105 related articles for article (PubMed ID: 9802331)
1. Reduced cholesterol accumulation and improved deficient peroxisomal functions in a murine model of Niemann-Pick type C disease upon treatment with peroxisomal proliferators.
Schedin S; Pentchev P; Dallner G
Biochem Pharmacol; 1998 Nov; 56(9):1195-9. PubMed ID: 9802331
[TBL] [Abstract][Full Text] [Related]
2. Effect of a peroxysomal proliferator agent on intracellular cholesterol accumulation in cultured fibroblasts from Niemann-Pick type C disease patients.
Beheregaray AP; Souza FT; Coelho JC
Clin Chim Acta; 2003 Oct; 336(1-2):137-42. PubMed ID: 14500046
[TBL] [Abstract][Full Text] [Related]
3. Peroxisomal impairment in Niemann-Pick type C disease.
Schedin S; Sindelar PJ; Pentchev P; Brunk U; Dallner G
J Biol Chem; 1997 Mar; 272(10):6245-51. PubMed ID: 9045641
[TBL] [Abstract][Full Text] [Related]
4. Defect in fatty acid esterification of dolichol in Niemann-Pick type C1 mouse livers in vivo.
Turunen M; Schedin-Weiss S
Biochim Biophys Acta; 2007 Apr; 1771(4):506-13. PubMed ID: 17292665
[TBL] [Abstract][Full Text] [Related]
5. Murine model of Niemann-Pick C disease: mutation in a cholesterol homeostasis gene.
Loftus SK; Morris JA; Carstea ED; Gu JZ; Cummings C; Brown A; Ellison J; Ohno K; Rosenfeld MA; Tagle DA; Pentchev PG; Pavan WJ
Science; 1997 Jul; 277(5323):232-5. PubMed ID: 9211850
[TBL] [Abstract][Full Text] [Related]
6. Further studies on the involvement of selenium in peroxisome proliferation in rat liver. Comparison of effects with clofibric acid and perfluorooctanoic acid and the pharmacokinetics of [14C]clofibrate.
Olsson U; Sundberg C; Andersson K; De Pierre JW
Biochem Pharmacol; 1993 Nov; 46(10):1805-10. PubMed ID: 8250967
[TBL] [Abstract][Full Text] [Related]
7. Neuronal localization of sterol regulatory element binding protein-1 in the rodent and primate brain: a light and electron microscopic immunocytochemical study.
Ong WY; Hu CY; Soh YP; Lim TM; Pentchev PG; Patel SC
Neuroscience; 2000; 97(1):143-53. PubMed ID: 10771346
[TBL] [Abstract][Full Text] [Related]
8. Niemann-Pick disease type C and defective peroxisomal beta-oxidation of branched-chain substrates.
Sequeira JS; Vellodi A; Vanier MT; Clayton PT
J Inherit Metab Dis; 1998 Apr; 21(2):149-54. PubMed ID: 9584266
[TBL] [Abstract][Full Text] [Related]
9. Cholesterol esterification and Niemann-Pick disease: an approach to identifying the defect in fibroblasts.
Bowler LM; Shankaran R; Das I; Callahan JW
J Neurosci Res; 1990 Dec; 27(4):505-11. PubMed ID: 2079713
[TBL] [Abstract][Full Text] [Related]
10. A role for the peroxisomal 3-ketoacyl-CoA thiolase B enzyme in the control of PPARα-mediated upregulation of SREBP-2 target genes in the liver.
Fidaleo M; Arnauld S; Clémencet MC; Chevillard G; Royer MC; De Bruycker M; Wanders RJ; Athias A; Gresti J; Clouet P; Degrace P; Kersten S; Espeel M; Latruffe N; Nicolas-Francès V; Mandard S
Biochimie; 2011 May; 93(5):876-91. PubMed ID: 21352884
[TBL] [Abstract][Full Text] [Related]
11. Type C Niemann-Pick disease: a murine model of the lysosomal cholesterol lipidosis accumulates sphingosine and sphinganine in liver.
Goldin E; Roff CF; Miller SP; Rodriguez-Lafrasse C; Vanier MT; Brady RO; Pentchev PG
Biochim Biophys Acta; 1992 Aug; 1127(3):303-11. PubMed ID: 1324734
[TBL] [Abstract][Full Text] [Related]
12. Elevation of ubiquinone content by peroxisomal inducers in rat liver during aging.
Turunen M; Dallner G
Chem Biol Interact; 1998 Nov; 116(1-2):79-91. PubMed ID: 9877202
[TBL] [Abstract][Full Text] [Related]
13. Niemann-Pick C disease: cystine and lipids accumulate in the murine model of this lysosomal cholesterol lipidosis.
Butler JD; Vanier MT; Pentchev PG
Biochem Biophys Res Commun; 1993 Oct; 196(1):154-9. PubMed ID: 8216287
[TBL] [Abstract][Full Text] [Related]
14. Pharmacological and genetic modifications of somatic cholesterol do not substantially alter the course of CNS disease in Niemann-Pick C mice.
Erickson RP; Garver WS; Camargo F; Hossain GS; Heidenreich RA
J Inherit Metab Dis; 2000 Feb; 23(1):54-62. PubMed ID: 10682308
[TBL] [Abstract][Full Text] [Related]
15. Niemann-Pick C1 disease gene: homology to mediators of cholesterol homeostasis.
Carstea ED; Morris JA; Coleman KG; Loftus SK; Zhang D; Cummings C; Gu J; Rosenfeld MA; Pavan WJ; Krizman DB; Nagle J; Polymeropoulos MH; Sturley SL; Ioannou YA; Higgins ME; Comly M; Cooney A; Brown A; Kaneski CR; Blanchette-Mackie EJ; Dwyer NK; Neufeld EB; Chang TY; Liscum L; Strauss JF; Ohno K; Zeigler M; Carmi R; Sokol J; Markie D; O'Neill RR; van Diggelen OP; Elleder M; Patterson MC; Brady RO; Vanier MT; Pentchev PG; Tagle DA
Science; 1997 Jul; 277(5323):228-31. PubMed ID: 9211849
[TBL] [Abstract][Full Text] [Related]
16. Understanding Niemann-Pick type C disease: a fat problem.
Vincent I; Bu B; Erickson RP
Curr Opin Neurol; 2003 Apr; 16(2):155-61. PubMed ID: 12644742
[TBL] [Abstract][Full Text] [Related]
17. Cholesterol and tau protein--findings in Alzheimer's and Niemann Pick C's disease.
Ohm TG; Treiber-Held S; Distl R; Glöckner F; Schönheit B; Tamanai M; Meske V
Pharmacopsychiatry; 2003 Sep; 36 Suppl 2():S120-6. PubMed ID: 14574625
[TBL] [Abstract][Full Text] [Related]
18. Cholesterol accumulation and liver cell death in mice with Niemann-Pick type C disease.
Beltroy EP; Richardson JA; Horton JD; Turley SD; Dietschy JM
Hepatology; 2005 Oct; 42(4):886-93. PubMed ID: 16175610
[TBL] [Abstract][Full Text] [Related]
19. Regulation of perfluorooctanoic acid--induced peroxisomal enzyme activities and hepatocellular growth by adrenal hormones.
Thottassery J; Winberg L; Youssef J; Cunningham M; Badr M
Hepatology; 1992 Feb; 15(2):316-22. PubMed ID: 1735536
[TBL] [Abstract][Full Text] [Related]
20. Niemann-pick variant disorders: comparison of errors of cellular cholesterol homeostasis in group D and group C fibroblasts.
Butler JD; Comly ME; Kruth HS; Vanier M; Filling-Katz M; Fink J; Barton N; Weintroub H; Quirk JM; Tokoro T
Proc Natl Acad Sci U S A; 1987 Jan; 84(2):556-60. PubMed ID: 3540969
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
