These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.


Pubmed for Handhelds

PUBMED FOR HANDHELDS

Search MEDLINE/PubMed

  • Title: [Peripheral neuropathy and chronic cholestasis due to paucity of interlobular bile ducts (author's transl)].
    Author: Landrieu P, Saïd G.
    Journal: Arch Fr Pediatr; 1980; 37(7):445-9. PubMed ID: 6254460.
    Abstract:
    Peripheral neuropathy was observed in three patients in the course of a chronic cholestasis due to paucity of interlobular bile ducts associated with several malformations (Alagille's syndrome). In two patients, investigations showed a chronic axonal neuropathy. In a third, the low density of myelinated fibers was associated with onion-bulb proliferation on the Schwann-cells and myelin abnormalities related to an associated dominant inherited primary hypertrophic neuropathy. The responsibility of a chronic vitamin E deficiency in the development of axonal lesions is discussed.
    [Abstract] [Full Text] [Related] [New Search]