250 related articles for article (PubMed ID: 9305991)
1. Disease-associated mutations in cytoplasmic loops 1 and 2 of cystic fibrosis transmembrane conductance regulator impede processing or opening of the channel.
Seibert FS; Jia Y; Mathews CJ; Hanrahan JW; Riordan JR; Loo TW; Clarke DM
Biochemistry; 1997 Sep; 36(39):11966-74. PubMed ID: 9305991
[TBL] [Abstract][Full Text] [Related]
2. Selective activation of cystic fibrosis transmembrane conductance regulator Cl- and HCO3- conductances.
Reddy MM; Quinton PM
JOP; 2001 Jul; 2(4 Suppl):212-8. PubMed ID: 11875262
[TBL] [Abstract][Full Text] [Related]
3. Altered chloride ion channel kinetics associated with the delta F508 cystic fibrosis mutation.
Dalemans W; Barbry P; Champigny G; Jallat S; Dott K; Dreyer D; Crystal RG; Pavirani A; Lecocq JP; Lazdunski M
Nature; 1991 Dec 19-26; 354(6354):526-8. PubMed ID: 1722027
[TBL] [Abstract][Full Text] [Related]
4. Cystic fibrosis transmembrane conductance regulator (CFTR) and renal function.
Stanton BA
Wien Klin Wochenschr; 1997 Jun; 109(12-13):457-64. PubMed ID: 9261986
[TBL] [Abstract][Full Text] [Related]
5. Discovery of alpha-aminoazaheterocycle-methylglyoxal adducts as a new class of high-affinity inhibitors of cystic fibrosis transmembrane conductance regulator chloride channels.
Routaboul C; Norez C; Melin P; Molina MC; Boucherle B; Bossard F; Noel S; Robert R; Gauthier C; Becq F; Décout JL
J Pharmacol Exp Ther; 2007 Sep; 322(3):1023-35. PubMed ID: 17578899
[TBL] [Abstract][Full Text] [Related]
6. Disease-associated mutations in the fourth cytoplasmic loop of cystic fibrosis transmembrane conductance regulator compromise biosynthetic processing and chloride channel activity.
Seibert FS; Linsdell P; Loo TW; Hanrahan JW; Clarke DM; Riordan JR
J Biol Chem; 1996 Jun; 271(25):15139-45. PubMed ID: 8662892
[TBL] [Abstract][Full Text] [Related]
7. N-terminal CFTR missense variants severely affect the behavior of the CFTR chloride channel.
Gené GG; Llobet A; Larriba S; de Semir D; Martínez I; Escalada A; Solsona C; Casals T; Aran JM
Hum Mutat; 2008 May; 29(5):738-49. PubMed ID: 18306312
[TBL] [Abstract][Full Text] [Related]
8. Cytoplasmic loop three of cystic fibrosis transmembrane conductance regulator contributes to regulation of chloride channel activity.
Seibert FS; Linsdell P; Loo TW; Hanrahan JW; Riordan JR; Clarke DM
J Biol Chem; 1996 Nov; 271(44):27493-9. PubMed ID: 8910333
[TBL] [Abstract][Full Text] [Related]
9. Mutations in CFTR associated with mild-disease-form Cl- channels with altered pore properties.
Sheppard DN; Rich DP; Ostedgaard LS; Gregory RJ; Smith AE; Welsh MJ
Nature; 1993 Mar; 362(6416):160-4. PubMed ID: 7680769
[TBL] [Abstract][Full Text] [Related]
10. Control of dynamic CFTR selectivity by glutamate and ATP in epithelial cells.
Reddy MM; Quinton PM
Nature; 2003 Jun; 423(6941):756-60. PubMed ID: 12802335
[TBL] [Abstract][Full Text] [Related]
11. Direct interaction of a small-molecule modulator with G551D-CFTR, a cystic fibrosis-causing mutation associated with severe disease.
Pasyk S; Li C; Ramjeesingh M; Bear CE
Biochem J; 2009 Feb; 418(1):185-90. PubMed ID: 18945216
[TBL] [Abstract][Full Text] [Related]
12. Rescuing cystic fibrosis transmembrane conductance regulator (CFTR)-processing mutants by transcomplementation.
Cormet-Boyaka E; Jablonsky M; Naren AP; Jackson PL; Muccio DD; Kirk KL
Proc Natl Acad Sci U S A; 2004 May; 101(21):8221-6. PubMed ID: 15141088
[TBL] [Abstract][Full Text] [Related]
13. Mechanism of direct bicarbonate transport by the CFTR anion channel.
Tang L; Fatehi M; Linsdell P
J Cyst Fibros; 2009 Mar; 8(2):115-21. PubMed ID: 19019741
[TBL] [Abstract][Full Text] [Related]
14. Defective regulatory volume decrease in human cystic fibrosis tracheal cells because of altered regulation of intermediate conductance Ca2+-dependent potassium channels.
Vázquez E; Nobles M; Valverde MA
Proc Natl Acad Sci U S A; 2001 Apr; 98(9):5329-34. PubMed ID: 11309505
[TBL] [Abstract][Full Text] [Related]
15. CFTR Cl- channel and CFTR-associated ATP channel: distinct pores regulated by common gates.
Sugita M; Yue Y; Foskett JK
EMBO J; 1998 Feb; 17(4):898-908. PubMed ID: 9463368
[TBL] [Abstract][Full Text] [Related]
16. Direct block of the cystic fibrosis transmembrane conductance regulator Cl(-) channel by niflumic acid.
Scott-Ward TS; Li H; Schmidt A; Cai Z; Sheppard DN
Mol Membr Biol; 2004; 21(1):27-38. PubMed ID: 14668136
[TBL] [Abstract][Full Text] [Related]
17. Extent of the selectivity filter conferred by the sixth transmembrane region in the CFTR chloride channel pore.
Gupta J; Lindsell P
Mol Membr Biol; 2003; 20(1):45-52. PubMed ID: 12745925
[TBL] [Abstract][Full Text] [Related]
18. Revertant mutants G550E and 4RK rescue cystic fibrosis mutants in the first nucleotide-binding domain of CFTR by different mechanisms.
Roxo-Rosa M; Xu Z; Schmidt A; Neto M; Cai Z; Soares CM; Sheppard DN; Amaral MD
Proc Natl Acad Sci U S A; 2006 Nov; 103(47):17891-6. PubMed ID: 17098864
[TBL] [Abstract][Full Text] [Related]
19. Walker mutations reveal loose relationship between catalytic and channel-gating activities of purified CFTR (cystic fibrosis transmembrane conductance regulator).
Ramjeesingh M; Li C; Garami E; Huan LJ; Galley K; Wang Y; Bear CE
Biochemistry; 1999 Feb; 38(5):1463-8. PubMed ID: 9931011
[TBL] [Abstract][Full Text] [Related]
20. Potentiation of cystic fibrosis transmembrane conductance regulator (CFTR) Cl- currents by the chemical solvent tetrahydrofuran.
Hughes LK; Ju M; Sheppard DN
Mol Membr Biol; 2008 Sep; 25(6-7):528-38. PubMed ID: 18989824
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]