These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.


Pubmed for Handhelds

PUBMED FOR HANDHELDS

Journal Abstract Search

230 related items for PubMed ID: 12655352

  • 1. Lysosomal high molecular weight multienzyme complex.
    Ostrowska H, Krukowska K, Kalinowska J, Orłowska M, Lengiewicz I.
    Cell Mol Biol Lett; 2003; 8(1):19-24. PubMed ID: 12655352
    [Abstract] [Full Text] [Related]

  • 2. New mutations in the PPBG gene lead to loss of PPCA protein which affects the level of the beta-galactosidase/neuraminidase complex and the EBP-receptor.
    Malvagia S, Morrone A, Caciotti A, Bardelli T, d'Azzo A, Ancora G, Zammarchi E, Donati MA.
    Mol Genet Metab; 2004 May; 82(1):48-55. PubMed ID: 15110321
    [Abstract] [Full Text] [Related]

  • 3. Lysosomal multienzyme complex: biochemistry, genetics, and molecular pathophysiology.
    Pshezhetsky AV, Ashmarina M.
    Prog Nucleic Acid Res Mol Biol; 2001 May; 69():81-114. PubMed ID: 11550799
    [Abstract] [Full Text] [Related]

  • 4. Association of N-acetylgalactosamine-6-sulfate sulfatase with the multienzyme lysosomal complex of beta-galactosidase, cathepsin A, and neuraminidase. Possible implication for intralysosomal catabolism of keratan sulfate.
    Pshezhetsky AV, Potier M.
    J Biol Chem; 1996 Nov 08; 271(45):28359-65. PubMed ID: 8910459
    [Abstract] [Full Text] [Related]

  • 5. Transport of human lysosomal neuraminidase to mature lysosomes requires protective protein/cathepsin A.
    van der Spoel A, Bonten E, d'Azzo A.
    EMBO J; 1998 Mar 16; 17(6):1588-97. PubMed ID: 9501080
    [Abstract] [Full Text] [Related]

  • 6. Molecular pathology of galactosialidosis in a patient affected with two new frameshift mutations in the cathepsin A/protective protein gene.
    Richard C, Tranchemontagne J, Elsliger MA, Mitchell GA, Potier M, Pshezhetsky AV.
    Hum Mutat; 1998 Mar 16; 11(6):461-9. PubMed ID: 9603439
    [Abstract] [Full Text] [Related]

  • 7. Cathepsin A/protective protein: an unusual lysosomal multifunctional protein.
    Hiraiwa M.
    Cell Mol Life Sci; 1999 Dec 16; 56(11-12):894-907. PubMed ID: 11212324
    [Abstract] [Full Text] [Related]

  • 8. Enzymatic activity of lysosomal carboxypeptidase (cathepsin) A is required for proper elastic fiber formation and inactivation of endothelin-1.
    Seyrantepe V, Hinek A, Peng J, Fedjaev M, Ernest S, Kadota Y, Canuel M, Itoh K, Morales CR, Lavoie J, Tremblay J, Pshezhetsky AV.
    Circulation; 2008 Apr 15; 117(15):1973-81. PubMed ID: 18391110
    [Abstract] [Full Text] [Related]

  • 9. Lysosomal multienzyme complex: pros and cons of working together.
    Bonten EJ, Annunziata I, d'Azzo A.
    Cell Mol Life Sci; 2014 Jun 15; 71(11):2017-32. PubMed ID: 24337808
    [Abstract] [Full Text] [Related]

  • 10. Molecular mechanisms of pathogenesis in a glycosphingolipid and a glycoprotein storage disease.
    d'Azzo A, Bonten E.
    Biochem Soc Trans; 2010 Dec 15; 38(6):1453-7. PubMed ID: 21118106
    [Abstract] [Full Text] [Related]

  • 11. Impact of beta-galactosidase mutations on the expression of the canine lysosomal multienzyme complex.
    Kreutzer R, Kreutzer M, Sewell AC, Techangamsuwan S, Leeb T, Baumgärtner W.
    Biochim Biophys Acta; 2009 Oct 15; 1792(10):982-7. PubMed ID: 19607915
    [Abstract] [Full Text] [Related]

  • 12. [Orientation of three lysosomal enzymes in the mouse inner ear and hearing loss in enzyme gene deficiency].
    Guo YK, Xie DH, Yang XM.
    Zhong Nan Da Xue Xue Bao Yi Xue Ban; 2006 Feb 15; 31(1):79-84. PubMed ID: 16562682
    [Abstract] [Full Text] [Related]

  • 13. Direct affinity purification and supramolecular organization of human lysosomal cathepsin A.
    Pshezhetsky AV, Potier M.
    Arch Biochem Biophys; 1994 Aug 15; 313(1):64-70. PubMed ID: 8053688
    [Abstract] [Full Text] [Related]

  • 14. Role of beta-galactosidase and elastin binding protein in lysosomal and nonlysosomal complexes of patients with GM1-gangliosidosis.
    Caciotti A, Donati MA, Boneh A, d'Azzo A, Federico A, Parini R, Antuzzi D, Bardelli T, Nosi D, Kimonis V, Zammarchi E, Morrone A.
    Hum Mutat; 2005 Mar 15; 25(3):285-92. PubMed ID: 15714521
    [Abstract] [Full Text] [Related]

  • 15. Protective protein/cathepsin A loss in cultured cells derived from an early-infantile form of galactosialidosis patients homozygous for the A1184-G transition (Y395C mutation).
    Itoh K, Shimmoto M, Utsumi K, Mizoguchi N, Miharu N, Ohama K, Sakuraba H.
    Biochem Biophys Res Commun; 1998 Jun 09; 247(1):12-7. PubMed ID: 9636645
    [Abstract] [Full Text] [Related]

  • 16. Targeting macrophages with baculovirus-produced lysosomal enzymes: implications for enzyme replacement therapy of the glycoprotein storage disorder galactosialidosis.
    Bonten EJ, Wang D, Toy JN, Mann L, Mignardot A, Yogalingam G, D'Azzo A.
    FASEB J; 2004 Jun 09; 18(9):971-3. PubMed ID: 15084520
    [Abstract] [Full Text] [Related]

  • 17. Protective protein in the bovine lysosomal beta-galactosidase complex.
    Hiraiwa M, Saitoh M, Arai N, Shiraishi T, Odani S, Uda Y, Ono T, O'Brien JS.
    Biochim Biophys Acta; 1997 Sep 05; 1341(2):189-99. PubMed ID: 9357958
    [Abstract] [Full Text] [Related]

  • 18. A case of galactosialidosis with a homozygous Q49R point mutation.
    Matsumoto N, Gondo K, Kukita J, Higaki K, Paragison RC, Nanba E.
    Brain Dev; 2008 Oct 05; 30(9):595-8. PubMed ID: 18396002
    [Abstract] [Full Text] [Related]

  • 19. Three-dimensional structure of the human 'protective protein': structure of the precursor form suggests a complex activation mechanism.
    Rudenko G, Bonten E, d'Azzo A, Hol WG.
    Structure; 1995 Nov 15; 3(11):1249-59. PubMed ID: 8591035
    [Abstract] [Full Text] [Related]

  • 20. Mutations in sialidosis impair sialidase binding to the lysosomal multienzyme complex.
    Lukong KE, Landry K, Elsliger MA, Chang Y, Lefrancois S, Morales CR, Pshezhetsky AV.
    J Biol Chem; 2001 May 18; 276(20):17286-90. PubMed ID: 11279074
    [Abstract] [Full Text] [Related]

    Page: [Next] [New Search]
    of 12.