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  • Title: [Congenital intestinal lymphangiectasia: a rare differential diagnosis in hypoproteinemia in infants].
    Author: Möller A, Kalhoff H, Reuter T, Friedrichs N, Wagner N.
    Journal: Klin Padiatr; 2006; 218(4):224-5. PubMed ID: 16586269.
    Abstract:
    BACKGROUND: Congenital intestinal lymphangiectasia is a rare disease in childhood, which may already cause protein-losing enteropathy in newborns. PATIENT, METHODS AND RESULTS: This is a case report of an infant with generalized edema and protein-losing enteropathy, in whom intestinal lymphangiectasia was diagnosed at the age of two months. Following repetitive intravenous albumin und gamma globulin infusions, the elimination of long-chain fats from the diet and the substitution with medium-chain triglycerides (MCT) led to an improvement of the protein-losing enteropathy. CONCLUSION: In newborns with low level of serum protein and edema protein-losing enteropathy caused by congenital lymphangiectasia might be considered as a differential diagnosis.
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