These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
25. The role of cystic fibrosis transmembrane conductance regulator phenylalanine 508 side chain in ion channel gating. Cui L; Aleksandrov L; Hou YX; Gentzsch M; Chen JH; Riordan JR; Aleksandrov AA J Physiol; 2006 Apr; 572(Pt 2):347-58. PubMed ID: 16484308 [TBL] [Abstract][Full Text] [Related]
26. Converting nonhydrolyzable nucleotides to strong cystic fibrosis transmembrane conductance regulator (CFTR) agonists by gain of function (GOF) mutations. Okeyo G; Wang W; Wei S; Kirk KL J Biol Chem; 2013 Jun; 288(24):17122-33. PubMed ID: 23620589 [TBL] [Abstract][Full Text] [Related]
27. ATP hydrolysis cycles and the gating of CFTR Cl- channels. Gadsby DC; Dousmanis AG; Nairn AC Acta Physiol Scand Suppl; 1998 Aug; 643():247-56. PubMed ID: 9789567 [TBL] [Abstract][Full Text] [Related]
28. Conserved allosteric hot spots in the transmembrane domains of cystic fibrosis transmembrane conductance regulator (CFTR) channels and multidrug resistance protein (MRP) pumps. Wei S; Roessler BC; Chauvet S; Guo J; Hartman JL; Kirk KL J Biol Chem; 2014 Jul; 289(29):19942-57. PubMed ID: 24876383 [TBL] [Abstract][Full Text] [Related]
29. Two rare variants that affect the same amino acid in CFTR have distinct responses to ivacaftor. Li H; Rodrat M; Al-Salmani MK; Veselu DF; Han ST; Raraigh KS; Cutting GR; Sheppard DN J Physiol; 2024 Jan; 602(2):333-354. PubMed ID: 38186087 [TBL] [Abstract][Full Text] [Related]
30. Severed channels probe regulation of gating of cystic fibrosis transmembrane conductance regulator by its cytoplasmic domains. Csanády L; Chan KW; Seto-Young D; Kopsco DC; Nairn AC; Gadsby DC J Gen Physiol; 2000 Sep; 116(3):477-500. PubMed ID: 10962022 [TBL] [Abstract][Full Text] [Related]
31. Repair of CFTR folding defects with correctors that function as pharmacological chaperones. Loo TW; Clarke DM Methods Mol Biol; 2011; 741():23-37. PubMed ID: 21594776 [TBL] [Abstract][Full Text] [Related]
33. Mutation of Walker-A lysine 464 in cystic fibrosis transmembrane conductance regulator reveals functional interaction between its nucleotide-binding domains. Powe AC; Al-Nakkash L; Li M; Hwang TC J Physiol; 2002 Mar; 539(Pt 2):333-46. PubMed ID: 11882668 [TBL] [Abstract][Full Text] [Related]
34. A chemical corrector modifies the channel function of F508del-CFTR. Kim Chiaw P; Wellhauser L; Huan LJ; Ramjeesingh M; Bear CE Mol Pharmacol; 2010 Sep; 78(3):411-8. PubMed ID: 20501743 [TBL] [Abstract][Full Text] [Related]
35. CFTR potentiators partially restore channel function to A561E-CFTR, a cystic fibrosis mutant with a similar mechanism of dysfunction as F508del-CFTR. Wang Y; Liu J; Loizidou A; Bugeja LA; Warner R; Hawley BR; Cai Z; Toye AM; Sheppard DN; Li H Br J Pharmacol; 2014 Oct; 171(19):4490-503. PubMed ID: 24902474 [TBL] [Abstract][Full Text] [Related]
36. The role of exocytosis in the activation of the chloride conductance in Chinese hamster ovary cells (CHO) stably expressing CFTR. Hug MJ; Thiele IE; Greger R Pflugers Arch; 1997 Nov; 434(6):779-84. PubMed ID: 9306012 [TBL] [Abstract][Full Text] [Related]
37. State-dependent regulation of cystic fibrosis transmembrane conductance regulator (CFTR) gating by a high affinity Fe3+ bridge between the regulatory domain and cytoplasmic loop 3. Wang G J Biol Chem; 2010 Dec; 285(52):40438-47. PubMed ID: 20952391 [TBL] [Abstract][Full Text] [Related]
38. Revertant mutants modify, but do not rescue, the gating defect of the cystic fibrosis mutant G551D-CFTR. Xu Z; Pissarra LS; Farinha CM; Liu J; Cai Z; Thibodeau PH; Amaral MD; Sheppard DN J Physiol; 2014 May; 592(9):1931-47. PubMed ID: 24591578 [TBL] [Abstract][Full Text] [Related]
39. The major cystic fibrosis causing mutation exhibits defective propensity for phosphorylation. Pasyk S; Molinski S; Ahmadi S; Ramjeesingh M; Huan LJ; Chin S; Du K; Yeger H; Taylor P; Moran MF; Bear CE Proteomics; 2015 Jan; 15(2-3):447-61. PubMed ID: 25330774 [TBL] [Abstract][Full Text] [Related]
40. Stoichiometry and novel gating mechanism within the cystic fibrosis transmembrane conductance regulator channel. Qian F; Li T; Yang F; Liu L Exp Physiol; 2014 Dec; 99(12):1611-23. PubMed ID: 25326525 [TBL] [Abstract][Full Text] [Related] [Previous] [Next] [New Search]