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  • Title: [Pancreatic neuroendocrine tumors and von Hippel-Lindau disease].
    Author: Musso C, Paraf F, Petit B, Archambeaud-Mouveroux F, Valleix D, Labrousse F.
    Journal: Ann Pathol; 2000 Mar; 20(2):130-3. PubMed ID: 10740008.
    Abstract:
    Pancreatic neuroendocrine tumors are rare in von Hippel-Lindau disease, most often asymptomatic, nonfunctioning, non secreting, and benign. We report a case of low grade malignant pancreatic, secreting and asymptomatic neuroendocrine tumors, occurring in a 27 year old woman in the setting von Hippel-Lindau disease with recurrent pheochromocytoma, retinal and medullary hemangioblastomas, paraganglioma of the carotid body and ovarian cystadenoma. Neuroendocrine pancreatic tumors of von Hippel-Lindau disease are often constituted by clear cells, in the contrary of other neuroendocrine tumors of the pancreas. Occurrence of a pancreatic neuroendocrine tumor, especially in association with pheochromocytoma, may be misdiagnosed with a type 2 multiple endocrine neoplasia syndrom instead of von Hippel-Lindau disease.
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