310 related articles for article (PubMed ID: 9353120)
1. Ataxin-1 with an expanded glutamine tract alters nuclear matrix-associated structures.
Skinner PJ; Koshy BT; Cummings CJ; Klement IA; Helin K; Servadio A; Zoghbi HY; Orr HT
Nature; 1997 Oct; 389(6654):971-4. PubMed ID: 9353120
[TBL] [Abstract][Full Text] [Related]
2. Progress in pathogenesis studies of spinocerebellar ataxia type 1.
Cummings CJ; Orr HT; Zoghbi HY
Philos Trans R Soc Lond B Biol Sci; 1999 Jun; 354(1386):1079-81. PubMed ID: 10434309
[TBL] [Abstract][Full Text] [Related]
3. Ataxin-1 nuclear localization and aggregation: role in polyglutamine-induced disease in SCA1 transgenic mice.
Klement IA; Skinner PJ; Kaytor MD; Yi H; Hersch SM; Clark HB; Zoghbi HY; Orr HT
Cell; 1998 Oct; 95(1):41-53. PubMed ID: 9778246
[TBL] [Abstract][Full Text] [Related]
4. Mutation of the E6-AP ubiquitin ligase reduces nuclear inclusion frequency while accelerating polyglutamine-induced pathology in SCA1 mice.
Cummings CJ; Reinstein E; Sun Y; Antalffy B; Jiang Y; Ciechanover A; Orr HT; Beaudet AL; Zoghbi HY
Neuron; 1999 Dec; 24(4):879-92. PubMed ID: 10624951
[TBL] [Abstract][Full Text] [Related]
5. The cerebellar leucine-rich acidic nuclear protein interacts with ataxin-1.
Matilla A; Koshy BT; Cummings CJ; Isobe T; Orr HT; Zoghbi HY
Nature; 1997 Oct; 389(6654):974-8. PubMed ID: 9353121
[TBL] [Abstract][Full Text] [Related]
6. Chaperone suppression of aggregation and altered subcellular proteasome localization imply protein misfolding in SCA1.
Cummings CJ; Mancini MA; Antalffy B; DeFranco DB; Orr HT; Zoghbi HY
Nat Genet; 1998 Jun; 19(2):148-54. PubMed ID: 9620770
[TBL] [Abstract][Full Text] [Related]
7. USP7, a ubiquitin-specific protease, interacts with ataxin-1, the SCA1 gene product.
Hong S; Kim SJ; Ka S; Choi I; Kang S
Mol Cell Neurosci; 2002 Jun; 20(2):298-306. PubMed ID: 12093161
[TBL] [Abstract][Full Text] [Related]
8. p80 coilin, a coiled body-specific protein, interacts with ataxin-1, the SCA1 gene product.
Hong S; Ka S; Kim S; Park Y; Kang S
Biochim Biophys Acta; 2003 May; 1638(1):35-42. PubMed ID: 12757932
[TBL] [Abstract][Full Text] [Related]
9. Serine 776 of ataxin-1 is critical for polyglutamine-induced disease in SCA1 transgenic mice.
Emamian ES; Kaytor MD; Duvick LA; Zu T; Tousey SK; Zoghbi HY; Clark HB; Orr HT
Neuron; 2003 May; 38(3):375-87. PubMed ID: 12741986
[TBL] [Abstract][Full Text] [Related]
10. Amino acids in a region of ataxin-1 outside of the polyglutamine tract influence the course of disease in SCA1 transgenic mice.
Skinner PJ; Vierra-Green CA; Emamian E; Zoghbi HY; Orr HT
Neuromolecular Med; 2002; 1(1):33-42. PubMed ID: 12025814
[TBL] [Abstract][Full Text] [Related]
11. Recovery from polyglutamine-induced neurodegeneration in conditional SCA1 transgenic mice.
Zu T; Duvick LA; Kaytor MD; Berlinger MS; Zoghbi HY; Clark HB; Orr HT
J Neurosci; 2004 Oct; 24(40):8853-61. PubMed ID: 15470152
[TBL] [Abstract][Full Text] [Related]
12. Altered trafficking of membrane proteins in purkinje cells of SCA1 transgenic mice.
Skinner PJ; Vierra-Green CA; Clark HB; Zoghbi HY; Orr HT
Am J Pathol; 2001 Sep; 159(3):905-13. PubMed ID: 11549583
[TBL] [Abstract][Full Text] [Related]
13. SCA1 transgenic mice: a model for neurodegeneration caused by an expanded CAG trinucleotide repeat.
Burright EN; Clark HB; Servadio A; Matilla T; Feddersen RM; Yunis WS; Duvick LA; Zoghbi HY; Orr HT
Cell; 1995 Sep; 82(6):937-48. PubMed ID: 7553854
[TBL] [Abstract][Full Text] [Related]
14. Polyglutamine-expanded ataxin-7 promotes non-cell-autonomous purkinje cell degeneration and displays proteolytic cleavage in ataxic transgenic mice.
Garden GA; Libby RT; Fu YH; Kinoshita Y; Huang J; Possin DE; Smith AC; Martinez RA; Fine GC; Grote SK; Ware CB; Einum DD; Morrison RS; Ptacek LJ; Sopher BL; La Spada AR
J Neurosci; 2002 Jun; 22(12):4897-905. PubMed ID: 12077187
[TBL] [Abstract][Full Text] [Related]
15. Spinocerebellar ataxia type 1--modeling the pathogenesis of a polyglutamine neurodegenerative disorder in transgenic mice.
Clark HB; Orr HT
J Neuropathol Exp Neurol; 2000 Apr; 59(4):265-70. PubMed ID: 10759181
[TBL] [Abstract][Full Text] [Related]
16. Glial S100B protein modulates mutant ataxin-1 aggregation and toxicity: TRTK12 peptide, a potential candidate for SCA1 therapy.
Vig PJ; Hearst S; Shao Q; Lopez ME; Murphy HA; Safaya E
Cerebellum; 2011 Jun; 10(2):254-66. PubMed ID: 21384195
[TBL] [Abstract][Full Text] [Related]
17. Cloning and developmental expression analysis of the murine homolog of the spinocerebellar ataxia type 1 gene (Sca1).
Banfi S; Servadio A; Chung M; Capozzoli F; Duvick LA; Elde R; Zoghbi HY; Orr HT
Hum Mol Genet; 1996 Jan; 5(1):33-40. PubMed ID: 8789437
[TBL] [Abstract][Full Text] [Related]
18. Expression analysis of the ataxin-1 protein in tissues from normal and spinocerebellar ataxia type 1 individuals.
Servadio A; Koshy B; Armstrong D; Antalffy B; Orr HT; Zoghbi HY
Nat Genet; 1995 May; 10(1):94-8. PubMed ID: 7647801
[TBL] [Abstract][Full Text] [Related]
19. The AXH domain of Ataxin-1 mediates neurodegeneration through its interaction with Gfi-1/Senseless proteins.
Tsuda H; Jafar-Nejad H; Patel AJ; Sun Y; Chen HK; Rose MF; Venken KJ; Botas J; Orr HT; Bellen HJ; Zoghbi HY
Cell; 2005 Aug; 122(4):633-44. PubMed ID: 16122429
[TBL] [Abstract][Full Text] [Related]
20. SUMO-1 interacts with mutant ataxin-1 and colocalizes to its aggregates in Purkinje cells of SCA1 transgenic mice.
Kang S; Hong S
Arch Ital Biol; 2010 Dec; 148(4):351-63. PubMed ID: 21308649
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
