532 related articles for article (PubMed ID: 9922383)
1. Role of CFTR in airway disease.
Pilewski JM; Frizzell RA
Physiol Rev; 1999 Jan; 79(1 Suppl):S215-55. PubMed ID: 9922383
[TBL] [Abstract][Full Text] [Related]
2. Cystic Fibrosis: Pathophysiology of Lung Disease.
Bergeron C; Cantin AM
Semin Respir Crit Care Med; 2019 Dec; 40(6):715-726. PubMed ID: 31659725
[TBL] [Abstract][Full Text] [Related]
3. Cellular heterogeneity of CFTR expression and function in the lung: implications for gene therapy of cystic fibrosis.
Jiang Q; Engelhardt JF
Eur J Hum Genet; 1998 Jan; 6(1):12-31. PubMed ID: 9781011
[TBL] [Abstract][Full Text] [Related]
4. The role of airway epithelium and blood neutrophils in the inflammatory response in cystic fibrosis.
Terheggen-Lagro SW; Rijkers GT; van der Ent CK
J Cyst Fibros; 2005 Aug; 4 Suppl 2():15-23. PubMed ID: 15967736
[TBL] [Abstract][Full Text] [Related]
5. Pharmacotherapy of the ion transport defect in cystic fibrosis: role of purinergic receptor agonists and other potential therapeutics.
Kunzelmann K; Mall M
Am J Respir Med; 2003; 2(4):299-309. PubMed ID: 14719996
[TBL] [Abstract][Full Text] [Related]
6. Airway surface liquid homeostasis in cystic fibrosis: pathophysiology and therapeutic targets.
Haq IJ; Gray MA; Garnett JP; Ward C; Brodlie M
Thorax; 2016 Mar; 71(3):284-7. PubMed ID: 26719229
[TBL] [Abstract][Full Text] [Related]
7. Modulation of Ion Transport to Restore Airway Hydration in Cystic Fibrosis.
Reihill JA; Douglas LEJ; Martin SL
Genes (Basel); 2021 Mar; 12(3):. PubMed ID: 33810137
[TBL] [Abstract][Full Text] [Related]
8. Ion channels as targets to treat cystic fibrosis lung disease.
Martin SL; Saint-Criq V; Hwang TC; Csanády L
J Cyst Fibros; 2018 Mar; 17(2S):S22-S27. PubMed ID: 29102290
[TBL] [Abstract][Full Text] [Related]
9. Cystic fibrosis: a disease of vulnerability to airway surface dehydration.
Boucher RC
Trends Mol Med; 2007 Jun; 13(6):231-40. PubMed ID: 17524805
[TBL] [Abstract][Full Text] [Related]
10. Introduction to section I: overview of approaches to study cystic fibrosis pathophysiology.
Clunes MT; Boucher RC
Methods Mol Biol; 2011; 742():3-14. PubMed ID: 21547723
[TBL] [Abstract][Full Text] [Related]
11. Reduced airway surface pH impairs bacterial killing in the porcine cystic fibrosis lung.
Pezzulo AA; Tang XX; Hoegger MJ; Abou Alaiwa MH; Ramachandran S; Moninger TO; Karp PH; Wohlford-Lenane CL; Haagsman HP; van Eijk M; Bánfi B; Horswill AR; Stoltz DA; McCray PB; Welsh MJ; Zabner J
Nature; 2012 Jul; 487(7405):109-13. PubMed ID: 22763554
[TBL] [Abstract][Full Text] [Related]
12. Role of airway surface liquid and submucosal glands in cystic fibrosis lung disease.
Verkman AS; Song Y; Thiagarajah JR
Am J Physiol Cell Physiol; 2003 Jan; 284(1):C2-15. PubMed ID: 12475759
[TBL] [Abstract][Full Text] [Related]
13. Lumacaftor and ivacaftor in the management of patients with cystic fibrosis: current evidence and future prospects.
Kuk K; Taylor-Cousar JL
Ther Adv Respir Dis; 2015 Dec; 9(6):313-26. PubMed ID: 26416827
[TBL] [Abstract][Full Text] [Related]
14. [CFTR and transepithelial ionic transport abnormalities in cystic fibrosis].
Becq F
Arch Pediatr; 2003 Sep; 10 Suppl 2():325s-332s. PubMed ID: 14671929
[TBL] [Abstract][Full Text] [Related]
15. [Physiopathology of cystic fibrosis lung disease].
Chinet T
Rev Mal Respir; 1999 Jun; 16(3):339-45. PubMed ID: 10472642
[TBL] [Abstract][Full Text] [Related]
16. Model of mucociliary clearance in cystic fibrosis lungs.
Kurbatova P; Bessonov N; Volpert V; Tiddens HA; Cornu C; Nony P; Caudri D;
J Theor Biol; 2015 May; 372():81-8. PubMed ID: 25746843
[TBL] [Abstract][Full Text] [Related]
17. Evidence of early increased sialylation of airway mucins and defective mucociliary clearance in CFTR-deficient piglets.
Caballero I; Ringot-Destrez B; Si-Tahar M; Barbry P; Guillon A; Lantier I; Berri M; Chevaleyre C; Fleurot I; Barc C; Ramphal R; Pons N; Paquet A; Lebrigand K; Baron C; Bähr A; Klymiuk N; Léonard R; Robbe-Masselot C
J Cyst Fibros; 2021 Jan; 20(1):173-182. PubMed ID: 32978064
[TBL] [Abstract][Full Text] [Related]
18. Immunopathology of Airway Surface Liquid Dehydration Disease.
Lewis BW; Patial S; Saini Y
J Immunol Res; 2019; 2019():2180409. PubMed ID: 31396541
[TBL] [Abstract][Full Text] [Related]
19. The epithelial sodium channel (ENaC) as a therapeutic target for cystic fibrosis.
Shei RJ; Peabody JE; Kaza N; Rowe SM
Curr Opin Pharmacol; 2018 Dec; 43():152-165. PubMed ID: 30340955
[TBL] [Abstract][Full Text] [Related]
20. Induction of a cAMP-stimulated chloride secretion in regenerating poorly differentiated airway epithelial cells by adenovirus-mediated CFTR gene transfer.
Dupuit F; Chinet T; Zahm JM; Pierrot D; Hinnrasky J; Kaplan H; Bonnet N; Puchelle E
Hum Gene Ther; 1997 Aug; 8(12):1439-50. PubMed ID: 9287144
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
