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Journal Abstract Search


255 related items for PubMed ID: 4091843

  • 1. Transient hyperammonemia during aging in ornithine transcarbamylase-deficient, sparse-fur mice.
    Gushiken T, Yoshimura N, Saheki T.
    Biochem Int; 1985 Nov; 11(5):637-43. PubMed ID: 4091843
    [Abstract] [Full Text] [Related]

  • 2. Long-term correction of ammonia metabolism and prolonged survival in ornithine transcarbamylase-deficient mice following liver-directed treatment with adeno-associated viral vectors.
    Moscioni D, Morizono H, McCarter RJ, Stern A, Cabrera-Luque J, Hoang A, Sanmiguel J, Wu D, Bell P, Gao GP, Raper SE, Wilson JM, Batshaw ML.
    Mol Ther; 2006 Jul; 14(1):25-33. PubMed ID: 16677864
    [Abstract] [Full Text] [Related]

  • 3. Interaction between murine spf-ash mutation and genetic background yields different metabolic phenotypes.
    Marini JC, Erez A, Castillo L, Lee B.
    Am J Physiol Endocrinol Metab; 2007 Dec; 293(6):E1764-71. PubMed ID: 17925451
    [Abstract] [Full Text] [Related]

  • 4. The sparse fur mouse as a model for gene therapy in ornithine carbamoyltransferase deficiency.
    Batshaw ML, Yudkoff M, McLaughlin BA, Gorry E, Anegawa NJ, Smith IA, Hyman SL, Robinson MB.
    Gene Ther; 1995 Dec; 2(10):743-9. PubMed ID: 8750014
    [Abstract] [Full Text] [Related]

  • 5. The effects of various inhibitors on the regulation of orotic acid excretion in sparse-fur mutant mice (spf/Y) deficient in ornithine transcarbamylase.
    Nelson J, Qureshi IA, Vasudevan S, Sarma DS.
    Chem Biol Interact; 1993 Oct; 89(1):35-47. PubMed ID: 8221965
    [Abstract] [Full Text] [Related]

  • 6. [Variability of enzyme activity and urinary orotic acid in ornithine transcarbamylase deficient spf/+ heterozygotic mice].
    Qureshi IA, Letarte J, Lebel S, Ouellet R.
    Diabete Metab; 1986 Oct; 12(5):250-5. PubMed ID: 3803679
    [Abstract] [Full Text] [Related]

  • 7. Comprehensive characterization of ureagenesis in the spfash mouse, a model of human ornithine transcarbamylase deficiency, reveals age-dependency of ammonia detoxification.
    Allegri G, Deplazes S, Rimann N, Causton B, Scherer T, Leff JW, Diez-Fernandez C, Klimovskaia A, Fingerhut R, Krijt J, Kožich V, Nuoffer JM, Grisch-Chan HM, Thöny B, Häberle J.
    J Inherit Metab Dis; 2019 Nov; 42(6):1064-1076. PubMed ID: 30714172
    [Abstract] [Full Text] [Related]

  • 8. Study of enzyme defect in a case of ornithine transcarbamylase deficiency.
    Qureshi IA, Letarte J, Quellet R.
    Diabete Metab; 1978 Dec; 4(4):239-41. PubMed ID: 729890
    [Abstract] [Full Text] [Related]

  • 9. Importance of ornithine transcarbamylase (OTC) deficiency in small intestine for urinary orotic acid excretion: analysis of OTC-deficient spf-ash mice with OTC transgene.
    Saheki T, Mori K, Kobayashi K, Horiuchi M, Shige T, Obara T, Suzuki S, Mori M, Yamamura K.
    Biochim Biophys Acta; 1995 Jan 25; 1270(1):87-93. PubMed ID: 7827141
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  • 12. Development and inducibility of the hepatic and renal hippurate-synthesizing system in sparse-fur (spf) mutant mice with ornithine transcarbamylase deficiency.
    Qureshi IA, Lebel S, Letarte J.
    Biochem Int; 1989 Sep 25; 19(3):657-66. PubMed ID: 2818615
    [Abstract] [Full Text] [Related]

  • 13. Aberrations of ammonia metabolism in ornithine carbamoyltransferase-deficient spf-ash mice and their prevention by treatment with urea cycle intermediate amino acids and an ornithine aminotransferase inactivator.
    Li MX, Nakajima T, Fukushige T, Kobayashi K, Seiler N, Saheki T.
    Biochim Biophys Acta; 1999 Sep 20; 1455(1):1-11. PubMed ID: 10524224
    [Abstract] [Full Text] [Related]

  • 14. Developmental deficiency of the cholinergic system in congenitally hyperammonemic spf mice: effect of acetyl-L-carnitine.
    Ratnakumari L, Qureshi IA, Maysinger D, Butterworth RF.
    J Pharmacol Exp Ther; 1995 Jul 20; 274(1):437-43. PubMed ID: 7616428
    [Abstract] [Full Text] [Related]

  • 15. Hyperammonemia increases sensitivity to LPS.
    Marini JC, Broussard SR.
    Mol Genet Metab; 2006 Jun 20; 88(2):131-7. PubMed ID: 16497529
    [Abstract] [Full Text] [Related]

  • 16. Breeding experiments to combine the X-linked sparse-fur (spf) mutation with the autosomal recessive BALB/cByJ strain: testing the biochemical phenotype of double-mutant mice as a model for ammonia: fatty acyl CoA synergism.
    Qureshi IA, Leblanc D, Cyr D, Giguère R, Mitchell G.
    Biochem Biophys Res Commun; 1993 Mar 15; 191(2):744-9. PubMed ID: 8461026
    [Abstract] [Full Text] [Related]

  • 17. Developmental study of hepatic glutamine synthetase in a mouse model of congenital hyperammonemia.
    Skarpetas A, Mawal Y, Qureshi IA.
    Biochem Mol Biol Int; 1997 Sep 15; 43(1):133-9. PubMed ID: 9315291
    [Abstract] [Full Text] [Related]

  • 18. Effects of congenital hyperammonemia on the cerebral and hepatic levels of the intermediates of energy metabolism in spf mice.
    Ratnakumari L, Qureshi IA, Butterworth RF.
    Biochem Biophys Res Commun; 1992 Apr 30; 184(2):746-51. PubMed ID: 1575747
    [Abstract] [Full Text] [Related]

  • 19. Transient depletion of CD4 lymphocyte improves efficacy of repeated administration of recombinant adenovirus in the ornithine transcarbamylase deficient sparse fur mouse.
    Ye X, Robinson MB, Pabin C, Batshaw ML, Wilson JM.
    Gene Ther; 2000 Oct 30; 7(20):1761-7. PubMed ID: 11083498
    [Abstract] [Full Text] [Related]

  • 20. The role of hepatic ornithine transcarbamylase deficiency in the orotic aciduria of pregnant mice.
    Qureshi IA, Letarte J, Tuchweber B, Yousef I, Qureshi SR.
    Eur J Obstet Gynecol Reprod Biol; 1986 Jul 30; 22(3):183-91. PubMed ID: 3732588
    [Abstract] [Full Text] [Related]


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