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3. Combined malonic, methylmalonic and ethylmalonic acid semialdehyde dehydrogenase deficiencies: an inborn error of beta-alanine, L-valine and L-alloisoleucine metabolism? Gibson KM; Lee CF; Bennett MJ; Holmes B; Nyhan WL J Inherit Metab Dis; 1993; 16(3):563-7. PubMed ID: 7609453 [No Abstract] [Full Text] [Related]
4. Methylmalonic semialdehyde dehydrogenase deficiency: demonstration of defective valine and beta-alanine metabolism and reduced malonic semialdehyde dehydrogenase activity in cultured fibroblasts. Gray RG; Pollitt RJ; Webley J Biochem Med Metab Biol; 1987 Aug; 38(1):121-4. PubMed ID: 3117077 [TBL] [Abstract][Full Text] [Related]
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8. Purification and characterization of methylmalonate-semialdehyde dehydrogenase from rat liver. Identity to malonate-semialdehyde dehydrogenase. Goodwin GW; Rougraff PM; Davis EJ; Harris RA J Biol Chem; 1989 Sep; 264(25):14965-71. PubMed ID: 2768248 [TBL] [Abstract][Full Text] [Related]
9. Succinic semialdehyde dehydrogenase deficiency in children and adults. Pearl PL; Novotny EJ; Acosta MT; Jakobs C; Gibson KM Ann Neurol; 2003; 54 Suppl 6():S73-80. PubMed ID: 12891657 [TBL] [Abstract][Full Text] [Related]