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4. Molecular basis of methylmalonyl-CoA mutase apoenzyme defect in 40 European patients affected by mut(o) and mut- forms of methylmalonic acidemia: identification of 29 novel mutations in the MUT gene. Acquaviva C; Benoist JF; Pereira S; Callebaut I; Koskas T; Porquet D; Elion J Hum Mutat; 2005 Feb; 25(2):167-76. PubMed ID: 15643616 [TBL] [Abstract][Full Text] [Related]
5. Molecular basis for dysfunction of some mutant forms of methylmalonyl-CoA mutase: deductions from the structure of methionine synthase. Drennan CL; Matthews RG; Rosenblatt DS; Ledley FD; Fenton WA; Ludwig ML Proc Natl Acad Sci U S A; 1996 May; 93(11):5550-5. PubMed ID: 8643613 [TBL] [Abstract][Full Text] [Related]
6. mut0 methylmalonic acidemia: eleven novel mutations of the methylmalonyl CoA mutase including a deletion-insertion mutation. Fuchshuber A; Mucha B; Baumgartner ER; Vollmer M; Hildebrandt F Hum Mutat; 2000 Aug; 16(2):179. PubMed ID: 10923046 [TBL] [Abstract][Full Text] [Related]
7. Identification of the gene responsible for the cblA complementation group of vitamin B12-responsive methylmalonic acidemia based on analysis of prokaryotic gene arrangements. Dobson CM; Wai T; Leclerc D; Wilson A; Wu X; Doré C; Hudson T; Rosenblatt DS; Gravel RA Proc Natl Acad Sci U S A; 2002 Nov; 99(24):15554-9. PubMed ID: 12438653 [TBL] [Abstract][Full Text] [Related]
8. Homology modeling of human methylmalonyl-CoA mutase: a structural basis for point mutations causing methylmalonic aciduria. Thomä NH; Leadlay PF Protein Sci; 1996 Sep; 5(9):1922-7. PubMed ID: 8880917 [TBL] [Abstract][Full Text] [Related]
9. A homozygous nonsense mutation in the methylmalonyl-CoA epimerase gene (MCEE) results in mild methylmalonic aciduria. Bikker H; Bakker HD; Abeling NG; Poll-The BT; Kleijer WJ; Rosenblatt DS; Waterham HR; Wanders RJ; Duran M Hum Mutat; 2006 Jul; 27(7):640-3. PubMed ID: 16752391 [TBL] [Abstract][Full Text] [Related]
10. Molecular studies in mutase-deficient (MUT) methylmalonic aciduria: identification of five novel mutations. Peters HL; Nefedov M; Lee LW; Abdenur JE; Chamoles NA; Kahler SG; Ioannou PA Hum Mutat; 2002 Nov; 20(5):406. PubMed ID: 12402345 [TBL] [Abstract][Full Text] [Related]
11. Genetic analysis of three genes causing isolated methylmalonic acidemia: identification of 21 novel allelic variants. Martínez MA; Rincón A; Desviat LR; Merinero B; Ugarte M; Pérez B Mol Genet Metab; 2005 Apr; 84(4):317-25. PubMed ID: 15781192 [TBL] [Abstract][Full Text] [Related]
12. [Diagnosis and treatment of methylmalonic aciduria: a case report]. Mahfoud A; Domínguez CL; Pérez A; Rizzo C; Merinero B; Pérez B Invest Clin; 2007 Mar; 48(1):99-105. PubMed ID: 17432548 [TBL] [Abstract][Full Text] [Related]
13. Molecular analysis of methylmalonyl-CoA mutase deficiency: identification of three missense mutations in mut0 patients. Mikami H; Ogasawara M; Matsubara Y; Kikuchi M; Miyabayashi S; Kure S; Narisawa K J Hum Genet; 1999; 44(1):35-9. PubMed ID: 9929975 [TBL] [Abstract][Full Text] [Related]
14. Methylmalonic aciduria (cblF): case report and response to therapy. Waggoner DJ; Ueda K; Mantia C; Dowton SB Am J Med Genet; 1998 Oct; 79(5):373-5. PubMed ID: 9779804 [TBL] [Abstract][Full Text] [Related]
15. Clustering of mutations in methylmalonyl CoA mutase associated with mut- methylmalonic acidemia. Crane AM; Ledley FD Am J Hum Genet; 1994 Jul; 55(1):42-50. PubMed ID: 7912889 [TBL] [Abstract][Full Text] [Related]
16. Perspectives on methylmalonic acidemia resulting from molecular cloning of methylmalonyl CoA mutase. Ledley FD Bioessays; 1990 Jul; 12(7):335-40. PubMed ID: 1975493 [TBL] [Abstract][Full Text] [Related]
17. Homozygous nonsense mutation in the MCEE gene and siRNA suppression of methylmalonyl-CoA epimerase expression: a novel cause of mild methylmalonic aciduria. Dobson CM; Gradinger A; Longo N; Wu X; Leclerc D; Lerner-Ellis J; Lemieux M; Belair C; Watkins D; Rosenblatt DS; Gravel RA Mol Genet Metab; 2006 Aug; 88(4):327-33. PubMed ID: 16697227 [TBL] [Abstract][Full Text] [Related]
18. Gene identification for the cblD defect of vitamin B12 metabolism. Coelho D; Suormala T; Stucki M; Lerner-Ellis JP; Rosenblatt DS; Newbold RF; Baumgartner MR; Fowler B N Engl J Med; 2008 Apr; 358(14):1454-64. PubMed ID: 18385497 [TBL] [Abstract][Full Text] [Related]
19. [Analysis of the MUT gene mutations in patients with methylmalonic acidemia]. Wang F; Han L; Ye J; Qiu W; Zhang Y; Gao X; Wang Y; Yang Y; Gu X Zhonghua Yi Xue Yi Chuan Xue Za Zhi; 2009 Oct; 26(5):485-9. PubMed ID: 19806564 [TBL] [Abstract][Full Text] [Related]
20. [Prognosis of congenital methylmalonic aciduria. Correlations between tolerance to proteins, response to vitamin B12 and enzymatic defect (author's transl)]. Saudubray JM; Charpentier C; Coude FX; Ogier H; Pham Dinh D; Bartlett K; Gompertz D Arch Fr Pediatr; 1980; 37 Suppl 2():IX-XIV. PubMed ID: 6108749 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]