These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.


Pubmed for Handhelds

PUBMED FOR HANDHELDS

Search MEDLINE/PubMed

  • Title: Deafness due to bilateral endolymphatic sac tumours in a case of von Hippel-Lindau syndrome.
    Author: Kempermann G, Neumann HP, Scheremet R, Volk B, Mann W, Gilsbach J, Laszig R.
    Journal: J Neurol Neurosurg Psychiatry; 1996 Sep; 61(3):318-20. PubMed ID: 8795608.
    Abstract:
    A case of bilateral endolymphatic sac tumours is reported. In a patient with von Hippel-Lindau syndrome, tumour growth in the right cerebellopontine angle caused deafness. The tumour was removed and classified as a metastasis from a thyroid carcinoma. However, on thyroidectomy no primary neoplasm could be found. Eight years later a similar tumour was operated on in the left petrosal bone. Histological appearance, immunocytochemical findings, and the clinical context gave evidence that the tumours had to be reclassified as endolymphatic sac tumours--extremely rare entities. The report supports the hypothesis, suggested by the few earlier case reports, that endolymphatic sac tumours could be one of the inherent tumour manifestations in von Hippel-Lindau syndrome.
    [Abstract] [Full Text] [Related] [New Search]