TBL] [Abstract][Full Text] [Related]
11. Muscular carnitine palmitoyltransferase II deficiency in infancy. Hurvitz H; Klar A; Korn-Lubetzki I; Wanders RJ; Elpeleg ON Pediatr Neurol; 2000 Feb; 22(2):148-50. PubMed ID: 10738923 [TBL] [Abstract][Full Text] [Related]
12. Carnitine palmitoyltransferase deficiency: a common cause of recurrent myoglobinuria. Sadeh M; Gutman A Isr J Med Sci; 1990 Sep; 26(9):510-5. PubMed ID: 2228562 [TBL] [Abstract][Full Text] [Related]
14. Deficiency of dihydrolipoamide dehydrogenase due to two mutant alleles (E340K and G101del). Analysis of a family and prenatal testing. Hong YS; Kerr DS; Liu TC; Lusk M; Powell BR; Patel MS Biochim Biophys Acta; 1997 Dec; 1362(2-3):160-8. PubMed ID: 9540846 [TBL] [Abstract][Full Text] [Related]
15. Mitochondrial trifunctional protein deficiency associated with recurrent myoglobinuria in adolescence. Miyajima H; Orii KE; Shindo Y; Hashimoto T; Shinka T; Kuhara T; Matsumoto I; Shimizu H; Kaneko E Neurology; 1997 Sep; 49(3):833-7. PubMed ID: 9305349 [TBL] [Abstract][Full Text] [Related]
16. Phosphoglycerate kinase deficiency: a new cause of recurrent myoglobinuria. DiMauro S; Dalakas M; Miranda AF Trans Am Neurol Assoc; 1981; 106():202-5. PubMed ID: 7348995 [No Abstract] [Full Text] [Related]
17. Lipoamide dehydrogenase deficiency with primary lactic acidosis: favorable response to treatment with oral lipoic acid. Matalon R; Stumpf DA; Michals K; Hart RD; Parks JK; Goodman SI J Pediatr; 1984 Jan; 104(1):65-9. PubMed ID: 6418873 [TBL] [Abstract][Full Text] [Related]
18. Leigh syndrome due to compound heterozygosity of dihydrolipoamide dehydrogenase gene mutations. Description of the first E3 splice site mutation. Grafakou O; Oexle K; van den Heuvel L; Smeets R; Trijbels F; Goebel HH; Bosshard N; Superti-Furga A; Steinmann B; Smeitink J Eur J Pediatr; 2003 Oct; 162(10):714-8. PubMed ID: 12925875 [TBL] [Abstract][Full Text] [Related]
19. Very long-chain acyl coenzyme A dehydrogenase deficiency presenting with exercise-induced myoglobinuria. Ogilvie I; Pourfarzam M; Jackson S; Stockdale C; Bartlett K; Turnbull DM Neurology; 1994 Mar; 44(3 Pt 1):467-73. PubMed ID: 8145917 [TBL] [Abstract][Full Text] [Related]
20. [Clinical aspects of disorders of lipid metabolism in humans. II. Carnitine palmitoyltransferase deficiency]. Czyzewski K Neurol Neurochir Pol; 1988; 22(6):548-52. PubMed ID: 3077435 [No Abstract] [Full Text] [Related] [Next] [New Search]