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2. Carbohydrate-deficient glycoprotein syndrome due to phosphomannomutase deficiency: the first reported cases from Latin America. de Michelena MI; Franchi LM; Summers PG; De La Fuente C; Campos PJ; Jaeken J Am J Med Genet; 1999 Jun; 84(5):481-3. PubMed ID: 10360403 [No Abstract] [Full Text] [Related]
3. Congenital disorder of glycosylation Ia with deficient phosphomannomutase activity but normal plasma glycoprotein pattern. Dupre T; Cuer M; Barrot S; Barnier A; Cormier-Daire V; Munnich A; Durand G; Seta N Clin Chem; 2001 Jan; 47(1):132-4. PubMed ID: 11148191 [No Abstract] [Full Text] [Related]
4. Mannose supplementation in carbohydrate-deficient glycoprotein syndrome type I and phosphomannomutase deficiency. Mayatepek E; Kohlmüller D Eur J Pediatr; 1998 Jul; 157(7):605-6. PubMed ID: 9686827 [No Abstract] [Full Text] [Related]
5. Phosphomannomutase deficiency is the main cause of carbohydrate-deficient glycoprotein syndrome with type I isoelectrofocusing pattern of serum sialotransferrins. Jaeken J; Artigas J; Barone R; Fiumara A; de Koning TJ; Poll-The BT; de Rijk-van Andel JF; Hoffmann GF; Assmann B; Mayatepek E; Pineda M; Vilaseca MA; Saudubray JM; Schlüter B; Wevers R; Van Schaftingen E J Inherit Metab Dis; 1997 Jul; 20(3):447-9. PubMed ID: 9266378 [No Abstract] [Full Text] [Related]
6. Phosphomannomutase deficiency: the molecular basis of the classical Jaeken syndrome (CDGS type Ia). Matthijs G; Schollen E; Heykants L; Grünewald S Mol Genet Metab; 1999 Oct; 68(2):220-6. PubMed ID: 10527672 [No Abstract] [Full Text] [Related]
7. Phosphomannomutase deficiency is a cause of carbohydrate-deficient glycoprotein syndrome type I. Van Schaftingen E; Jaeken J FEBS Lett; 1995 Dec; 377(3):318-20. PubMed ID: 8549746 [TBL] [Abstract][Full Text] [Related]
8. Lysosomal enzyme activities in serum and leukocytes from patients with carbohydrate-deficient glycoprotein syndrome type IA (phosphomannomutase deficiency). Barone R; Carchon H; Jansen E; Pavone L; Fiumara A; Bosshard NU; Gitzelmann R; Jaeken J J Inherit Metab Dis; 1998 Apr; 21(2):167-72. PubMed ID: 9584269 [TBL] [Abstract][Full Text] [Related]
9. The clinical spectrum of phosphomannomutase 2 deficiency (CDG-Ia). Grünewald S Biochim Biophys Acta; 2009 Sep; 1792(9):827-34. PubMed ID: 19272306 [TBL] [Abstract][Full Text] [Related]
10. Expanding the phenotype of phosphomannomutase-2 gene congenital disorder of glycosylation: Cervical dystonia. Rossi M; Medina Escobar A; Ameghino L; Merello M J Neurol Sci; 2017 Jul; 378():52-54. PubMed ID: 28566178 [No Abstract] [Full Text] [Related]
11. Identification of a IVS4-58delATG polymorphism in the human phosphomannomutase 2 (PMM2) gene. Vuillaumier-Barrot S; Bizec CL; Durand G; Grandchamp B; Seta N Hum Mutat; 2000 May; 15(5):486. PubMed ID: 10790224 [No Abstract] [Full Text] [Related]
13. [Metabolic disorders in patients with primary carbohydrate deficient glycoprotein syndrome]. Zwierz K; Midro AT Postepy Hig Med Dosw; 1997; 51(2):205-26. PubMed ID: 9235566 [TBL] [Abstract][Full Text] [Related]
14. Abnormal synthesis of mannose 1-phosphate derived carbohydrates in carbohydrate-deficient glycoprotein syndrome type I fibroblasts with phosphomannomutase deficiency. Körner C; Lehle L; von Figura K Glycobiology; 1998 Feb; 8(2):165-71. PubMed ID: 9451026 [TBL] [Abstract][Full Text] [Related]
15. Carbohydrate-deficient glycoprotein syndrome type IA (phosphomannomutase-deficiency). Carchon H; Van Schaftingen E; Matthijs G; Jaeken J Biochim Biophys Acta; 1999 Oct; 1455(2-3):155-65. PubMed ID: 10571009 [TBL] [Abstract][Full Text] [Related]
16. [Congenital disorder of glycosylation type Ia (CDG Ia) - underdiagnosed entity?]. Sätilä H; Kuusela AL; Pietilä K; Niinikoski H; Keskinen P Duodecim; 2016; 132(3):253-9. PubMed ID: 26951030 [TBL] [Abstract][Full Text] [Related]
17. A quantitative assessment of the evolution of cerebellar syndrome in children with phosphomannomutase-deficiency (PMM2-CDG). Serrano NL; De Diego V; Cuadras D; Martinez Monseny AF; Velázquez-Fragua R; López L; Felipe A; Gutiérrez-Solana LG; Macaya A; Pérez-Dueñas B; Serrano M; Orphanet J Rare Dis; 2017 Sep; 12(1):155. PubMed ID: 28915903 [TBL] [Abstract][Full Text] [Related]
18. Phosphomannomutase deficiency (PMM2-CDG): ataxia and cerebellar assessment. Serrano M; de Diego V; Muchart J; Cuadras D; Felipe A; Macaya A; Velázquez R; Poo MP; Fons C; O'Callaghan MM; García-Cazorla A; Boix C; Robles B; Carratalá F; Girós M; Briones P; Gort L; Artuch R; Pérez-Cerdá C; Jaeken J; Pérez B; Pérez-Dueñas B Orphanet J Rare Dis; 2015 Oct; 10():138. PubMed ID: 26502900 [TBL] [Abstract][Full Text] [Related]
19. Cerebellar ataxia and congenital disorder of glycosylation Ia (CDG-Ia) with normal routine CDG screening. Vermeer S; Kremer HP; Leijten QH; Scheffer H; Matthijs G; Wevers RA; Knoers NA; Morava E; Lefeber DJ J Neurol; 2007 Oct; 254(10):1356-8. PubMed ID: 17694350 [TBL] [Abstract][Full Text] [Related]
20. Hypoglycosylation of a brain glycoprotein (beta-trace protein) in CDG syndromes due to phosphomannomutase deficiency and N-acetylglucosaminyl-transferase II deficiency. Pohl S; Hoffmann A; Rüdiger A; Nimtz M; Jaeken J; Conradt HS Glycobiology; 1997 Dec; 7(8):1077-84. PubMed ID: 9455908 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]