These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
2. A triple-blinded crossover study to evaluate the short-term safety of sweet manioc starch for the treatment of glycogen storage disease type Ia. Monteiro VCL, de Oliveira BM, Dos Santos BB, Sperb-Ludwig F, Refosco LF, Nalin T, Derks TGJ, Moura de Souza CF, Schwartz IVD. Orphanet J Rare Dis; 2021 Jun 03; 16(1):254. PubMed ID: 34082801 [Abstract] [Full Text] [Related]
4. Impact of hematopoietic stem cell transplantation in glycogen storage disease type Ib: A single-subject research design using 13C-glucose breath test. Turki A, Stockler S, Sirrs S, Duddy K, Ho G, Elango R. Mol Genet Metab Rep; 2023 Mar 03; 34():100955. PubMed ID: 36632325 [Abstract] [Full Text] [Related]
5. Use of modified cornstarch therapy to extend fasting in glycogen storage disease types Ia and Ib. Correia CE, Bhattacharya K, Lee PJ, Shuster JJ, Theriaque DW, Shankar MN, Smit GP, Weinstein DA. Am J Clin Nutr; 2008 Nov 03; 88(5):1272-6. PubMed ID: 18996862 [Abstract] [Full Text] [Related]
6. A novel starch for the treatment of glycogen storage diseases. Bhattacharya K, Orton RC, Qi X, Mundy H, Morley DW, Champion MP, Eaton S, Tester RF, Lee PJ. J Inherit Metab Dis; 2007 Jun 03; 30(3):350-7. PubMed ID: 17514432 [Abstract] [Full Text] [Related]
8. A pilot longitudinal study of the use of waxy maize heat modified starch in the treatment of adults with glycogen storage disease type I: a randomized double-blind cross-over study. Bhattacharya K, Mundy H, Lilburn MF, Champion MP, Morley DW, Maillot F. Orphanet J Rare Dis; 2015 Feb 15; 10():18. PubMed ID: 25758258 [Abstract] [Full Text] [Related]
9. Potential use of other starch sources in the treatment of glycogen storage disease type Ia - an in vitro study. Monteiro V, Colonetti K, Pagno CH, Schmidt HO, Sperb-Ludwig F, Oliveira BM, Poloni S, Rios AO, de Souza CFM, Schwartz IVD. Orphanet J Rare Dis; 2024 Jul 30; 19(1):283. PubMed ID: 39080776 [Abstract] [Full Text] [Related]
10. Utilization of cornstarch in glycogen storage disease type Ia. Bodamer OA, Feillet F, Lane RE, Lee PJ, Dixon MA, Halliday D, Leonard JV. Eur J Gastroenterol Hepatol; 2002 Nov 30; 14(11):1251-6. PubMed ID: 12439121 [Abstract] [Full Text] [Related]
11. The effect of tailoring of cornstarch intake on stature in children with glycogen storage disease type III. El-Karaksy H, El-Raziky MS, Anwar G, Mogahed E. J Pediatr Endocrinol Metab; 2015 Jan 30; 28(1-2):195-200. PubMed ID: 25153581 [Abstract] [Full Text] [Related]
12. Glycemic control and complications in glycogen storage disease type I: Results from the Swiss registry. Kaiser N, Gautschi M, Bosanska L, Meienberg F, Baumgartner MR, Spinas GA, Hochuli M. Mol Genet Metab; 2019 Apr 30; 126(4):355-361. PubMed ID: 30846352 [Abstract] [Full Text] [Related]
13. Alternative nighttime nutrition regimens in glycogen storage disease type I: a controlled crossover study. Hochuli M, Christ E, Meienberg F, Lehmann R, Krützfeldt J, Baumgartner MR. J Inherit Metab Dis; 2015 Nov 30; 38(6):1093-8. PubMed ID: 26109257 [Abstract] [Full Text] [Related]
14. Continuous glucose monitoring metrics in people with liver glycogen storage disease and idiopathic ketotic hypoglycemia: A single-center, retrospective, observational study. Overduin RJ, Venema A, Lubout CMA, Fokkert-Wilts MJ, De Boer F, Schreuder AB, Rossi A, Derks TGJ. Mol Genet Metab; 2024 Nov 30; 143(1-2):108573. PubMed ID: 39243574 [Abstract] [Full Text] [Related]
15. Effect of dietary interventions in the maintenance of normoglycaemia in glycogen storage disease type 1a: a systematic review and meta-analysis. Shah KK, O'Dell SD. J Hum Nutr Diet; 2013 Aug 30; 26(4):329-39. PubMed ID: 23294025 [Abstract] [Full Text] [Related]
16. Use of waxy maize heat modified starch in the treatment of children between 2 and 5 years with glycogen storage disease type I: A retrospective study. Hijazi G, Pai N, Nagy LL, Herd S, Dickson J, Ram M, Inbar-Feigenberg M. Mol Genet Metab Rep; 2019 Dec 30; 21():100536. PubMed ID: 31844626 [Abstract] [Full Text] [Related]
17. Glycogen Storage Disease Type Ia: Current Management Options, Burden and Unmet Needs. Derks TGJ, Rodriguez-Buritica DF, Ahmad A, de Boer F, Couce ML, Grünert SC, Labrune P, López Maldonado N, Fischinger Moura de Souza C, Riba-Wolman R, Rossi A, Saavedra H, Gupta RN, Valayannopoulos V, Mitchell J. Nutrients; 2021 Oct 27; 13(11):. PubMed ID: 34836082 [Abstract] [Full Text] [Related]
18. Body composition in patients with hepatic glycogen storage diseases. Dos Santos BB, Colonetti K, Nalin T, de Oliveira BM, de Souza CFM, Spritzer PM, Schwartz IVD. Nutrition; 2022 Oct 27; 103-104():111763. PubMed ID: 35843041 [Abstract] [Full Text] [Related]
20. Safety and Efficacy of Chronic Extended Release Cornstarch Therapy for Glycogen Storage Disease Type I. Ross KM, Brown LM, Corrado MM, Chengsupanimit T, Curry LM, Ferrecchia IA, Porras LY, Mathew JT, Weinstein DA. JIMD Rep; 2016 Oct 27; 26():85-90. PubMed ID: 26303612 [Abstract] [Full Text] [Related] Page: [Next] [New Search]