116 related articles for article (PubMed ID: 9434090)
1. Mitochondrial abnormalities in a murine model of primary carnitine deficiency. Systemic pathology and trial of replacement therapy.
Kaido M; Fujimura H; Ono A; Toyooka K; Yoshikawa H; Nishimura T; Ozaki K; Narama I; Kuwajima M
Eur Neurol; 1997; 38(4):302-9. PubMed ID: 9434090
[TBL] [Abstract][Full Text] [Related]
2. Mitochondrial abnormalities of muscle tissue in mice with juvenile visceral steatosis associated with systemic carnitine deficiency.
Miyagawa J; Kuwajima M; Hanafusa T; Ozaki K; Fujimura H; Ono A; Uenaka R; Narama I; Oue T; Yamamoto K
Virchows Arch; 1995; 426(3):271-9. PubMed ID: 7773507
[TBL] [Abstract][Full Text] [Related]
3. Secondary abnormality of carnitine biosynthesis results from carnitine reabsorptional system defect in juvenile visceral steatosis mice.
Horiuchi M; Kobayashi K; Asaka N; Saheki T
Biochim Biophys Acta; 1997 Dec; 1362(2-3):263-8. PubMed ID: 9540857
[TBL] [Abstract][Full Text] [Related]
4. Characteristics of cardiac hypertrophy in the juvenile visceral steatosis mouse with systemic carnitine deficiency.
Kuwajima M; Lu K; Sei M; Ono A; Hayashi M; Ishiguro K; Ozaki K; Hotta K; Okita K; Murakami T; Miyagawa J; Narama I; Nikaido H; Hayakawa J; Nakajima H; Namba M; Hanafusa T; Matsuzawa Y; Shima K
J Mol Cell Cardiol; 1998 Apr; 30(4):773-81. PubMed ID: 9602426
[TBL] [Abstract][Full Text] [Related]
5. Carnitine transport defect in fibroblasts of juvenile visceral steatosis (JVS) mouse.
Kuwajima M; Lu K; Harashima H; Ono A; Sato I; Mizuno A; Murakami T; Nakajima H; Miyagawa J; Namba M; Hanafusa T; Hayakawa J; Matsuzawa Y; Shima K
Biochem Biophys Res Commun; 1996 Jun; 223(2):283-7. PubMed ID: 8670273
[TBL] [Abstract][Full Text] [Related]
6. Combined therapy with PPARalpha agonist and L-carnitine rescues lipotoxic cardiomyopathy due to systemic carnitine deficiency.
Asai T; Okumura K; Takahashi R; Matsui H; Numaguchi Y; Murakami H; Murakami R; Murohara T
Cardiovasc Res; 2006 Jun; 70(3):566-77. PubMed ID: 16546150
[TBL] [Abstract][Full Text] [Related]
7. Induction of PDK4 in the heart muscle of JVS mice, an animal model of systemic carnitine deficiency, does not appear to reduce glucose utilization by the heart.
Ushikai M; Horiuchi M; Kobayashi K; Matuda S; Inui A; Takeuchi T; Saheki T
Mol Genet Metab; 2011 Mar; 102(3):349-55. PubMed ID: 21190881
[TBL] [Abstract][Full Text] [Related]
8. Effect of carnitine deprivation on carnitine homeostasis and energy metabolism in mice with systemic carnitine deficiency.
Knapp AC; Todesco L; Torok M; Beier K; Krähenbühl S
Ann Nutr Metab; 2008; 52(2):136-44. PubMed ID: 18417958
[TBL] [Abstract][Full Text] [Related]
9. Cardiac hypertrophy in juvenile visceral steatosis (jvs) mice with systemic carnitine deficiency.
Horiuchi M; Yoshida H; Kobayashi K; Kuriwaki K; Yoshimine K; Tomomura M; Koizumi T; Nikaido H; Hayakawa J; Kuwajima M
FEBS Lett; 1993 Jul; 326(1-3):267-71. PubMed ID: 8325377
[TBL] [Abstract][Full Text] [Related]
10. Primary defect of juvenile visceral steatosis (jvs) mouse with systemic carnitine deficiency is probably in renal carnitine transport system.
Horiuchi M; Kobayashi K; Yamaguchi S; Shimizu N; Koizumi T; Nikaido H; Hayakawa J; Kuwajima M; Saheki T
Biochim Biophys Acta; 1994 Apr; 1226(1):25-30. PubMed ID: 8155735
[TBL] [Abstract][Full Text] [Related]
11. A heterozygote phenotype is present in the jvs +/- mutant mouse livers.
Lahjouji K; Elimrani I; Wu J; Mitchell GA; Qureshi IA
Mol Genet Metab; 2002 May; 76(1):76-80. PubMed ID: 12175785
[TBL] [Abstract][Full Text] [Related]
12. Prolonged effect of single carnitine administration on fasted carnitine-deficient JVS mice regarding their locomotor activity and energy expenditure.
Li MX; Yoshida G; Horiuchi M; Kobayashi K; Saheki T
Biochim Biophys Acta; 2006 Oct; 1761(10):1191-9. PubMed ID: 17027329
[TBL] [Abstract][Full Text] [Related]
13. The effect of carnitine on ketogenesis in perfused livers from juvenile visceral steatosis mice with systemic carnitine deficiency.
Nakajima T; Horiuchi M; Yamanaka H; Kizaki Z; Inoue F; Kodo N; Kinugasa A; Saheki T; Sawada T
Pediatr Res; 1997 Jul; 42(1):108-13. PubMed ID: 9212045
[TBL] [Abstract][Full Text] [Related]
14. Altered expression of atrial natriuretic peptide and contractile protein genes in hypertrophied ventricle of JVS mice with systemic carnitine deficiency.
Yoshimine K; Horiuchi M; Suzuki S; Kobayashi K; Abdul JM; Masuda M; Tomomura M; Ogawa Y; Itoh H; Nakao K; Osame M; Saheki T
J Mol Cell Cardiol; 1997 Feb; 29(2):571-8. PubMed ID: 9140816
[TBL] [Abstract][Full Text] [Related]
15. Attenuation of cardiac hypertrophy in carnitine-deficient juvenile visceral steatosis (JVS) mice achieved by lowering dietary lipid.
Jalil MA; Horiuchi M; Wakamatsu M; Li MX; Begum L; Suzuki K; Kobayashi K; Oka T; Saheki T
J Biochem; 2006 Feb; 139(2):263-70. PubMed ID: 16452314
[TBL] [Abstract][Full Text] [Related]
16. Dietary fish oil attenuates cardiac hypertrophy in lipotoxic cardiomyopathy due to systemic carnitine deficiency.
Takahashi R; Okumura K; Asai T; Hirai T; Murakami H; Murakami R; Numaguchi Y; Matsui H; Ito M; Murohara T
Cardiovasc Res; 2005 Nov; 68(2):213-23. PubMed ID: 15963478
[TBL] [Abstract][Full Text] [Related]
17. Decreased tissue distribution of L-carnitine in juvenile visceral steatosis mice.
Yokogawa K; Higashi Y; Tamai I; Nomura M; Hashimoto N; Nikaido H; Hayakawa J; Miyamoto K; Tsuji A
J Pharmacol Exp Ther; 1999 Apr; 289(1):224-30. PubMed ID: 10087008
[TBL] [Abstract][Full Text] [Related]
18. Catecholamine metabolism inhibitors and receptor blockades only partially suppress cardiac hypertrophy of juvenile visceral steatosis mice with systemic carnitine deficiency.
Jalil A; Horiuchi M; Nomoto M; Kobayashi K; Saheki T
Life Sci; 1999; 64(13):1137-44. PubMed ID: 10210276
[TBL] [Abstract][Full Text] [Related]
19. A missense mutation of mouse OCTN2, a sodium-dependent carnitine cotransporter, in the juvenile visceral steatosis mouse.
Lu Km; Nishimori H; Nakamura Y; Shima K; Kuwajima M
Biochem Biophys Res Commun; 1998 Nov; 252(3):590-4. PubMed ID: 9837751
[TBL] [Abstract][Full Text] [Related]
20. Toxicity of valproic acid in mice with decreased plasma and tissue carnitine stores.
Knapp AC; Todesco L; Beier K; Terracciano L; Sägesser H; Reichen J; Krähenbühl S
J Pharmacol Exp Ther; 2008 Feb; 324(2):568-75. PubMed ID: 17986647
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
