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7. Specific delay in the degradation of mitochondrial ATP synthase subunit c in late infantile neuronal ceroid lipofuscinosis is derived from cellular proteolytic dysfunction rather than structural alteration of subunit c. Ezaki J, Wolfe LS, Kominami E. J Neurochem; 1996 Oct; 67(4):1677-87. PubMed ID: 8858953 [Abstract] [Full Text] [Related]
8. [Batten disease (Neuronal ceroid lipofuscinoses)--accumulation of ATP synthase subunit c caused by the delay of lysosomal degradation]. Ezaki J, Kominami E. Nihon Rinsho; 1995 Dec; 53(12):3055-61. PubMed ID: 8577058 [Abstract] [Full Text] [Related]
9. Tripeptidyl peptidase I, the late infantile neuronal ceroid lipofuscinosis gene product, initiates the lysosomal degradation of subunit c of ATP synthase. Ezaki J, Takeda-Ezaki M, Kominami E. J Biochem; 2000 Sep; 128(3):509-16. PubMed ID: 10965052 [Abstract] [Full Text] [Related]
10. Mitochondrial ATP synthase subunit c storage in the ceroid-lipofuscinoses (Batten disease). Palmer DN, Fearnley IM, Walker JE, Hall NA, Lake BD, Wolfe LS, Haltia M, Martinus RD, Jolly RD. Am J Med Genet; 1992 Feb 15; 42(4):561-7. PubMed ID: 1535179 [Abstract] [Full Text] [Related]
13. The ovine model of neuronal ceroid lipofuscinosis (NCL): its contribution to understanding the pathogenesis of Batten disease. Jolly RD. Neuropediatrics; 1997 Feb 15; 28(1):60-2. PubMed ID: 9151325 [Abstract] [Full Text] [Related]
15. Accumulation of mitochondrial ATP synthase subunit c in muscle in a patient with neuronal ceroid lipofuscinosis (late infantile form). Umehara F, Higuchi I, Tanaka K, Niiyama T, Ezaki J, Kominami E, Osame M. Acta Neuropathol; 1997 Jun 15; 93(6):628-32. PubMed ID: 9194903 [Abstract] [Full Text] [Related]
16. Light and electron microscopic studies on subunit c in cultured fibroblasts in late infantile and juvenile Batten disease. Lake BD, Rowan SA. Neuropediatrics; 1997 Feb 15; 28(1):56-9. PubMed ID: 9151324 [Abstract] [Full Text] [Related]
18. Submitochondrial distribution and delayed proteolysis of subunit c of the H+-transporting ATP-synthase in ovine ceroid-lipofuscinosis. Hughes SM, Moroni-Rawson P, Jolly RD, Jordan TW. Electrophoresis; 2001 May 15; 22(9):1785-94. PubMed ID: 11425233 [Abstract] [Full Text] [Related]
19. Lysosomal storage of subunit c of mitochondrial ATP synthase in Batten's disease (ceroid-lipofuscinosis). Hall NA, Lake BD, Dewji NN, Patrick AD. Biochem J; 1991 Apr 01; 275 ( Pt 1)(Pt 1):269-72. PubMed ID: 1826833 [Abstract] [Full Text] [Related]
20. Turnover of F1F0-ATP synthase subunit 9 and other proteolipids in normal and Batten disease fibroblasts. Tanner A, Shen BH, Dice JF. Biochim Biophys Acta; 1997 Oct 24; 1361(3):251-62. PubMed ID: 9375799 [Abstract] [Full Text] [Related] Page: [Next] [New Search]