These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
5. Neuronal ceroid lipofuscinoses and possible pathogenic mechanism. Zhong N Mol Genet Metab; 2000; 71(1-2):195-206. PubMed ID: 11001811 [TBL] [Abstract][Full Text] [Related]
6. Alterations in ROS activity and lysosomal pH account for distinct patterns of macroautophagy in LINCL and JNCL fibroblasts. Vidal-Donet JM; Cárcel-Trullols J; Casanova B; Aguado C; Knecht E PLoS One; 2013; 8(2):e55526. PubMed ID: 23408996 [TBL] [Abstract][Full Text] [Related]
7. Subcellular localization of mannose 6-phosphate glycoproteins in rat brain. Jadot M; Lin L; Sleat DE; Sohar I; Hsu MS; Pintar J; Dubois F; Wattiaux-De Coninck S; Wattiaux R; Lobel P J Biol Chem; 1999 Jul; 274(30):21104-13. PubMed ID: 10409663 [TBL] [Abstract][Full Text] [Related]
8. Molecular diagnosis of and carrier screening for the neuronal ceroid lipofuscinoses. Zhong NA; Wisniewski KE; Ju W; Moroziewicz DN; Jurkiewicz A; McLendon L; Jenkins EC; Brown WT Genet Test; 2000; 4(3):243-8. PubMed ID: 11142754 [TBL] [Abstract][Full Text] [Related]
9. Clinical protocol. Administration of a replication-deficient adeno-associated virus gene transfer vector expressing the human CLN2 cDNA to the brain of children with late infantile neuronal ceroid lipofuscinosis. Crystal RG; Sondhi D; Hackett NR; Kaminsky SM; Worgall S; Stieg P; Souweidane M; Hosain S; Heier L; Ballon D; Dinner M; Wisniewski K; Kaplitt M; Greenwald BM; Howell JD; Strybing K; Dyke J; Voss H Hum Gene Ther; 2004 Nov; 15(11):1131-54. PubMed ID: 15610613 [TBL] [Abstract][Full Text] [Related]
10. Acid phosphatase 5 is responsible for removing the mannose 6-phosphate recognition marker from lysosomal proteins. Sun P; Sleat DE; Lecocq M; Hayman AR; Jadot M; Lobel P Proc Natl Acad Sci U S A; 2008 Oct; 105(43):16590-5. PubMed ID: 18940929 [TBL] [Abstract][Full Text] [Related]
12. alpha-Glucosidase and N-acetylglucosamine-6-sulphatase are the major mannose-6-phosphate glycoproteins in human urine. Sleat DE; Kraus SR; Sohar I; Lackland H; Lobel P Biochem J; 1997 May; 324 ( Pt 1)(Pt 1):33-9. PubMed ID: 9164838 [TBL] [Abstract][Full Text] [Related]
13. Atypical late infantile and juvenile forms of neuronal ceroid lipofuscinosis and their diagnostic difficulties. Wiśniewski KE; Zhong N; Kida E; Kaczmarski W; Kaczmarski A; Connell F; Brooks SS; Brown WT Folia Neuropathol; 1997; 35(2):73-9. PubMed ID: 9377079 [TBL] [Abstract][Full Text] [Related]
14. Molecular basis of the neuronal ceroid lipofuscinoses: mutations in CLN1, CLN2, CLN3, and CLN5. Mole SE; Mitchison HM; Munroe PB Hum Mutat; 1999; 14(3):199-215. PubMed ID: 10477428 [TBL] [Abstract][Full Text] [Related]
15. Lysosomal ceroid depletion by drugs: therapeutic implications for a hereditary neurodegenerative disease of childhood. Zhang Z; Butler JD; Levin SW; Wisniewski KE; Brooks SS; Mukherjee AB Nat Med; 2001 Apr; 7(4):478-84. PubMed ID: 11283676 [TBL] [Abstract][Full Text] [Related]
16. Mechanisms of neurodegeneration in neuronal ceroid-lipofuscinoses. Hachiya Y; Hayashi M; Kumada S; Uchiyama A; Tsuchiya K; Kurata K Acta Neuropathol; 2006 Feb; 111(2):168-77. PubMed ID: 16465529 [TBL] [Abstract][Full Text] [Related]
17. Increased levels of glycoproteins containing mannose 6-phosphate in human breast carcinomas. Sleat DE; Chen TL; Raska K; Lobel P Cancer Res; 1995 Aug; 55(15):3424-30. PubMed ID: 7614483 [TBL] [Abstract][Full Text] [Related]
18. The human brain mannose 6-phosphate glycoproteome: a complex mixture composed of multiple isoforms of many soluble lysosomal proteins. Sleat DE; Lackland H; Wang Y; Sohar I; Xiao G; Li H; Lobel P Proteomics; 2005 Apr; 5(6):1520-32. PubMed ID: 15789345 [TBL] [Abstract][Full Text] [Related]
19. Enrichment of high mannose-type glycans in nervous tissue glycoproteins in neuronal ceroid-lipofuscinosis. Krusius T; Viitala J; Palo J; Maury CP J Neurol Sci; 1986 Jan; 72(1):1-10. PubMed ID: 3950650 [TBL] [Abstract][Full Text] [Related]
20. Defective lysosomal arginine transport in juvenile Batten disease. Ramirez-Montealegre D; Pearce DA Hum Mol Genet; 2005 Dec; 14(23):3759-73. PubMed ID: 16251196 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]