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2. Gerstmann-Sträussler-Scheinker disease and the French-Alsatian A117V variant. Mohr M; Tranchant C; Steinmetz G; Floquet J; Grignon Y; Warter JM Clin Exp Pathol; 1999; 47(3-4):161-75. PubMed ID: 10472736 [TBL] [Abstract][Full Text] [Related]
3. Mutant prion proteins in Gerstmann-Sträussler-Scheinker disease with neurofibrillary tangles. Hsiao K; Dlouhy SR; Farlow MR; Cass C; Da Costa M; Conneally PM; Hodes ME; Ghetti B; Prusiner SB Nat Genet; 1992 Apr; 1(1):68-71. PubMed ID: 1363810 [TBL] [Abstract][Full Text] [Related]
4. Gerstmann-Sträussler-Scheinker disease with A117V mutation in a second French-Alsatian family. Heldt N; Boellaard JW; Brown P; Cervenákova L; Doerr-Schott J; Thomas C; Scherer C; Rohmer F Clin Neuropathol; 1998; 17(4):229-34. PubMed ID: 9707339 [TBL] [Abstract][Full Text] [Related]
5. A second case of Gerstmann-Sträussler-Scheinker disease linked to the G131V mutation in the prion protein gene in a Dutch patient. Jansen C; Parchi P; Capellari S; Strammiello R; Dopper EG; van Swieten JC; Kamphorst W; Rozemuller AJ J Neuropathol Exp Neurol; 2011 Aug; 70(8):698-702. PubMed ID: 21760536 [TBL] [Abstract][Full Text] [Related]
7. Neuropathological features of a case with schizophrenia and prion protein gene P102L mutation before onset of Gerstmann-Sträussler-Scheinker disease. Sasaki K; Doh-ura K; Furuta A; Nakashima S; Morisada Y; Tateishi J; Iwaki T Acta Neuropathol; 2003 Jul; 106(1):92-6. PubMed ID: 12682740 [TBL] [Abstract][Full Text] [Related]
8. [Mutation of codon 117 of the prion gene in Gerstmann-Sträussler-Scheinker disease]. Tranchant C; Doh-Ura K; Steinmetz G; Chevalier Y; Kitamoto T; Tateishi J; Warter JM Rev Neurol (Paris); 1991; 147(4):274-8. PubMed ID: 2063076 [TBL] [Abstract][Full Text] [Related]
9. Gerstmann-Sträussler-Scheinker disease. I. Human diseases. Liberski PP; Budka H Folia Neuropathol; 2004; 42 Suppl B():120-40. PubMed ID: 16903147 [TBL] [Abstract][Full Text] [Related]
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11. A synthetic peptide initiates Gerstmann-Sträussler-Scheinker (GSS) disease in transgenic mice. Kaneko K; Ball HL; Wille H; Zhang H; Groth D; Torchia M; Tremblay P; Safar J; Prusiner SB; DeArmond SJ; Baldwin MA; Cohen FE J Mol Biol; 2000 Jan; 295(4):997-1007. PubMed ID: 10656806 [TBL] [Abstract][Full Text] [Related]
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13. A new PRNP mutation (G131V) associated with Gerstmann-Sträussler-Scheinker disease. Panegyres PK; Toufexis K; Kakulas BA; Cernevakova L; Brown P; Ghetti B; Piccardo P; Dlouhy SR Arch Neurol; 2001 Nov; 58(11):1899-902. PubMed ID: 11709001 [TBL] [Abstract][Full Text] [Related]
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18. [A case of variant Gerstmann-Sträussler-Scheinker disease with the mutation of codon P105L]. Kubo M; Nishimura T; Shikata E; Kokubun Y; Takasu T Rinsho Shinkeigaku; 1995 Aug; 35(8):873-7. PubMed ID: 8665729 [TBL] [Abstract][Full Text] [Related]
19. Familial spongiform encephalopathy associated with a novel prion protein gene mutation. Nitrini R; Rosemberg S; Passos-Bueno MR; da Silva LS; Iughetti P; Papadopoulos M; Carrilho PM; Caramelli P; Albrecht S; Zatz M; LeBlanc A Ann Neurol; 1997 Aug; 42(2):138-46. PubMed ID: 9266722 [TBL] [Abstract][Full Text] [Related]
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