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140 related items for PubMed ID: 2105058

  • 1. A murine model of mucopolysaccharidosis VII. Gross and microscopic findings in beta-glucuronidase-deficient mice.
    Vogler C, Birkenmeier EH, Sly WS, Levy B, Pegors C, Kyle JW, Beamer WG.
    Am J Pathol; 1990 Jan; 136(1):207-17. PubMed ID: 2105058
    [Abstract] [Full Text] [Related]

  • 2. Early onset of lysosomal storage disease in a murine model of mucopolysaccharidosis type VII: undegraded substrate accumulates in many tissues in the fetus and very young MPS VII mouse.
    Vogler C, Levy B, Galvin N, Lessard M, Soper B, Barker J.
    Pediatr Dev Pathol; 2005 Jan; 8(4):453-62. PubMed ID: 16222480
    [Abstract] [Full Text] [Related]

  • 3. Murine mucopolysaccharidosis type VII. Characterization of a mouse with beta-glucuronidase deficiency.
    Birkenmeier EH, Davisson MT, Beamer WG, Ganschow RE, Vogler CA, Gwynn B, Lyford KA, Maltais LM, Wawrzyniak CJ.
    J Clin Invest; 1989 Apr; 83(4):1258-66. PubMed ID: 2495302
    [Abstract] [Full Text] [Related]

  • 4. A novel model of murine mucopolysaccharidosis type VII due to an intracisternal a particle element transposition into the beta-glucuronidase gene: clinical and pathologic findings.
    Vogler C, Levy B, Galvin N, Sands MS, Birkenmeier EH, Sly WS, Barker J.
    Pediatr Res; 2001 Mar; 49(3):342-8. PubMed ID: 11228259
    [Abstract] [Full Text] [Related]

  • 5. Increased life span and correction of metabolic defects in murine mucopolysaccharidosis type VII after syngeneic bone marrow transplantation.
    Birkenmeier EH, Barker JE, Vogler CA, Kyle JW, Sly WS, Gwynn B, Levy B, Pegors C.
    Blood; 1991 Dec 01; 78(11):3081-92. PubMed ID: 1954394
    [Abstract] [Full Text] [Related]

  • 6. Enzyme replacement in murine mucopolysaccharidosis type VII: neuronal and glial response to beta-glucuronidase requires early initiation of enzyme replacement therapy.
    Vogler C, Levy B, Galvin NJ, Thorpe C, Sands MS, Barker JE, Baty J, Birkenmeier EH, Sly WS.
    Pediatr Res; 1999 Jun 01; 45(6):838-44. PubMed ID: 10367775
    [Abstract] [Full Text] [Related]

  • 7. Neuropathology of murine mucopolysaccharidosis type VII.
    Levy B, Galvin N, Vogler C, Birkenmeier EH, Sly WS.
    Acta Neuropathol; 1996 Dec 01; 92(6):562-8. PubMed ID: 8960313
    [Abstract] [Full Text] [Related]

  • 8. Variant clinical course of mucopolysaccharidosis type VII in two groups of mice carrying the same mutation.
    Casal ML, Wolfe JH.
    Lab Invest; 1998 Dec 01; 78(12):1575-81. PubMed ID: 9881957
    [Abstract] [Full Text] [Related]

  • 9. Correction of lysosomal storage in the liver and spleen of MPS VII mice by implantation of genetically modified skin fibroblasts.
    Moullier P, Bohl D, Heard JM, Danos O.
    Nat Genet; 1993 Jun 01; 4(2):154-9. PubMed ID: 8348154
    [Abstract] [Full Text] [Related]

  • 10. Treatment of murine mucopolysaccharidosis type VII by syngeneic bone marrow transplantation in neonates.
    Sands MS, Barker JE, Vogler C, Levy B, Gwynn B, Galvin N, Sly WS, Birkenmeier E.
    Lab Invest; 1993 Jun 01; 68(6):676-86. PubMed ID: 8515654
    [Abstract] [Full Text] [Related]

  • 11. Recombinant adeno-associated virus-mediated correction of lysosomal storage within the central nervous system of the adult mucopolysaccharidosis type VII mouse.
    Sferra TJ, Qu G, McNeely D, Rennard R, Clark KR, Lo WD, Johnson PR.
    Hum Gene Ther; 2000 Mar 01; 11(4):507-19. PubMed ID: 10724030
    [Abstract] [Full Text] [Related]

  • 12. Enzyme replacement with recombinant beta-glucuronidase in murine mucopolysaccharidosis type VII: impact of therapy during the first six weeks of life on subsequent lysosomal storage, growth, and survival.
    Vogler C, Sands MS, Levy B, Galvin N, Birkenmeier EH, Sly WS.
    Pediatr Res; 1996 Jun 01; 39(6):1050-4. PubMed ID: 8725268
    [Abstract] [Full Text] [Related]

  • 13. Beta-glucuronidase deficiency in a dog: a model of human mucopolysaccharidosis VII.
    Haskins ME, Desnick RJ, DiFerrante N, Jezyk PF, Patterson DF.
    Pediatr Res; 1984 Oct 01; 18(10):980-4. PubMed ID: 6436780
    [Abstract] [Full Text] [Related]

  • 14. Treatment of a lysosomal storage disease, mucopolysaccharidosis VII, with microencapsulated recombinant cells.
    Ross CJ, Bastedo L, Maier SA, Sands MS, Chang PL.
    Hum Gene Ther; 2000 Oct 10; 11(15):2117-27. PubMed ID: 11044913
    [Abstract] [Full Text] [Related]

  • 15. Numerous transcriptional alterations in liver persist after short-term enzyme-replacement therapy in a murine model of mucopolysaccharidosis type VII.
    Woloszynek JC, Roberts M, Coleman T, Vogler C, Sly W, Semenkovich CF, Sands MS.
    Biochem J; 2004 Apr 15; 379(Pt 2):461-9. PubMed ID: 14705966
    [Abstract] [Full Text] [Related]

  • 16. Widespread biochemical correction of murine mucopolysaccharidosis type VII pathology by liver hydrodynamic plasmid delivery.
    Richard M, Arfi A, Seguin J, Gandolphe C, Scherman D.
    Gene Ther; 2009 Jun 15; 16(6):746-56. PubMed ID: 19357715
    [Abstract] [Full Text] [Related]

  • 17. Morphological alterations in dental and periodontal tissues in murine mucopolysaccharidosis type VII.
    Gritli-Linde A, Linde A, Goldberg M.
    Calcif Tissue Int; 1995 Sep 15; 57(3):178-84. PubMed ID: 8574933
    [Abstract] [Full Text] [Related]

  • 18. Correction of murine mucopolysaccharidosis VII by a human beta-glucuronidase transgene.
    Kyle JW, Birkenmeier EH, Gwynn B, Vogler C, Hoppe PC, Hoffmann JW, Sly WS.
    Proc Natl Acad Sci U S A; 1990 May 15; 87(10):3914-8. PubMed ID: 2111021
    [Abstract] [Full Text] [Related]

  • 19. Lentiviral-mediated gene therapy results in sustained expression of β-glucuronidase for up to 12 months in the gus(mps/mps) and up to 18 months in the gus(tm(L175F)Sly) mouse models of mucopolysaccharidosis type VII.
    Derrick-Roberts AL, Pyragius CE, Kaidonis XM, Jackson MR, Anson DS, Byers S.
    Hum Gene Ther; 2014 Sep 15; 25(9):798-810. PubMed ID: 25003807
    [Abstract] [Full Text] [Related]

  • 20. Neonatal intramuscular injection with recombinant adeno-associated virus results in prolonged beta-glucuronidase expression in situ and correction of liver pathology in mucopolysaccharidosis type VII mice.
    Daly TM, Okuyama T, Vogler C, Haskins ME, Muzyczka N, Sands MS.
    Hum Gene Ther; 1999 Jan 01; 10(1):85-94. PubMed ID: 10022533
    [Abstract] [Full Text] [Related]

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