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  • Title: Type IV Ehlers-Danlos syndrome with isolated arterial involvement.
    Author: Bellenot F, Boisgard S, Kantelip B, Maillard P, Tissandier P, Ribal JP, Glanddier G.
    Journal: Ann Vasc Surg; 1990 Jan; 4(1):15-9. PubMed ID: 2297468.
    Abstract:
    Ehlers-Danlos syndrome is a connective tissue disorder characterized by skin hyperelasticity and friability, hyperextensible small articulations, vascular fragility, and ocular and visceral symptoms. Ten types of Ehlers-Danlos syndrome have been described to date. Type IV is characterized by isolated arterial involvement with the risk of rupture, making diagnosis difficult. A 25-year-old man was operated on for a ruptured left and then right iliac artery and once again for a hepatic artery aneurysm within a nine month period. The diagnosis of Ehlers-Danlos syndrome was based on clinical and histopathologic findings. An asymptomatic iliac artery aneurysm was found in the patient's 23-year-old brother.
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