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5. Phosphomannomutase deficiency is the main cause of carbohydrate-deficient glycoprotein syndrome with type I isoelectrofocusing pattern of serum sialotransferrins. Jaeken J; Artigas J; Barone R; Fiumara A; de Koning TJ; Poll-The BT; de Rijk-van Andel JF; Hoffmann GF; Assmann B; Mayatepek E; Pineda M; Vilaseca MA; Saudubray JM; Schlüter B; Wevers R; Van Schaftingen E J Inherit Metab Dis; 1997 Jul; 20(3):447-9. PubMed ID: 9266378 [No Abstract] [Full Text] [Related]
7. Molecular basis of carbohydrate-deficient glycoprotein syndromes type I with normal phosphomannomutase activity. Freeze HH; Aebi M Biochim Biophys Acta; 1999 Oct; 1455(2-3):167-78. PubMed ID: 10571010 [TBL] [Abstract][Full Text] [Related]
8. A novel disorder of N-glycosylation due to phosphomannose isomerase deficiency. de Koning TJ; Dorland L; van Diggelen OP; Boonman AM; de Jong GJ; van Noort WL; De Schryver J; Duran M; van den Berg IE; Gerwig GJ; Berger R; Poll-The BT Biochem Biophys Res Commun; 1998 Apr; 245(1):38-42. PubMed ID: 9535779 [TBL] [Abstract][Full Text] [Related]
9. Carbohydrate-deficient glycoprotein syndrome type 1: correction of the glycosylation defect by deprivation of glucose or supplementation of mannose. Körner C; Lehle L; von Figura K Glycoconj J; 1998 May; 15(5):499-505. PubMed ID: 9881752 [TBL] [Abstract][Full Text] [Related]
10. Phosphomannomutase deficiency is a cause of carbohydrate-deficient glycoprotein syndrome type I. Van Schaftingen E; Jaeken J FEBS Lett; 1995 Dec; 377(3):318-20. PubMed ID: 8549746 [TBL] [Abstract][Full Text] [Related]
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18. A Novel N-Tetrasaccharide in Patients with Congenital Disorders of Glycosylation, Including Asparagine-Linked Glycosylation Protein 1, Phosphomannomutase 2, and Mannose Phosphate Isomerase Deficiencies. Zhang W; James PM; Ng BG; Li X; Xia B; Rong J; Asif G; Raymond K; Jones MA; Hegde M; Ju T; Cummings RD; Clarkson K; Wood T; Boerkoel CF; Freeze HH; He M Clin Chem; 2016 Jan; 62(1):208-17. PubMed ID: 26430078 [TBL] [Abstract][Full Text] [Related]
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